Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival

Abstract Aspergillus-related immune reconstitution inflammatory syndrome (IRIS) is a challenge to diagnose in immunocompromised pediatric cancer patients with Invasive Pulmonary Aspergillosis (IPA). If not recognized, it can mimic disease progression and lead to overtreatment. Studies on Aspergillus...

Full description

Saved in:
Bibliographic Details
Main Authors: Ali Amanati, Mehdi Ghaderian Jahromi, Hadis Jafarian, Seyed Reza Abdipour Mehrian, Sarvin Sajedianfard, Shahdad Farokhmanesh, Arman Maddahi, Farima Safari, Seyed Ali Nabavizadeh, Mohammad Matin Karbalaee Alinazari
Format: Article
Language:English
Published: BMC 2024-12-01
Series:BMC Infectious Diseases
Subjects:
Online Access:https://doi.org/10.1186/s12879-024-10298-z
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850134797657047040
author Ali Amanati
Mehdi Ghaderian Jahromi
Hadis Jafarian
Seyed Reza Abdipour Mehrian
Sarvin Sajedianfard
Shahdad Farokhmanesh
Arman Maddahi
Farima Safari
Seyed Ali Nabavizadeh
Mohammad Matin Karbalaee Alinazari
author_facet Ali Amanati
Mehdi Ghaderian Jahromi
Hadis Jafarian
Seyed Reza Abdipour Mehrian
Sarvin Sajedianfard
Shahdad Farokhmanesh
Arman Maddahi
Farima Safari
Seyed Ali Nabavizadeh
Mohammad Matin Karbalaee Alinazari
author_sort Ali Amanati
collection DOAJ
description Abstract Aspergillus-related immune reconstitution inflammatory syndrome (IRIS) is a challenge to diagnose in immunocompromised pediatric cancer patients with Invasive Pulmonary Aspergillosis (IPA). If not recognized, it can mimic disease progression and lead to overtreatment. Studies on Aspergillus-related IRIS in the pediatric population are scarce. We prospectively identified four pediatric cancer patients diagnosed with IPA who developed paradoxical worsening of pulmonary symptoms following neutrophil recovery. The clinical course, imaging findings, and response to corticosteroids were also reviewed. All patients had refractory respiratory symptoms, including cough, breathing difficulties (dyspnea), and chest pain, despite antifungal therapy. Serial imaging revealed new or enlarging pulmonary infiltrates. Symptoms improved dramatically with corticosteroids without antifungal escalation, confirming Aspergillus-related IRIS diagnosis. Aspergillus-related IRIS can occur in immunocompromised children with cancer and IPA, mimicking disease progression. Recognition is important for avoiding overtreatment. This is the first report highlighting the features of Aspergillus-related IRIS in pediatric cancer patients.
format Article
id doaj-art-ec9ceaa7457e478dbd4872ea203a0784
institution OA Journals
issn 1471-2334
language English
publishDate 2024-12-01
publisher BMC
record_format Article
series BMC Infectious Diseases
spelling doaj-art-ec9ceaa7457e478dbd4872ea203a07842025-08-20T02:31:38ZengBMCBMC Infectious Diseases1471-23342024-12-0124111310.1186/s12879-024-10298-zAspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survivalAli Amanati0Mehdi Ghaderian Jahromi1Hadis Jafarian2Seyed Reza Abdipour Mehrian3Sarvin Sajedianfard4Shahdad Farokhmanesh5Arman Maddahi6Farima Safari7Seyed Ali Nabavizadeh8Mohammad Matin Karbalaee Alinazari9Shiraz University of Medical SciencesDepartment of Radiology, Medical Imaging Research Center, Shiraz University of Medical SciencesAlborzi Clinical Microbiology Research Center, Shiraz University of Medical SciencesHealth Policy Research Center, Institute of Health, Shiraz University of Medical SciencesShiraz University of Medical SciencesAlborzi Clinical Microbiology Research Center, Shiraz University of Medical SciencesAlborzi Clinical Microbiology Research Center, Shiraz University of Medical SciencesHealth Policy Research Center, Institute of Health, Shiraz University of Medical SciencesStudent Research Committee, School of Medicine, Shiraz University of Medical SciencesStudent Research Committee, School of Medicine, Shiraz University of Medical SciencesAbstract Aspergillus-related immune reconstitution inflammatory syndrome (IRIS) is a challenge to diagnose in immunocompromised pediatric cancer patients with Invasive Pulmonary Aspergillosis (IPA). If not recognized, it can mimic disease progression and lead to overtreatment. Studies on Aspergillus-related IRIS in the pediatric population are scarce. We prospectively identified four pediatric cancer patients diagnosed with IPA who developed paradoxical worsening of pulmonary symptoms following neutrophil recovery. The clinical course, imaging findings, and response to corticosteroids were also reviewed. All patients had refractory respiratory symptoms, including cough, breathing difficulties (dyspnea), and chest pain, despite antifungal therapy. Serial imaging revealed new or enlarging pulmonary infiltrates. Symptoms improved dramatically with corticosteroids without antifungal escalation, confirming Aspergillus-related IRIS diagnosis. Aspergillus-related IRIS can occur in immunocompromised children with cancer and IPA, mimicking disease progression. Recognition is important for avoiding overtreatment. This is the first report highlighting the features of Aspergillus-related IRIS in pediatric cancer patients.https://doi.org/10.1186/s12879-024-10298-zImmune reconstitution inflammatory syndromePediatric cancer patientsInvasive pulmonary aspergillosis
spellingShingle Ali Amanati
Mehdi Ghaderian Jahromi
Hadis Jafarian
Seyed Reza Abdipour Mehrian
Sarvin Sajedianfard
Shahdad Farokhmanesh
Arman Maddahi
Farima Safari
Seyed Ali Nabavizadeh
Mohammad Matin Karbalaee Alinazari
Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
BMC Infectious Diseases
Immune reconstitution inflammatory syndrome
Pediatric cancer patients
Invasive pulmonary aspergillosis
title Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
title_full Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
title_fullStr Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
title_full_unstemmed Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
title_short Aspergillus-related immune reconstitution inflammatory syndrome in pediatric cancer patients, clinical characteristics, imaging findings, and survival
title_sort aspergillus related immune reconstitution inflammatory syndrome in pediatric cancer patients clinical characteristics imaging findings and survival
topic Immune reconstitution inflammatory syndrome
Pediatric cancer patients
Invasive pulmonary aspergillosis
url https://doi.org/10.1186/s12879-024-10298-z
work_keys_str_mv AT aliamanati aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT mehdighaderianjahromi aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT hadisjafarian aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT seyedrezaabdipourmehrian aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT sarvinsajedianfard aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT shahdadfarokhmanesh aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT armanmaddahi aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT farimasafari aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT seyedalinabavizadeh aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival
AT mohammadmatinkarbalaeealinazari aspergillusrelatedimmunereconstitutioninflammatorysyndromeinpediatriccancerpatientsclinicalcharacteristicsimagingfindingsandsurvival