Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis

The human acetylcholine receptor (AChR) is well characterized as the target antigen in myasthenia gravis (MG). Pathogenic antibody responses against the AChR alpha-chain have been investigated extensively and are of diagnostic and prognostic value. However, less is known on the pathogenetic relevanc...

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Main Authors: Oliver Neuhaus, Karl-Heinz Wiesmüller, Hans-Peter Hartung, Heinz Wiendl
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Neurology Research International
Online Access:http://dx.doi.org/10.1155/2019/1969068
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author Oliver Neuhaus
Karl-Heinz Wiesmüller
Hans-Peter Hartung
Heinz Wiendl
author_facet Oliver Neuhaus
Karl-Heinz Wiesmüller
Hans-Peter Hartung
Heinz Wiendl
author_sort Oliver Neuhaus
collection DOAJ
description The human acetylcholine receptor (AChR) is well characterized as the target antigen in myasthenia gravis (MG). Pathogenic antibody responses against the AChR alpha-chain have been investigated extensively and are of diagnostic and prognostic value. However, less is known on the pathogenetic relevance of T-cell responses against epitopes of the different AChR chains (alpha, epsilon, gamma). Using an enzyme-linked immunospot (ELISPOT) assay we measured T-cell responses against recombinant fragments and synthetic peptides of the α and the ε subunits of the human AChR in MG patients (n=15) and in healthy donors (HD; n=9). In MG, highest T-cell responses were noted against recombinantly expressed Epsilon 1-221. Among the synthetic peptides Epsilon 201-215 showed the most prominent T-cell response and represented the peptide with the most remarkable difference between MG and HD. Taken together, prominent T-cell responses against the ε subunit of the human AChR indicate an important role in the pathogenesis of MG.
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spelling doaj-art-ec8e18f7567d4c68bb0e099374afcec12025-08-20T02:21:49ZengWileyNeurology Research International2090-18522090-18602019-01-01201910.1155/2019/19690681969068Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia GravisOliver Neuhaus0Karl-Heinz Wiesmüller1Hans-Peter Hartung2Heinz Wiendl3Department of Neurology, Medical University of Graz, Graz, AustriaEMC Microcollections GmbH, Tübingen, GermanyDepartment of Neurology, Medical University of Graz, Graz, AustriaDepartment of Neurology, University of Tübingen, Tübingen, GermanyThe human acetylcholine receptor (AChR) is well characterized as the target antigen in myasthenia gravis (MG). Pathogenic antibody responses against the AChR alpha-chain have been investigated extensively and are of diagnostic and prognostic value. However, less is known on the pathogenetic relevance of T-cell responses against epitopes of the different AChR chains (alpha, epsilon, gamma). Using an enzyme-linked immunospot (ELISPOT) assay we measured T-cell responses against recombinant fragments and synthetic peptides of the α and the ε subunits of the human AChR in MG patients (n=15) and in healthy donors (HD; n=9). In MG, highest T-cell responses were noted against recombinantly expressed Epsilon 1-221. Among the synthetic peptides Epsilon 201-215 showed the most prominent T-cell response and represented the peptide with the most remarkable difference between MG and HD. Taken together, prominent T-cell responses against the ε subunit of the human AChR indicate an important role in the pathogenesis of MG.http://dx.doi.org/10.1155/2019/1969068
spellingShingle Oliver Neuhaus
Karl-Heinz Wiesmüller
Hans-Peter Hartung
Heinz Wiendl
Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
Neurology Research International
title Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
title_full Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
title_fullStr Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
title_full_unstemmed Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
title_short Prominent T-Cell Responses against the Acetylcholine Receptor ε Subunit in Myasthenia Gravis
title_sort prominent t cell responses against the acetylcholine receptor ε subunit in myasthenia gravis
url http://dx.doi.org/10.1155/2019/1969068
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