Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension

Abstract Background Prognosis of chronic thromboembolic pulmonary hypertension (CTEPH) has improved after the availability of balloon pulmonary angioplasty (BPA) and approved drugs. However, the clinical effects of cancer, which is one of the associated medical conditions of CTEPH, remain unclear. W...

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Main Authors: Hiroyuki Fujii, Yu Taniguchi, Yuichi Tamura, Miki Sakamoto, Sachiyo Yoneda, Kenichi Yanaka, Noriaki Emoto, Ken-ichi Hirata, Hiromasa Otake
Format: Article
Language:English
Published: BMC 2025-01-01
Series:BMC Pulmonary Medicine
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Online Access:https://doi.org/10.1186/s12890-024-03460-5
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author Hiroyuki Fujii
Yu Taniguchi
Yuichi Tamura
Miki Sakamoto
Sachiyo Yoneda
Kenichi Yanaka
Noriaki Emoto
Ken-ichi Hirata
Hiromasa Otake
author_facet Hiroyuki Fujii
Yu Taniguchi
Yuichi Tamura
Miki Sakamoto
Sachiyo Yoneda
Kenichi Yanaka
Noriaki Emoto
Ken-ichi Hirata
Hiromasa Otake
author_sort Hiroyuki Fujii
collection DOAJ
description Abstract Background Prognosis of chronic thromboembolic pulmonary hypertension (CTEPH) has improved after the availability of balloon pulmonary angioplasty (BPA) and approved drugs. However, the clinical effects of cancer, which is one of the associated medical conditions of CTEPH, remain unclear. We aimed to investigate prognosis in patients with CTEPH and comorbid cancer. Methods Between January 2011 and December 2022, data of 264 consecutive patients with CTEPH who were treated with pulmonary endarterectomy, BPA, or medical therapy were retrospectively analyzed. The patients were allocated, based on the comorbidity of cancer as of December 2022, into the cancer (n = 47) and non-cancer (n = 217) groups. In the cancer group, active and non-active cancers were identified in 30 (64%) and 17 (36%) patients, respectively. Results The baseline characteristics, hemodynamics, and treatments were similar between the groups. More than half of the cancer were diagnosed within two years before or after CTEPH diagnosis. Twenty-seven patients died during the study period. Among them, 13 (48%) and 7 (26%) died of cancer and right heart failure, respectively. The 5-year survival rate was lower in the cancer group than in the non-cancer group (67.8% vs. 94.5%, p < 0.001). In the active cancer group, the 5-year survival rate was also lower than that in the non-active cancer and non-cancer groups (52.0% vs. 99.5%, p < 0.001 and 52.0% vs. 92.3%, p < 0.001, respectively). Multivariate Cox hazard analysis revealed that hemodialysis (p < 0.001) and cancer (p < 0.001) were independently associated with poor survival. Conclusion Patients with CTEPH rarely die of right heart failure, even if hemodynamically severe at diagnosis in the modern management era. However, patients with CTEPH frequently have comorbid cancer, which may be a strong prognostic factor.
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spelling doaj-art-ec186bffe01f4c8ea164e61edc938aee2025-08-20T01:48:03ZengBMCBMC Pulmonary Medicine1471-24662025-01-012511810.1186/s12890-024-03460-5Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertensionHiroyuki Fujii0Yu Taniguchi1Yuichi Tamura2Miki Sakamoto3Sachiyo Yoneda4Kenichi Yanaka5Noriaki Emoto6Ken-ichi Hirata7Hiromasa Otake8Division of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicinePulmonary Hypertension Center, International University of Health and Welfare Mita HospitalDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineDivision of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of MedicineAbstract Background Prognosis of chronic thromboembolic pulmonary hypertension (CTEPH) has improved after the availability of balloon pulmonary angioplasty (BPA) and approved drugs. However, the clinical effects of cancer, which is one of the associated medical conditions of CTEPH, remain unclear. We aimed to investigate prognosis in patients with CTEPH and comorbid cancer. Methods Between January 2011 and December 2022, data of 264 consecutive patients with CTEPH who were treated with pulmonary endarterectomy, BPA, or medical therapy were retrospectively analyzed. The patients were allocated, based on the comorbidity of cancer as of December 2022, into the cancer (n = 47) and non-cancer (n = 217) groups. In the cancer group, active and non-active cancers were identified in 30 (64%) and 17 (36%) patients, respectively. Results The baseline characteristics, hemodynamics, and treatments were similar between the groups. More than half of the cancer were diagnosed within two years before or after CTEPH diagnosis. Twenty-seven patients died during the study period. Among them, 13 (48%) and 7 (26%) died of cancer and right heart failure, respectively. The 5-year survival rate was lower in the cancer group than in the non-cancer group (67.8% vs. 94.5%, p < 0.001). In the active cancer group, the 5-year survival rate was also lower than that in the non-active cancer and non-cancer groups (52.0% vs. 99.5%, p < 0.001 and 52.0% vs. 92.3%, p < 0.001, respectively). Multivariate Cox hazard analysis revealed that hemodialysis (p < 0.001) and cancer (p < 0.001) were independently associated with poor survival. Conclusion Patients with CTEPH rarely die of right heart failure, even if hemodynamically severe at diagnosis in the modern management era. However, patients with CTEPH frequently have comorbid cancer, which may be a strong prognostic factor.https://doi.org/10.1186/s12890-024-03460-5Chronic thromboembolic pulmonary hypertensionCancerPrognosisBalloon pulmonary angioplasty
spellingShingle Hiroyuki Fujii
Yu Taniguchi
Yuichi Tamura
Miki Sakamoto
Sachiyo Yoneda
Kenichi Yanaka
Noriaki Emoto
Ken-ichi Hirata
Hiromasa Otake
Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
BMC Pulmonary Medicine
Chronic thromboembolic pulmonary hypertension
Cancer
Prognosis
Balloon pulmonary angioplasty
title Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
title_full Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
title_fullStr Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
title_full_unstemmed Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
title_short Association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
title_sort association between the prognosis and comorbidity of active cancer in chronic thromboembolic pulmonary hypertension
topic Chronic thromboembolic pulmonary hypertension
Cancer
Prognosis
Balloon pulmonary angioplasty
url https://doi.org/10.1186/s12890-024-03460-5
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