What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.

Abstract Background Research and management of juvenile idiopathic arthritis (JIA) are challenging due to its heterogeneous nature, chronicity, and unpredictable, multidimensional long-term outcomes. Main body Long-term studies have consistently shown that a majority of children with JIA reach adult...

Full description

Saved in:
Bibliographic Details
Main Authors: Marite Rygg, Filipa Oliveira Ramos, Ellen Berit Nordal
Format: Article
Language:English
Published: BMC 2025-02-01
Series:Pediatric Rheumatology Online Journal
Subjects:
Online Access:https://doi.org/10.1186/s12969-025-01070-x
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849472441218236416
author Marite Rygg
Filipa Oliveira Ramos
Ellen Berit Nordal
author_facet Marite Rygg
Filipa Oliveira Ramos
Ellen Berit Nordal
author_sort Marite Rygg
collection DOAJ
description Abstract Background Research and management of juvenile idiopathic arthritis (JIA) are challenging due to its heterogeneous nature, chronicity, and unpredictable, multidimensional long-term outcomes. Main body Long-term studies have consistently shown that a majority of children with JIA reach adulthood with ongoing disease activity, on medication, or with recurrent flares. The heterogeneity is evident both between and within the present JIA categories based on The International League of Associations for Rheumatology (ILAR) JIA classification system. Several baseline predicting factors are known, but prediction modelling is only in the initial phase, and more models need to be tested in independent cohorts and possibly also supplemented with new biomarkers. Many have criticized the ILAR classification system, but new or updated classification systems have not yet been validated and proved their superiority. The lack of prediction possibilities for long-term outcomes and the limited alignment between JIA classification categories and adult rheumatic conditions are challenges for research, may limit the accessibility to treatment, and hamper a smooth transition to adult care. Conclusion We need more prospective, long-term studies based on unselected JIA cohorts with disease onset in the biologic era that can aid decision-making for individualized early treatment, suggest intervention studies, and ensure our patients the best possible transition to adulthood and the best likelihood of optimal health and quality of life.
format Article
id doaj-art-eb5edcdf5ceb47dd8e85a0a23fe42703
institution Kabale University
issn 1546-0096
language English
publishDate 2025-02-01
publisher BMC
record_format Article
series Pediatric Rheumatology Online Journal
spelling doaj-art-eb5edcdf5ceb47dd8e85a0a23fe427032025-08-20T03:24:32ZengBMCPediatric Rheumatology Online Journal1546-00962025-02-0123111010.1186/s12969-025-01070-xWhat have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.Marite Rygg0Filipa Oliveira Ramos1Ellen Berit Nordal2Department of Clinical and Molecular Medicine, Faculty of Medicine and Health Sciences (IKOM), Norwegian University of Science and Technology (NTNU)Pediatric Rheumatology Unit, Hospital Universitário ULS Santa MariaDepartment of Clinical Medicine, The Arctic University of Norway (UiT)Abstract Background Research and management of juvenile idiopathic arthritis (JIA) are challenging due to its heterogeneous nature, chronicity, and unpredictable, multidimensional long-term outcomes. Main body Long-term studies have consistently shown that a majority of children with JIA reach adulthood with ongoing disease activity, on medication, or with recurrent flares. The heterogeneity is evident both between and within the present JIA categories based on The International League of Associations for Rheumatology (ILAR) JIA classification system. Several baseline predicting factors are known, but prediction modelling is only in the initial phase, and more models need to be tested in independent cohorts and possibly also supplemented with new biomarkers. Many have criticized the ILAR classification system, but new or updated classification systems have not yet been validated and proved their superiority. The lack of prediction possibilities for long-term outcomes and the limited alignment between JIA classification categories and adult rheumatic conditions are challenges for research, may limit the accessibility to treatment, and hamper a smooth transition to adult care. Conclusion We need more prospective, long-term studies based on unselected JIA cohorts with disease onset in the biologic era that can aid decision-making for individualized early treatment, suggest intervention studies, and ensure our patients the best possible transition to adulthood and the best likelihood of optimal health and quality of life.https://doi.org/10.1186/s12969-025-01070-xJuvenile idiopathic arthritisAdultOutcomePredictionClassificationTransition
spellingShingle Marite Rygg
Filipa Oliveira Ramos
Ellen Berit Nordal
What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
Pediatric Rheumatology Online Journal
Juvenile idiopathic arthritis
Adult
Outcome
Prediction
Classification
Transition
title What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
title_full What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
title_fullStr What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
title_full_unstemmed What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
title_short What have we learned from long-term studies in juvenile idiopathic arthritis? – Prediction, classification, transition.
title_sort what have we learned from long term studies in juvenile idiopathic arthritis prediction classification transition
topic Juvenile idiopathic arthritis
Adult
Outcome
Prediction
Classification
Transition
url https://doi.org/10.1186/s12969-025-01070-x
work_keys_str_mv AT mariterygg whathavewelearnedfromlongtermstudiesinjuvenileidiopathicarthritispredictionclassificationtransition
AT filipaoliveiraramos whathavewelearnedfromlongtermstudiesinjuvenileidiopathicarthritispredictionclassificationtransition
AT ellenberitnordal whathavewelearnedfromlongtermstudiesinjuvenileidiopathicarthritispredictionclassificationtransition