Doença de Kennedy: Relato de dois casos Kennedy disease: report of two cases

Doença de Kennedy: Relato de dois casos Kennedy disease: report of two cases

Relatamos, pela primeira vez em nosso meio, dois pacientes com atrofia muscular bulbo espinhal de início tardio (doença de Kennedy), caracterizada por fraqueza, atrofia muscular, tremores e manifestações endocrinológicas, com sinais eletromiográficos de desnervação. Esta entidade diferencia-se das d...

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Bibliographic Details
Main Authors:	M. Seefeld, F. Marcos Cunha, Leila Elizabeth Ferraz, Rosana Herminia Scola, Lineu Cesar Werneck
Format:	Article
Language:	English
Published:	Thieme Revinter Publicações 1995-09-01
Series:	Arquivos de Neuro-Psiquiatria
Subjects:	doença de Kennedy doença do neurônio motor neuronopatia hereditária Kennedy disease motor neuron diseases hereditary neuronopathy
Online Access:	http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1995000300017
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