VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW

The steadily growing interest in studying of endocrine genetics is driven not only by the search for new pathologies but also by the most pressing need to develop methods for early diagnosis, treatment and management of patients. Though 20% of all the patients with von Hippel-Lindau syndrome do not...

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Main Authors: I. I. Larina, N. M. Platonova, E. A. Troshina, A. A. Roslyakova, D. G. Belzevich, L. S. Selivanova, M. Yu. Ukina, L. V. Nikankina, N. M. Malysheva, A. N. Tyulpakov, L. D. Kovalevich
Format: Article
Language:Russian
Published: SINAPS LLC 2019-05-01
Series:Архивъ внутренней медицины
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Online Access:https://www.medarhive.ru/jour/article/view/924
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author I. I. Larina
N. M. Platonova
E. A. Troshina
A. A. Roslyakova
D. G. Belzevich
L. S. Selivanova
M. Yu. Ukina
L. V. Nikankina
N. M. Malysheva
A. N. Tyulpakov
L. D. Kovalevich
author_facet I. I. Larina
N. M. Platonova
E. A. Troshina
A. A. Roslyakova
D. G. Belzevich
L. S. Selivanova
M. Yu. Ukina
L. V. Nikankina
N. M. Malysheva
A. N. Tyulpakov
L. D. Kovalevich
author_sort I. I. Larina
collection DOAJ
description The steadily growing interest in studying of endocrine genetics is driven not only by the search for new pathologies but also by the most pressing need to develop methods for early diagnosis, treatment and management of patients. Though 20% of all the patients with von Hippel-Lindau syndrome do not have a family history of the disease; a genetic basis is a natural characteristic of the disease and determinates a phenotype. Despite the nonaggressive course, in general, a relative unpredictability of the syndrome signs onset and the lack of regular monitoring can increase the risk of surgery complications and cause a disability at a young age. The presented clinical case shows the need for a multidisciplinary approach to management of the patients with von Hippel-Lindau syndrome.
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issn 2226-6704
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publishDate 2019-05-01
publisher SINAPS LLC
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series Архивъ внутренней медицины
spelling doaj-art-e962004f23b54a6084f19400f8fddd282025-08-20T03:00:39ZrusSINAPS LLCАрхивъ внутренней медицины2226-67042411-65642019-05-019316517110.20514/2226-6704-2019-9-3-165-171731VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEWI. I. Larina0N. M. Platonova1E. A. Troshina2A. A. Roslyakova3D. G. Belzevich4L. S. Selivanova5M. Yu. Ukina6L. V. Nikankina7N. M. Malysheva8A. N. Tyulpakov9L. D. Kovalevich10Endocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreEndocrinology research centreThe steadily growing interest in studying of endocrine genetics is driven not only by the search for new pathologies but also by the most pressing need to develop methods for early diagnosis, treatment and management of patients. Though 20% of all the patients with von Hippel-Lindau syndrome do not have a family history of the disease; a genetic basis is a natural characteristic of the disease and determinates a phenotype. Despite the nonaggressive course, in general, a relative unpredictability of the syndrome signs onset and the lack of regular monitoring can increase the risk of surgery complications and cause a disability at a young age. The presented clinical case shows the need for a multidisciplinary approach to management of the patients with von Hippel-Lindau syndrome.https://www.medarhive.ru/jour/article/view/924facomatosisvon hippel-lindau syndromepheochromocytomahemangioblastomavhl
spellingShingle I. I. Larina
N. M. Platonova
E. A. Troshina
A. A. Roslyakova
D. G. Belzevich
L. S. Selivanova
M. Yu. Ukina
L. V. Nikankina
N. M. Malysheva
A. N. Tyulpakov
L. D. Kovalevich
VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
Архивъ внутренней медицины
facomatosis
von hippel-lindau syndrome
pheochromocytoma
hemangioblastoma
vhl
title VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
title_full VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
title_fullStr VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
title_full_unstemmed VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
title_short VON HIPPEL-LINDAU SYNDROME: ASPECTS OF TREATMENT AND MANAGEMENT. CASE REPORT AND LITERATURE REVIEW
title_sort von hippel lindau syndrome aspects of treatment and management case report and literature review
topic facomatosis
von hippel-lindau syndrome
pheochromocytoma
hemangioblastoma
vhl
url https://www.medarhive.ru/jour/article/view/924
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