Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases

Introduction Fumarate hydratase (FH)-deficient renal cell carcinoma (RCC) is a rare, molecularly defined renal tumor with aggressive behavior. The diagnosis of these tumors is challenging because of varied morphology and limited access to molecular testing and immunohistochemistry (IHC) f...

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Main Authors: Aswathy A. Menon, Swapnil Rane, Uma Sakhadeo, Gagan Prakash, Amit Joshi, Mahendra Pal, Amandeep Arora, Nilesh Sable, Aparna Katdare, Palak Popat, Priyamvada Maitre, Archi Agarwal, Vedang Murthy, Sangeetha B. Desai, Santosh Menon
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2024-12-01
Series:Indian Journal of Medical and Paediatric Oncology
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Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0043-1775804
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author Aswathy A. Menon
Swapnil Rane
Uma Sakhadeo
Gagan Prakash
Amit Joshi
Mahendra Pal
Amandeep Arora
Nilesh Sable
Aparna Katdare
Palak Popat
Priyamvada Maitre
Archi Agarwal
Vedang Murthy
Sangeetha B. Desai
Santosh Menon
author_facet Aswathy A. Menon
Swapnil Rane
Uma Sakhadeo
Gagan Prakash
Amit Joshi
Mahendra Pal
Amandeep Arora
Nilesh Sable
Aparna Katdare
Palak Popat
Priyamvada Maitre
Archi Agarwal
Vedang Murthy
Sangeetha B. Desai
Santosh Menon
author_sort Aswathy A. Menon
collection DOAJ
description Introduction Fumarate hydratase (FH)-deficient renal cell carcinoma (RCC) is a rare, molecularly defined renal tumor with aggressive behavior. The diagnosis of these tumors is challenging because of varied morphology and limited access to molecular testing and immunohistochemistry (IHC) for FH and 2-succinocysteine. We aim to elucidate the histomorphology, clinical presentation, and follow-up of this tumor in this first series of cases of FH-deficient RCCs from India.
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institution OA Journals
issn 0971-5851
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language English
publishDate 2024-12-01
publisher Thieme Medical and Scientific Publishers Pvt. Ltd.
record_format Article
series Indian Journal of Medical and Paediatric Oncology
spelling doaj-art-e95621eda32843b5a9d062a03185721e2025-08-20T02:22:34ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58510975-21292024-12-01450650250810.1055/s-0043-1775804Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 CasesAswathy A. Menon0https://orcid.org/0000-0002-1363-7073Swapnil Rane1https://orcid.org/0000-0002-5374-3903Uma Sakhadeo2Gagan Prakash3https://orcid.org/0000-0003-1722-4337Amit Joshi4Mahendra Pal5Amandeep Arora6Nilesh Sable7Aparna Katdare8Palak Popat9Priyamvada Maitre10Archi Agarwal11Vedang Murthy12Sangeetha B. Desai13https://orcid.org/0000-0002-3588-9888Santosh Menon14https://orcid.org/0000-0002-4140-0671Department of Pathology, Neuberg Anand Reference Laboratory, Bengaluru, Karnataka, IndiaDepartment of Pathology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Pathology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Urology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Medical Oncology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Urology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Urology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Radiodiagnosis, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Radiodiagnosis, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Radiodiagnosis, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Radiation Oncology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Nuclear Medicine, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Radiation Oncology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Pathology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, IndiaDepartment of Pathology, Tata Memorial Hospital, Homi Bhabha National Institute, Mumbai, Maharashtra, India Introduction Fumarate hydratase (FH)-deficient renal cell carcinoma (RCC) is a rare, molecularly defined renal tumor with aggressive behavior. The diagnosis of these tumors is challenging because of varied morphology and limited access to molecular testing and immunohistochemistry (IHC) for FH and 2-succinocysteine. We aim to elucidate the histomorphology, clinical presentation, and follow-up of this tumor in this first series of cases of FH-deficient RCCs from India.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0043-1775804fumarate hydratase-deficient renal cell carcinomafumarate hydrataseRCCFH IHCHLRCC
spellingShingle Aswathy A. Menon
Swapnil Rane
Uma Sakhadeo
Gagan Prakash
Amit Joshi
Mahendra Pal
Amandeep Arora
Nilesh Sable
Aparna Katdare
Palak Popat
Priyamvada Maitre
Archi Agarwal
Vedang Murthy
Sangeetha B. Desai
Santosh Menon
Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
Indian Journal of Medical and Paediatric Oncology
fumarate hydratase-deficient renal cell carcinoma
fumarate hydratase
RCC
FH IHC
HLRCC
title Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
title_full Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
title_fullStr Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
title_full_unstemmed Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
title_short Fumarate Hydratase-Deficient Renal Cell Carcinoma—A Clinicopathological Study of a Series of 11 Cases
title_sort fumarate hydratase deficient renal cell carcinoma a clinicopathological study of a series of 11 cases
topic fumarate hydratase-deficient renal cell carcinoma
fumarate hydratase
RCC
FH IHC
HLRCC
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0043-1775804
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