Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas

Epidermodysplasia verruciformis (EV) is a rare genodermatosis characterized by chronic infection with human papillomavirus (HPV), leading to disseminated flat-topped papules and pityriasis versicolor-like lesions. Patients with EV are predisposed to developing non-melanoma skin cancers, particularly...

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Main Authors: Zijing Zhang, Chuanbo Liu, Jinsheng Li
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Medicine
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Online Access:https://www.frontiersin.org/articles/10.3389/fmed.2025.1565977/full
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author Zijing Zhang
Chuanbo Liu
Jinsheng Li
author_facet Zijing Zhang
Chuanbo Liu
Jinsheng Li
author_sort Zijing Zhang
collection DOAJ
description Epidermodysplasia verruciformis (EV) is a rare genodermatosis characterized by chronic infection with human papillomavirus (HPV), leading to disseminated flat-topped papules and pityriasis versicolor-like lesions. Patients with EV are predisposed to developing non-melanoma skin cancers, particularly squamous cell carcinoma (SCC) in sun-exposed areas. Currently, there is no definitive cure for EV, and management remains largely supportive and symptomatic. We report a case of EV in a 38-year-old male, presenting with classical clinical features and histopathological findings, complicated by the simultaneous development of squamous cell carcinoma(SCC) and basal cell carcinoma (BCC). This case highlights the oncogenic potential of EV-associated HPV subtypes and the importance of regular dermatologic surveillance in affected individuals.
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spelling doaj-art-e7fa29bd87d44c7dbba287d05d2800ff2025-08-20T02:03:04ZengFrontiers Media S.A.Frontiers in Medicine2296-858X2025-06-011210.3389/fmed.2025.15659771565977Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomasZijing Zhang0Chuanbo Liu1Jinsheng Li2The Fourth Clinical Medical College, Zhejiang Chinese Medicine University, Hangzhou, ChinaDepartment of Plastic and Cosmetic Surgery, Affiliated Hangzhou First People's Hospital, Hangzhou, Zhejiang, ChinaDepartment of Plastic and Cosmetic Surgery, Affiliated Hangzhou First People's Hospital, Hangzhou, Zhejiang, ChinaEpidermodysplasia verruciformis (EV) is a rare genodermatosis characterized by chronic infection with human papillomavirus (HPV), leading to disseminated flat-topped papules and pityriasis versicolor-like lesions. Patients with EV are predisposed to developing non-melanoma skin cancers, particularly squamous cell carcinoma (SCC) in sun-exposed areas. Currently, there is no definitive cure for EV, and management remains largely supportive and symptomatic. We report a case of EV in a 38-year-old male, presenting with classical clinical features and histopathological findings, complicated by the simultaneous development of squamous cell carcinoma(SCC) and basal cell carcinoma (BCC). This case highlights the oncogenic potential of EV-associated HPV subtypes and the importance of regular dermatologic surveillance in affected individuals.https://www.frontiersin.org/articles/10.3389/fmed.2025.1565977/fullepidermodysplasia verruciformissquamous cell carcinomabasal cell carcinomahistopathological examinationmalignancy
spellingShingle Zijing Zhang
Chuanbo Liu
Jinsheng Li
Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
Frontiers in Medicine
epidermodysplasia verruciformis
squamous cell carcinoma
basal cell carcinoma
histopathological examination
malignancy
title Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
title_full Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
title_fullStr Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
title_full_unstemmed Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
title_short Case Report: Epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
title_sort case report epidermodysplasia verruciformis with multiple squamous and basal cell carcinomas
topic epidermodysplasia verruciformis
squamous cell carcinoma
basal cell carcinoma
histopathological examination
malignancy
url https://www.frontiersin.org/articles/10.3389/fmed.2025.1565977/full
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