Cohort profile: the National Congenital Anomaly Registration Dataset in England

Purpose The National Congenital Anomaly and Rare Disease Registration Service (NCARDRS), part of National Disease Registration Service in National Health Service England, quality assures, curates and analyses individual data on the pregnancies, fetuses, babies, children and adults with congenital an...

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Main Authors: Danielle Martin, Sarah Stevens, John Broggio, Chloe Johnson, Kate M Fleming, Ben Wreyford, Sylvia Stoianova, Gabriella Melis, Ewoma Obaro, Jennifer M. Broughan, Kay Randall, Nicholas Aldridge, Donna Gibbard
Format: Article
Language:English
Published: BMJ Publishing Group 2024-01-01
Series:BMJ Open
Online Access:https://bmjopen.bmj.com/content/14/1/e077743.full
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author Danielle Martin
Sarah Stevens
John Broggio
Chloe Johnson
Kate M Fleming
Ben Wreyford
Sylvia Stoianova
Gabriella Melis
Ewoma Obaro
Jennifer M. Broughan
Kay Randall
Nicholas Aldridge
Donna Gibbard
author_facet Danielle Martin
Sarah Stevens
John Broggio
Chloe Johnson
Kate M Fleming
Ben Wreyford
Sylvia Stoianova
Gabriella Melis
Ewoma Obaro
Jennifer M. Broughan
Kay Randall
Nicholas Aldridge
Donna Gibbard
author_sort Danielle Martin
collection DOAJ
description Purpose The National Congenital Anomaly and Rare Disease Registration Service (NCARDRS), part of National Disease Registration Service in National Health Service England, quality assures, curates and analyses individual data on the pregnancies, fetuses, babies, children and adults with congenital anomalies and rare diseases across England. The congenital anomaly (CA) register provides a resource for patients and their families, clinicians, researchers and public health professionals in furthering the understanding of CAs.Participants NCARDRS registers CAs occurring in babies born alive and stillborn, fetal losses and terminations in England. NCARDRS collects data from secondary and tertiary healthcare providers, private providers and laboratories covering fetal medicine, maternity or paediatric services. Data describe the pregnancy, mother, baby and anomaly. Established in 2015, NCARDRS expanded CA registration coverage from 22% of total births in England in 2015 to national coverage, which was achieved in 2018. Prior to 2015, data collection was performed independently by regional registers in England; these data are also held by NCARDRS.Findings to date NCARDRS registers approximately 21 000 babies with CAs per year with surveillance covering around 600 000 total births, the largest birth coverage for a CA register globally. Data on prevalence, risk factors and survival for children with CAs are available. Data have been used in several peer-reviewed publications. Birth prevalence statistics, including public health indicators such as the association with maternal age, infant and perinatal mortality, are published annually. NCARDRS supports clinical audit for screening programmes and service evaluation.Future plans NCARDRS provides a valuable resource for the understanding of the epidemiology, surveillance, prevention and treatment of CAs. Currently, approximately 21 000 new registrations of babies or fetuses with suspected or confirmed CAs are added each year. Identifiers are collected, enabling linkage to routinely collected healthcare and population statistics, further enhancing the value of the data.
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spelling doaj-art-e782a79e9fe9433c9bf966ae09c2aef22025-08-20T03:12:40ZengBMJ Publishing GroupBMJ Open2044-60552024-01-0114110.1136/bmjopen-2023-077743Cohort profile: the National Congenital Anomaly Registration Dataset in EnglandDanielle Martin0Sarah Stevens1John Broggio2Chloe Johnson3Kate M Fleming4Ben Wreyford5Sylvia Stoianova6Gabriella Melis7Ewoma Obaro8Jennifer M. Broughan9Kay Randall10Nicholas Aldridge11Donna Gibbard12National Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, England2Aligos Therapeutics, Inc., South San Francisco, CA, USANational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandUniversity of Bristol, Bristol, UKNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandNational Disease Registration Service, Data & Analytics, Transformation Directorate, NHS England, Leeds, EnglandPurpose The National Congenital Anomaly and Rare Disease Registration Service (NCARDRS), part of National Disease Registration Service in National Health Service England, quality assures, curates and analyses individual data on the pregnancies, fetuses, babies, children and adults with congenital anomalies and rare diseases across England. The congenital anomaly (CA) register provides a resource for patients and their families, clinicians, researchers and public health professionals in furthering the understanding of CAs.Participants NCARDRS registers CAs occurring in babies born alive and stillborn, fetal losses and terminations in England. NCARDRS collects data from secondary and tertiary healthcare providers, private providers and laboratories covering fetal medicine, maternity or paediatric services. Data describe the pregnancy, mother, baby and anomaly. Established in 2015, NCARDRS expanded CA registration coverage from 22% of total births in England in 2015 to national coverage, which was achieved in 2018. Prior to 2015, data collection was performed independently by regional registers in England; these data are also held by NCARDRS.Findings to date NCARDRS registers approximately 21 000 babies with CAs per year with surveillance covering around 600 000 total births, the largest birth coverage for a CA register globally. Data on prevalence, risk factors and survival for children with CAs are available. Data have been used in several peer-reviewed publications. Birth prevalence statistics, including public health indicators such as the association with maternal age, infant and perinatal mortality, are published annually. NCARDRS supports clinical audit for screening programmes and service evaluation.Future plans NCARDRS provides a valuable resource for the understanding of the epidemiology, surveillance, prevention and treatment of CAs. Currently, approximately 21 000 new registrations of babies or fetuses with suspected or confirmed CAs are added each year. Identifiers are collected, enabling linkage to routinely collected healthcare and population statistics, further enhancing the value of the data.https://bmjopen.bmj.com/content/14/1/e077743.full
spellingShingle Danielle Martin
Sarah Stevens
John Broggio
Chloe Johnson
Kate M Fleming
Ben Wreyford
Sylvia Stoianova
Gabriella Melis
Ewoma Obaro
Jennifer M. Broughan
Kay Randall
Nicholas Aldridge
Donna Gibbard
Cohort profile: the National Congenital Anomaly Registration Dataset in England
BMJ Open
title Cohort profile: the National Congenital Anomaly Registration Dataset in England
title_full Cohort profile: the National Congenital Anomaly Registration Dataset in England
title_fullStr Cohort profile: the National Congenital Anomaly Registration Dataset in England
title_full_unstemmed Cohort profile: the National Congenital Anomaly Registration Dataset in England
title_short Cohort profile: the National Congenital Anomaly Registration Dataset in England
title_sort cohort profile the national congenital anomaly registration dataset in england
url https://bmjopen.bmj.com/content/14/1/e077743.full
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