Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil

ABSTRACT Data about pulmonary arterial hypertension (PAH) patients living in low‐ and middle‐income countries remain scarce. This study assessed prognostic factors associated with time to clinical worsening (CW) or death of a cohort of PAH patients in Minas Gerais, Brazil. This retrospective cohort...

Full description

Saved in:
Bibliographic Details
Main Authors: Ricardo Amorim Correa, Camila Farnese Rezende, Eliane Viana Mancuzo, Claudia Mickael, Camila M. C. Loureiro, Rudolf K. F. Oliveira, Joan F. Hilton, Brian B. Graham
Format: Article
Language:English
Published: Wiley 2025-04-01
Series:Pulmonary Circulation
Subjects:
Online Access:https://doi.org/10.1002/pul2.70086
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849426748315271168
author Ricardo Amorim Correa
Camila Farnese Rezende
Eliane Viana Mancuzo
Claudia Mickael
Camila M. C. Loureiro
Rudolf K. F. Oliveira
Joan F. Hilton
Brian B. Graham
author_facet Ricardo Amorim Correa
Camila Farnese Rezende
Eliane Viana Mancuzo
Claudia Mickael
Camila M. C. Loureiro
Rudolf K. F. Oliveira
Joan F. Hilton
Brian B. Graham
author_sort Ricardo Amorim Correa
collection DOAJ
description ABSTRACT Data about pulmonary arterial hypertension (PAH) patients living in low‐ and middle‐income countries remain scarce. This study assessed prognostic factors associated with time to clinical worsening (CW) or death of a cohort of PAH patients in Minas Gerais, Brazil. This retrospective cohort study describes baseline clinical variables by PAH etiology and estimates time from diagnosis to CW [all‐cause death, any‐cause hospitalization, or disease progression (decrease of ≥ 15% in 6MWD and need for additional PAH therapy or worsening of functional class (FC)] and time to death. 79 out of 102 participants developed CW and 38 died while under follow‐up. The most prevalent etiologies were PAH associated with schistosomiasis (PAH‐Sch), idiopathic (IPAH), with congenital heart disease (PAH‐CHD), and with connective tissue disease (PAH‐CTD). The overall median event‐free time to CW was 3.3 (95% CI, 2.3–4.6) years, which was similar across etiologies (log‐rank test: p = 0.12). WHO FC III‐IV, DLCO < 70%, heart rate recovery in 1 min after the 6‐min walk test (HRR1) < 18 beats/minute, and baseline mPAP ≥ 50 mmHg were predictive of CW‐free time. The median time to all‐cause mortality was 10.2 (95% CI, 6.8 – > 10) years and varied among etiologies (log‐rank test: p < 0.001). Time to CW was statistically independent of PAH etiology but depended on baseline WHO FC, DLCO, HRR, and mPAP. After CW events, PAH‐Sch and PAH‐CTD survived less on average than IPAH and PAH‐CHD participants.
format Article
id doaj-art-e72b40297d0242fc9479c08445cf748c
institution Kabale University
issn 2045-8940
language English
publishDate 2025-04-01
publisher Wiley
record_format Article
series Pulmonary Circulation
spelling doaj-art-e72b40297d0242fc9479c08445cf748c2025-08-20T03:29:15ZengWileyPulmonary Circulation2045-89402025-04-01152n/an/a10.1002/pul2.70086Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of BrazilRicardo Amorim Correa0Camila Farnese Rezende1Eliane Viana Mancuzo2Claudia Mickael3Camila M. C. Loureiro4Rudolf K. F. Oliveira5Joan F. Hilton6Brian B. Graham7Medical School, Hospital das Clínicas, Pulmonary Vascular Diseases Section Federal University of Minas Gerais Belo Horizonte Minas Gerais BrazilHospital das Clínicas Federal University of Minas Gerais, Pulmonary Vascular Diseases Section Belo Horizonte Minas Gerais BrazilMedical School, Hospital das Clínicas, Pulmonary Vascular Diseases Section Federal University of Minas Gerais Belo Horizonte Minas Gerais BrazilPulmonary and Critical Care Medicine University of Colorado Anschutz Medical, Campus Aurora Colorado USAPulmonary Medicine Santa Casa Hospital Salvador Bahia BrazilDepartment of Medicine, Division of Respiratory Diseases Federal University of São Paulo São Paulo BrazilDepartment of Epidemiology and Biostatistics University of California San Francisco San Francisco California USADepartment of Medicine, Division of Pulmonary and Critical Care Medicine University of California San Francisco San Francisco California USAABSTRACT Data about pulmonary arterial hypertension (PAH) patients living in low‐ and middle‐income countries remain scarce. This study assessed prognostic factors associated with time to clinical worsening (CW) or death of a cohort of PAH patients in Minas Gerais, Brazil. This retrospective cohort study describes baseline clinical variables by PAH etiology and estimates time from diagnosis to CW [all‐cause death, any‐cause hospitalization, or disease progression (decrease of ≥ 15% in 6MWD and need for additional PAH therapy or worsening of functional class (FC)] and time to death. 79 out of 102 participants developed CW and 38 died while under follow‐up. The most prevalent etiologies were PAH associated with schistosomiasis (PAH‐Sch), idiopathic (IPAH), with congenital heart disease (PAH‐CHD), and with connective tissue disease (PAH‐CTD). The overall median event‐free time to CW was 3.3 (95% CI, 2.3–4.6) years, which was similar across etiologies (log‐rank test: p = 0.12). WHO FC III‐IV, DLCO < 70%, heart rate recovery in 1 min after the 6‐min walk test (HRR1) < 18 beats/minute, and baseline mPAP ≥ 50 mmHg were predictive of CW‐free time. The median time to all‐cause mortality was 10.2 (95% CI, 6.8 – > 10) years and varied among etiologies (log‐rank test: p < 0.001). Time to CW was statistically independent of PAH etiology but depended on baseline WHO FC, DLCO, HRR, and mPAP. After CW events, PAH‐Sch and PAH‐CTD survived less on average than IPAH and PAH‐CHD participants.https://doi.org/10.1002/pul2.70086pulmonary arterial hypertensionrisk factorsschistosomiasissurvival
spellingShingle Ricardo Amorim Correa
Camila Farnese Rezende
Eliane Viana Mancuzo
Claudia Mickael
Camila M. C. Loureiro
Rudolf K. F. Oliveira
Joan F. Hilton
Brian B. Graham
Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
Pulmonary Circulation
pulmonary arterial hypertension
risk factors
schistosomiasis
survival
title Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
title_full Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
title_fullStr Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
title_full_unstemmed Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
title_short Morbidity and Mortality Associated With Pulmonary Arterial Hypertension in a Schistosomiasis‐Endemic Region of Brazil
title_sort morbidity and mortality associated with pulmonary arterial hypertension in a schistosomiasis endemic region of brazil
topic pulmonary arterial hypertension
risk factors
schistosomiasis
survival
url https://doi.org/10.1002/pul2.70086
work_keys_str_mv AT ricardoamorimcorrea morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT camilafarneserezende morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT elianevianamancuzo morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT claudiamickael morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT camilamcloureiro morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT rudolfkfoliveira morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT joanfhilton morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil
AT brianbgraham morbidityandmortalityassociatedwithpulmonaryarterialhypertensioninaschistosomiasisendemicregionofbrazil