Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report
Introduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reco...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações Ltda.
2022-06-01
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| Series: | Revista Brasileira de Cirurgia Plástica |
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| Online Access: | http://www.rbcp.org.br/export-pdf/3136/en_v37n2a18.pdf |
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| author | João Roberto Farias de Souza Maria Luiza Marialva Rodrigues Sérgio Antônio Saldanha Rodrigues Tamborini Lívia Dornelas Côrrea Clarissa Leite Turrer Armando Chiari |
| author_facet | João Roberto Farias de Souza Maria Luiza Marialva Rodrigues Sérgio Antônio Saldanha Rodrigues Tamborini Lívia Dornelas Côrrea Clarissa Leite Turrer Armando Chiari |
| author_sort | João Roberto Farias de Souza |
| collection | DOAJ |
| description | Introduction:
Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage.
Case Report:
A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reconstruction with local flaps and skin graft were performed.
Discussion:
Milroy disease is a rare autosomal dominant disease. The clinical presentation is progressive and results from hypoplasia of the lymphatic vessels of the lower limbs. Treatment in advanced cases is mainly surgical.
Conclusion:
In the case of a patient with Milroy disease and severe penoscrotal lymphedema, surgical treatment is a good option. The use of parascrotal flaps for scrotoplasty associated with a graft to recover the penis provides a good functional result. |
| format | Article |
| id | doaj-art-e71f5b2cf8f04bca8d7ba0fc3ed98bb8 |
| institution | DOAJ |
| issn | 1983-5175 2177-1235 |
| language | English |
| publishDate | 2022-06-01 |
| publisher | Thieme Revinter Publicações Ltda. |
| record_format | Article |
| series | Revista Brasileira de Cirurgia Plástica |
| spelling | doaj-art-e71f5b2cf8f04bca8d7ba0fc3ed98bb82025-08-20T02:51:45ZengThieme Revinter Publicações Ltda.Revista Brasileira de Cirurgia Plástica1983-51752177-12352022-06-01370225025510.5935/2177-1235.2022RBCP0040Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case reportJoão Roberto Farias de Souza0Maria Luiza Marialva Rodrigues1Sérgio Antônio Saldanha Rodrigues Tamborini2Lívia Dornelas Côrrea3Clarissa Leite Turrer4Armando Chiari5Faculdade Ciências Médicas de Minas Gerais, Belo Horizonte, MG, BrazilUniversidade do Estado do Amazonas, Manaus, AM, BrazilUniversidade Federal de Minas Gerais, Hospital das Clínicas, Belo Horizonte, MG, BrazilUniversidade Federal de Minas Gerais, Hospital das Clínicas, Belo Horizonte, MG, BrazilUniversidade Federal de Minas Gerais, Hospital das Clínicas, Belo Horizonte, MG, BrazilUniversidade Federal de Minas Gerais, Hospital das Clínicas, Belo Horizonte, MG, BrazilIntroduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reconstruction with local flaps and skin graft were performed. Discussion: Milroy disease is a rare autosomal dominant disease. The clinical presentation is progressive and results from hypoplasia of the lymphatic vessels of the lower limbs. Treatment in advanced cases is mainly surgical. Conclusion: In the case of a patient with Milroy disease and severe penoscrotal lymphedema, surgical treatment is a good option. The use of parascrotal flaps for scrotoplasty associated with a graft to recover the penis provides a good functional result.http://www.rbcp.org.br/export-pdf/3136/en_v37n2a18.pdflymphedemascrotumreconstructive surgical proceduresurologic surgical proceduresmalegenital diseases, malecongenital abnormalities |
| spellingShingle | João Roberto Farias de Souza Maria Luiza Marialva Rodrigues Sérgio Antônio Saldanha Rodrigues Tamborini Lívia Dornelas Côrrea Clarissa Leite Turrer Armando Chiari Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report Revista Brasileira de Cirurgia Plástica lymphedema scrotum reconstructive surgical procedures urologic surgical procedures male genital diseases, male congenital abnormalities |
| title | Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report |
| title_full | Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report |
| title_fullStr | Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report |
| title_full_unstemmed | Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report |
| title_short | Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report |
| title_sort | surgical treatment of penoscrotal lymphedema in a patient with milroy s disease case report |
| topic | lymphedema scrotum reconstructive surgical procedures urologic surgical procedures male genital diseases, male congenital abnormalities |
| url | http://www.rbcp.org.br/export-pdf/3136/en_v37n2a18.pdf |
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