Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy o...
Saved in:
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wiley
2011-01-01
|
| Series: | Case Reports in Hematology |
| Online Access: | http://dx.doi.org/10.1155/2011/941637 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850167559386562560 |
|---|---|
| author | Peter G. Pavlidakey Alok Mohanty Lisa J. Kohler Howard J. Meyerson |
| author_facet | Peter G. Pavlidakey Alok Mohanty Lisa J. Kohler Howard J. Meyerson |
| author_sort | Peter G. Pavlidakey |
| collection | DOAJ |
| description | Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma. |
| format | Article |
| id | doaj-art-e712c8680b7e4172b5f9a7f79b6d3152 |
| institution | OA Journals |
| issn | 2090-6560 2090-6579 |
| language | English |
| publishDate | 2011-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hematology |
| spelling | doaj-art-e712c8680b7e4172b5f9a7f79b6d31522025-08-20T02:21:10ZengWileyCase Reports in Hematology2090-65602090-65792011-01-01201110.1155/2011/941637941637Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal ProteinemiaPeter G. Pavlidakey0Alok Mohanty1Lisa J. Kohler2Howard J. Meyerson3Department of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USADepartment of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USAOffice of the Summit Count Medical Examiner, 85 N. Summit St., Akron, OH 44308-1948, USADepartment of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USAErdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma.http://dx.doi.org/10.1155/2011/941637 |
| spellingShingle | Peter G. Pavlidakey Alok Mohanty Lisa J. Kohler Howard J. Meyerson Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia Case Reports in Hematology |
| title | Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia |
| title_full | Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia |
| title_fullStr | Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia |
| title_full_unstemmed | Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia |
| title_short | Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia |
| title_sort | erdheim chester disease associated with marginal zone lymphoma and monoclonal proteinemia |
| url | http://dx.doi.org/10.1155/2011/941637 |
| work_keys_str_mv | AT petergpavlidakey erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia AT alokmohanty erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia AT lisajkohler erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia AT howardjmeyerson erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia |