Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease
Systemic onset juvenile idiopathic arthritis (SoJIA) is characterized by arthritis, fever and visceral organ involvement including hepatosplenomegaly, lympadenopathy and serositis. This is a case of SoJIA misdiagnosed as Kawasaki disease (KD) and developed machrophage activation syndrome (MAS...
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| Format: | Article |
| Language: | English |
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Hacettepe University Institute of Child Health
2015-10-01
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| Series: | The Turkish Journal of Pediatrics |
| Online Access: | https://turkjpediatr.org/article/view/1278 |
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| _version_ | 1850236821096628224 |
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| author | Gonca Keskindemirci Nuray Aktay Ayaz Neslihan Melikoğlu Helen Bornaun Çiğdem Aydoğmuş Esin Aldemir Gönül Aydoğan |
| author_facet | Gonca Keskindemirci Nuray Aktay Ayaz Neslihan Melikoğlu Helen Bornaun Çiğdem Aydoğmuş Esin Aldemir Gönül Aydoğan |
| author_sort | Gonca Keskindemirci |
| collection | DOAJ |
| description |
Systemic onset juvenile idiopathic arthritis (SoJIA) is characterized by arthritis, fever and visceral organ involvement including hepatosplenomegaly, lympadenopathy and serositis. This is a case of SoJIA misdiagnosed as Kawasaki disease (KD) and developed machrophage activation syndrome (MAS) secondary to Ebstein-Barr virus (EBV) infection. It is presented to point out the conditions that may come along. First of all, SoJIA should be kept in mind while making the differential diagnosis of coronary arterial ectasias and dilatations usually seen in vasculitic diseases like KD. Second, as a very fatal complication MAS should always be considered while following a patient with the diagnosis of SoJIA. Infections like EBV may be the potential triggers for development of MAS especially in immunesupressed patients.
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| format | Article |
| id | doaj-art-e6eb589539e9402689a3fef1e2216d67 |
| institution | OA Journals |
| issn | 0041-4301 2791-6421 |
| language | English |
| publishDate | 2015-10-01 |
| publisher | Hacettepe University Institute of Child Health |
| record_format | Article |
| series | The Turkish Journal of Pediatrics |
| spelling | doaj-art-e6eb589539e9402689a3fef1e2216d672025-08-20T02:01:53ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212015-10-01575Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki diseaseGonca Keskindemirci0Nuray Aktay AyazNeslihan MelikoğluHelen BornaunÇiğdem AydoğmuşEsin AldemirGönül AydoğanDivision of Pediatric Rheumatology, İstanbul Kanuni Sultan Süleyman Training and Research Hospital, İstanbul, Turkey. keskindemirci@hotmail.com. Systemic onset juvenile idiopathic arthritis (SoJIA) is characterized by arthritis, fever and visceral organ involvement including hepatosplenomegaly, lympadenopathy and serositis. This is a case of SoJIA misdiagnosed as Kawasaki disease (KD) and developed machrophage activation syndrome (MAS) secondary to Ebstein-Barr virus (EBV) infection. It is presented to point out the conditions that may come along. First of all, SoJIA should be kept in mind while making the differential diagnosis of coronary arterial ectasias and dilatations usually seen in vasculitic diseases like KD. Second, as a very fatal complication MAS should always be considered while following a patient with the diagnosis of SoJIA. Infections like EBV may be the potential triggers for development of MAS especially in immunesupressed patients. https://turkjpediatr.org/article/view/1278 |
| spellingShingle | Gonca Keskindemirci Nuray Aktay Ayaz Neslihan Melikoğlu Helen Bornaun Çiğdem Aydoğmuş Esin Aldemir Gönül Aydoğan Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease The Turkish Journal of Pediatrics |
| title | Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease |
| title_full | Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease |
| title_fullStr | Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease |
| title_full_unstemmed | Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease |
| title_short | Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as Kawasaki disease |
| title_sort | systemic onset juvenile idiopathic arthritis with macrophage activation syndrome and coronary artery dilatation misdiagnosed as kawasaki disease |
| url | https://turkjpediatr.org/article/view/1278 |
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