Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series
Congenital aniridia is a rare genetic eye disorder often associated with PAX6 gene mutations, leading to complex ocular manifestations, including aniridia-associated keratopathy (AAK) and cataracts. The surgical management of cataracts in these patients is particularly challenging due to severe corn...
Saved in:
| Main Authors: | , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
SAGE Publishing
2024-11-01
|
| Series: | Therapeutic Advances in Ophthalmology |
| Online Access: | https://doi.org/10.1177/25158414241302879 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850065253993283584 |
|---|---|
| author | Joseph Hu Chao-Chien Hu |
| author_facet | Joseph Hu Chao-Chien Hu |
| author_sort | Joseph Hu |
| collection | DOAJ |
| description | Congenital aniridia is a rare genetic eye disorder often associated with PAX6 gene mutations, leading to complex ocular manifestations, including aniridia-associated keratopathy (AAK) and cataracts. The surgical management of cataracts in these patients is particularly challenging due to severe corneal opacities, which obscure key surgical steps such as capsulorhexis and phacoemulsification. This report presents two cases of congenital aniridia with severe AAK, in which chandelier retroillumination-assisted cataract surgery was employed. This technique, typically used in vitreous surgery, provided enhanced visualization of the lens through posterior segment illumination, facilitating successful cataract extraction and intraocular lens implantation. Both patients showed significant postoperative improvement in visual acuity. These cases demonstrate the feasibility and effectiveness of chandelier retroillumination-assisted cataract surgery in patients with congenital aniridia complicated by severe corneal opacity. |
| format | Article |
| id | doaj-art-e61dd5ffc6894e18a806c784ab9d97eb |
| institution | DOAJ |
| issn | 2515-8414 |
| language | English |
| publishDate | 2024-11-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Therapeutic Advances in Ophthalmology |
| spelling | doaj-art-e61dd5ffc6894e18a806c784ab9d97eb2025-08-20T02:49:04ZengSAGE PublishingTherapeutic Advances in Ophthalmology2515-84142024-11-011610.1177/25158414241302879Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case seriesJoseph HuChao-Chien HuCongenital aniridia is a rare genetic eye disorder often associated with PAX6 gene mutations, leading to complex ocular manifestations, including aniridia-associated keratopathy (AAK) and cataracts. The surgical management of cataracts in these patients is particularly challenging due to severe corneal opacities, which obscure key surgical steps such as capsulorhexis and phacoemulsification. This report presents two cases of congenital aniridia with severe AAK, in which chandelier retroillumination-assisted cataract surgery was employed. This technique, typically used in vitreous surgery, provided enhanced visualization of the lens through posterior segment illumination, facilitating successful cataract extraction and intraocular lens implantation. Both patients showed significant postoperative improvement in visual acuity. These cases demonstrate the feasibility and effectiveness of chandelier retroillumination-assisted cataract surgery in patients with congenital aniridia complicated by severe corneal opacity.https://doi.org/10.1177/25158414241302879 |
| spellingShingle | Joseph Hu Chao-Chien Hu Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series Therapeutic Advances in Ophthalmology |
| title | Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series |
| title_full | Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series |
| title_fullStr | Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series |
| title_full_unstemmed | Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series |
| title_short | Chandelier retroillumination-assisted cataract surgery in two cases of congenital aniridia with severe aniridia-associated keratopathy: case series |
| title_sort | chandelier retroillumination assisted cataract surgery in two cases of congenital aniridia with severe aniridia associated keratopathy case series |
| url | https://doi.org/10.1177/25158414241302879 |
| work_keys_str_mv | AT josephhu chandelierretroilluminationassistedcataractsurgeryintwocasesofcongenitalaniridiawithsevereaniridiaassociatedkeratopathycaseseries AT chaochienhu chandelierretroilluminationassistedcataractsurgeryintwocasesofcongenitalaniridiawithsevereaniridiaassociatedkeratopathycaseseries |