Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion

Hypoglycemia is concerning for neurological complications in infants and children. Determining the cause of hypoglycemia is essential in providing appropriate treatment. Hyperinsulinism and growth hormone deficiency are known causes of hypoglycemia but are not commonly found together. We report a 4-...

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Main Authors: Erica Wee, John Herriges, Kavitha Dileepan, Sarah L. Tsai, Joseph T. Alaimo, Emily Paprocki
Format: Article
Language:English
Published: Wiley 2023-01-01
Series:Case Reports in Endocrinology
Online Access:http://dx.doi.org/10.1155/2023/8658540
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author Erica Wee
John Herriges
Kavitha Dileepan
Sarah L. Tsai
Joseph T. Alaimo
Emily Paprocki
author_facet Erica Wee
John Herriges
Kavitha Dileepan
Sarah L. Tsai
Joseph T. Alaimo
Emily Paprocki
author_sort Erica Wee
collection DOAJ
description Hypoglycemia is concerning for neurological complications in infants and children. Determining the cause of hypoglycemia is essential in providing appropriate treatment. Hyperinsulinism and growth hormone deficiency are known causes of hypoglycemia but are not commonly found together. We report a 4-month-old boy who presented with severe hypoglycemia and was found to have both hyperinsulinism and growth hormone deficiency. Treatment with both recombinant human growth hormone and diazoxide led to blood glucose normalization. Subsequently, he was found to have a genetic diagnosis of 20p11.22p11.21 deletion. 20p11 deletions have been associated with hypopituitarism, most commonly seen in growth hormone deficiency causing hypoglycemia. This case is one of a few to report hyperinsulinism as a manifestation of this deletion.
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spelling doaj-art-e3985ee070bc47959b105e52a37a01bd2025-08-20T02:21:24ZengWileyCase Reports in Endocrinology2090-651X2023-01-01202310.1155/2023/8658540Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 DeletionErica Wee0John Herriges1Kavitha Dileepan2Sarah L. Tsai3Joseph T. Alaimo4Emily Paprocki5Division of Pediatric Endocrinology and DiabetesUniversity of Missouri-Kansas City School of MedicineDivision of Pediatric Endocrinology and DiabetesDivision of Pediatric Endocrinology and DiabetesUniversity of Missouri-Kansas City School of MedicineDivision of Pediatric Endocrinology and DiabetesHypoglycemia is concerning for neurological complications in infants and children. Determining the cause of hypoglycemia is essential in providing appropriate treatment. Hyperinsulinism and growth hormone deficiency are known causes of hypoglycemia but are not commonly found together. We report a 4-month-old boy who presented with severe hypoglycemia and was found to have both hyperinsulinism and growth hormone deficiency. Treatment with both recombinant human growth hormone and diazoxide led to blood glucose normalization. Subsequently, he was found to have a genetic diagnosis of 20p11.22p11.21 deletion. 20p11 deletions have been associated with hypopituitarism, most commonly seen in growth hormone deficiency causing hypoglycemia. This case is one of a few to report hyperinsulinism as a manifestation of this deletion.http://dx.doi.org/10.1155/2023/8658540
spellingShingle Erica Wee
John Herriges
Kavitha Dileepan
Sarah L. Tsai
Joseph T. Alaimo
Emily Paprocki
Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
Case Reports in Endocrinology
title Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
title_full Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
title_fullStr Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
title_full_unstemmed Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
title_short Hyperinsulinemic Hypoglycemia and Growth Hormone Deficiency Secondary to 20p11 Deletion
title_sort hyperinsulinemic hypoglycemia and growth hormone deficiency secondary to 20p11 deletion
url http://dx.doi.org/10.1155/2023/8658540
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