The middle domain of Hsp104 can ensure substrates are functional after processing.

Molecular chaperones play a central role in protein disaggregation. However, the molecular determinants that regulate this process are poorly understood. Hsp104 is an AAA+ ATPase that disassembles stress granules and amyloids in yeast through collaboration with Hsp70 and Hsp40. In vitro studies show...

Full description

Saved in:
Bibliographic Details
Main Authors: Hannah E Buchholz, Jane E Dorweiler, Sam Guereca, Brett T Wisniewski, James Shorter, Anita L Manogaran
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2024-10-01
Series:PLoS Genetics
Online Access:https://doi.org/10.1371/journal.pgen.1011424
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850075333380800512
author Hannah E Buchholz
Jane E Dorweiler
Sam Guereca
Brett T Wisniewski
James Shorter
Anita L Manogaran
author_facet Hannah E Buchholz
Jane E Dorweiler
Sam Guereca
Brett T Wisniewski
James Shorter
Anita L Manogaran
author_sort Hannah E Buchholz
collection DOAJ
description Molecular chaperones play a central role in protein disaggregation. However, the molecular determinants that regulate this process are poorly understood. Hsp104 is an AAA+ ATPase that disassembles stress granules and amyloids in yeast through collaboration with Hsp70 and Hsp40. In vitro studies show that Hsp104 processes different types of protein aggregates by partially translocating or threading polypeptides through the central pore of the hexamer. However, it is unclear how Hsp104 processing influences client protein function in vivo. The middle domain (MD) of Hsp104 regulates ATPase activity and interactions with Hsp70. Here, we tested how MD variants, Hsp104A503S and Hsp104A503V, process different protein aggregates. We establish that engineered MD variants fail to resolve stress granules but retain prion fragmentation activity required for prion propagation. Using the Sup35 prion protein, our in vitro and in vivo data indicate that the MD variants can disassemble Sup35 aggregates, but the disaggregated protein has reduced GTPase and translation termination activity. These results suggest that the middle domain can play a role in sensing certain substrates and plays an essential role in ensuring the processed protein is functional.
format Article
id doaj-art-e2826c3948f9449a9840fe4d056c2004
institution DOAJ
issn 1553-7390
1553-7404
language English
publishDate 2024-10-01
publisher Public Library of Science (PLoS)
record_format Article
series PLoS Genetics
spelling doaj-art-e2826c3948f9449a9840fe4d056c20042025-08-20T02:46:20ZengPublic Library of Science (PLoS)PLoS Genetics1553-73901553-74042024-10-012010e101142410.1371/journal.pgen.1011424The middle domain of Hsp104 can ensure substrates are functional after processing.Hannah E BuchholzJane E DorweilerSam GuerecaBrett T WisniewskiJames ShorterAnita L ManogaranMolecular chaperones play a central role in protein disaggregation. However, the molecular determinants that regulate this process are poorly understood. Hsp104 is an AAA+ ATPase that disassembles stress granules and amyloids in yeast through collaboration with Hsp70 and Hsp40. In vitro studies show that Hsp104 processes different types of protein aggregates by partially translocating or threading polypeptides through the central pore of the hexamer. However, it is unclear how Hsp104 processing influences client protein function in vivo. The middle domain (MD) of Hsp104 regulates ATPase activity and interactions with Hsp70. Here, we tested how MD variants, Hsp104A503S and Hsp104A503V, process different protein aggregates. We establish that engineered MD variants fail to resolve stress granules but retain prion fragmentation activity required for prion propagation. Using the Sup35 prion protein, our in vitro and in vivo data indicate that the MD variants can disassemble Sup35 aggregates, but the disaggregated protein has reduced GTPase and translation termination activity. These results suggest that the middle domain can play a role in sensing certain substrates and plays an essential role in ensuring the processed protein is functional.https://doi.org/10.1371/journal.pgen.1011424
spellingShingle Hannah E Buchholz
Jane E Dorweiler
Sam Guereca
Brett T Wisniewski
James Shorter
Anita L Manogaran
The middle domain of Hsp104 can ensure substrates are functional after processing.
PLoS Genetics
title The middle domain of Hsp104 can ensure substrates are functional after processing.
title_full The middle domain of Hsp104 can ensure substrates are functional after processing.
title_fullStr The middle domain of Hsp104 can ensure substrates are functional after processing.
title_full_unstemmed The middle domain of Hsp104 can ensure substrates are functional after processing.
title_short The middle domain of Hsp104 can ensure substrates are functional after processing.
title_sort middle domain of hsp104 can ensure substrates are functional after processing
url https://doi.org/10.1371/journal.pgen.1011424
work_keys_str_mv AT hannahebuchholz themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT janeedorweiler themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT samguereca themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT bretttwisniewski themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT jamesshorter themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT anitalmanogaran themiddledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT hannahebuchholz middledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT janeedorweiler middledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT samguereca middledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT bretttwisniewski middledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT jamesshorter middledomainofhsp104canensuresubstratesarefunctionalafterprocessing
AT anitalmanogaran middledomainofhsp104canensuresubstratesarefunctionalafterprocessing