Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s”
Pheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The m...
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| Format: | Article |
| Language: | English |
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Thieme Medical and Scientific Publishers Pvt. Ltd.
2017-01-01
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| Series: | Indian Journal of Medical and Paediatric Oncology |
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| Online Access: | http://www.ijmpo.org/article.asp?issn=0971-5851;year=2017;volume=38;issue=1;spage=59;epage=61;aulast=Tripathy |
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| author | Prasanta Kumar Tripathy Kaumudee Pattnaik Manjushree Nayak Hiranya Kishor Mohanty |
| author_facet | Prasanta Kumar Tripathy Kaumudee Pattnaik Manjushree Nayak Hiranya Kishor Mohanty |
| author_sort | Prasanta Kumar Tripathy |
| collection | DOAJ |
| description | Pheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The most common presentation is sustained hypertension, which is absent in only 10% of children. We managed a 14-month-old female child with PCC, but she was not hypertensive. We report two unusual features, in this case, an extremely young age at presentation and a childhood case of nonhypertensive PCC contributing for “rule of 10s.” |
| format | Article |
| id | doaj-art-e15f13918ce643cc8fd20ce0369e9ef7 |
| institution | DOAJ |
| issn | 0971-5851 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Thieme Medical and Scientific Publishers Pvt. Ltd. |
| record_format | Article |
| series | Indian Journal of Medical and Paediatric Oncology |
| spelling | doaj-art-e15f13918ce643cc8fd20ce0369e9ef72025-08-20T03:10:35ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58512017-01-01381596110.4103/0971-5851.203503Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s”Prasanta Kumar TripathyKaumudee PattnaikManjushree NayakHiranya Kishor MohantyPheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The most common presentation is sustained hypertension, which is absent in only 10% of children. We managed a 14-month-old female child with PCC, but she was not hypertensive. We report two unusual features, in this case, an extremely young age at presentation and a childhood case of nonhypertensive PCC contributing for “rule of 10s.”http://www.ijmpo.org/article.asp?issn=0971-5851;year=2017;volume=38;issue=1;spage=59;epage=61;aulast=TripathyAdrenal medullachromaffin cellsparagangliomapheochromocytoma |
| spellingShingle | Prasanta Kumar Tripathy Kaumudee Pattnaik Manjushree Nayak Hiranya Kishor Mohanty Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” Indian Journal of Medical and Paediatric Oncology Adrenal medulla chromaffin cells paraganglioma pheochromocytoma |
| title | Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” |
| title_full | Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” |
| title_fullStr | Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” |
| title_full_unstemmed | Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” |
| title_short | Pheochromocytoma in a child without hypertension: A contribution to the “rule of 10s” |
| title_sort | pheochromocytoma in a child without hypertension a contribution to the rule of 10s |
| topic | Adrenal medulla chromaffin cells paraganglioma pheochromocytoma |
| url | http://www.ijmpo.org/article.asp?issn=0971-5851;year=2017;volume=38;issue=1;spage=59;epage=61;aulast=Tripathy |
| work_keys_str_mv | AT prasantakumartripathy pheochromocytomainachildwithouthypertensionacontributiontotheruleof10s AT kaumudeepattnaik pheochromocytomainachildwithouthypertensionacontributiontotheruleof10s AT manjushreenayak pheochromocytomainachildwithouthypertensionacontributiontotheruleof10s AT hiranyakishormohanty pheochromocytomainachildwithouthypertensionacontributiontotheruleof10s |