Recurrent Primary Intrasellar Paraganglioma

We describe a case of an 81-year-old male presenting with bitemporal visual field defects and blurry vision in the right eye. The patient was found to have a recurrent primary paraganglioma in the sellar and suprasellar region requiring a repeat transsphenoidal endoscopic resection. Immunohistochemi...

Full description

Saved in:
Bibliographic Details
Main Authors: Elizabeth A. Schueth, Daniel C. Martinez, Charles G. Kulwin, Jose M. Bonnin, Troy D. Payner, Jonathan Y. Ting
Format: Article
Language:English
Published: Wiley 2020-01-01
Series:Case Reports in Otolaryngology
Online Access:http://dx.doi.org/10.1155/2020/2580160
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849467872447823872
author Elizabeth A. Schueth
Daniel C. Martinez
Charles G. Kulwin
Jose M. Bonnin
Troy D. Payner
Jonathan Y. Ting
author_facet Elizabeth A. Schueth
Daniel C. Martinez
Charles G. Kulwin
Jose M. Bonnin
Troy D. Payner
Jonathan Y. Ting
author_sort Elizabeth A. Schueth
collection DOAJ
description We describe a case of an 81-year-old male presenting with bitemporal visual field defects and blurry vision in the right eye. The patient was found to have a recurrent primary paraganglioma in the sellar and suprasellar region requiring a repeat transsphenoidal endoscopic resection. Immunohistochemical examination confirmed paraganglioma with the classic zellballen appearance which stained positive for chromogranin, synaptophysin, and S-100 in the periphery. Paragangliomas (PGLs) in the sella turcica are a rare entity; only 19 cases have ever been reported in the literature. PGLs in the sellar region are often misdiagnosed or diagnosed in a delayed fashion. Earlier diagnosis of this locally aggressive tumor and meticulous debulking can prevent morbidity secondary to the tumor’s compressive effects. This report highlights the effectiveness of surgical interventions in treatment of paragangliomas. More research is still needed to determine the need for adjuvant therapies such as radiation.
format Article
id doaj-art-e11ee8704deb485cae04524e48770404
institution Kabale University
issn 2090-6765
2090-6773
language English
publishDate 2020-01-01
publisher Wiley
record_format Article
series Case Reports in Otolaryngology
spelling doaj-art-e11ee8704deb485cae04524e487704042025-08-20T03:26:00ZengWileyCase Reports in Otolaryngology2090-67652090-67732020-01-01202010.1155/2020/25801602580160Recurrent Primary Intrasellar ParagangliomaElizabeth A. Schueth0Daniel C. Martinez1Charles G. Kulwin2Jose M. Bonnin3Troy D. Payner4Jonathan Y. Ting5Indiana University School of Medicine, 1120 W. Michigan Street, Suite 200, Indianapolis, IN 46202, USADepartment of Otolaryngology – Head and Neck Surgery, Indiana University School of Medicine, 1130 W. Michigan Street, Fesler Hall, Suite 400, Indianapolis, IN 46202, USAGoodman Campbell Brain and Spine, 13345 Illinois Street, Carmel, IN 46032, USADepartment of Pathology and Laboratory Medicine, Indiana University School of Medicine, 350 W. 11th Street, Indiana University Health Pathology Laboratory, Indianapolis, IN 46202, USAGoodman Campbell Brain and Spine, 13345 Illinois Street, Carmel, IN 46032, USADepartment of Otolaryngology – Head and Neck Surgery, Indiana University School of Medicine, 1130 W. Michigan Street, Fesler Hall, Suite 400, Indianapolis, IN 46202, USAWe describe a case of an 81-year-old male presenting with bitemporal visual field defects and blurry vision in the right eye. The patient was found to have a recurrent primary paraganglioma in the sellar and suprasellar region requiring a repeat transsphenoidal endoscopic resection. Immunohistochemical examination confirmed paraganglioma with the classic zellballen appearance which stained positive for chromogranin, synaptophysin, and S-100 in the periphery. Paragangliomas (PGLs) in the sella turcica are a rare entity; only 19 cases have ever been reported in the literature. PGLs in the sellar region are often misdiagnosed or diagnosed in a delayed fashion. Earlier diagnosis of this locally aggressive tumor and meticulous debulking can prevent morbidity secondary to the tumor’s compressive effects. This report highlights the effectiveness of surgical interventions in treatment of paragangliomas. More research is still needed to determine the need for adjuvant therapies such as radiation.http://dx.doi.org/10.1155/2020/2580160
spellingShingle Elizabeth A. Schueth
Daniel C. Martinez
Charles G. Kulwin
Jose M. Bonnin
Troy D. Payner
Jonathan Y. Ting
Recurrent Primary Intrasellar Paraganglioma
Case Reports in Otolaryngology
title Recurrent Primary Intrasellar Paraganglioma
title_full Recurrent Primary Intrasellar Paraganglioma
title_fullStr Recurrent Primary Intrasellar Paraganglioma
title_full_unstemmed Recurrent Primary Intrasellar Paraganglioma
title_short Recurrent Primary Intrasellar Paraganglioma
title_sort recurrent primary intrasellar paraganglioma
url http://dx.doi.org/10.1155/2020/2580160
work_keys_str_mv AT elizabethaschueth recurrentprimaryintrasellarparaganglioma
AT danielcmartinez recurrentprimaryintrasellarparaganglioma
AT charlesgkulwin recurrentprimaryintrasellarparaganglioma
AT josembonnin recurrentprimaryintrasellarparaganglioma
AT troydpayner recurrentprimaryintrasellarparaganglioma
AT jonathanyting recurrentprimaryintrasellarparaganglioma