WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells

Mutations in WD40-repeat protein 62 (WDR62) are commonly associated with primary microcephaly and other developmental cortical malformations. We used human pluripotent stem cells (hPSC) to examine WDR62 function during human neural differentiation and model early stages of human corticogenesis. Neur...

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Main Authors: Abdullah J. Alshawaf, Ana Antonic, Efstratios Skafidas, Dominic Chi-Hung Ng, Mirella Dottori
Format: Article
Language:English
Published: Wiley 2017-01-01
Series:Stem Cells International
Online Access:http://dx.doi.org/10.1155/2017/7848932
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author Abdullah J. Alshawaf
Ana Antonic
Efstratios Skafidas
Dominic Chi-Hung Ng
Mirella Dottori
author_facet Abdullah J. Alshawaf
Ana Antonic
Efstratios Skafidas
Dominic Chi-Hung Ng
Mirella Dottori
author_sort Abdullah J. Alshawaf
collection DOAJ
description Mutations in WD40-repeat protein 62 (WDR62) are commonly associated with primary microcephaly and other developmental cortical malformations. We used human pluripotent stem cells (hPSC) to examine WDR62 function during human neural differentiation and model early stages of human corticogenesis. Neurospheres lacking WDR62 expression showed decreased expression of intermediate progenitor marker, TBR2, and also glial marker, S100β. In contrast, inhibition of c-Jun N-terminal kinase (JNK) signalling during hPSC neural differentiation induced upregulation of WDR62 with a corresponding increase in neural and glial progenitor markers, PAX6 and EAAT1, respectively. These findings may signify a role of WDR62 in specifying intermediate neural and glial progenitors during human pluripotent stem cell differentiation.
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institution Kabale University
issn 1687-966X
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language English
publishDate 2017-01-01
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series Stem Cells International
spelling doaj-art-e08eb42dbe164b9f9c9036340fab2ddc2025-08-20T03:26:09ZengWileyStem Cells International1687-966X1687-96782017-01-01201710.1155/2017/78489327848932WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem CellsAbdullah J. Alshawaf0Ana Antonic1Efstratios Skafidas2Dominic Chi-Hung Ng3Mirella Dottori4Centre for Neural Engineering, The University of Melbourne, Carlton, VIC 3010, AustraliaCentre for Neural Engineering, The University of Melbourne, Carlton, VIC 3010, AustraliaCentre for Neural Engineering, The University of Melbourne, Carlton, VIC 3010, AustraliaSchool of Biomedical Science, Faculty of Medicine and Biomedical Sciences, University of Queensland, St Lucia, QLD 4072, AustraliaCentre for Neural Engineering, The University of Melbourne, Carlton, VIC 3010, AustraliaMutations in WD40-repeat protein 62 (WDR62) are commonly associated with primary microcephaly and other developmental cortical malformations. We used human pluripotent stem cells (hPSC) to examine WDR62 function during human neural differentiation and model early stages of human corticogenesis. Neurospheres lacking WDR62 expression showed decreased expression of intermediate progenitor marker, TBR2, and also glial marker, S100β. In contrast, inhibition of c-Jun N-terminal kinase (JNK) signalling during hPSC neural differentiation induced upregulation of WDR62 with a corresponding increase in neural and glial progenitor markers, PAX6 and EAAT1, respectively. These findings may signify a role of WDR62 in specifying intermediate neural and glial progenitors during human pluripotent stem cell differentiation.http://dx.doi.org/10.1155/2017/7848932
spellingShingle Abdullah J. Alshawaf
Ana Antonic
Efstratios Skafidas
Dominic Chi-Hung Ng
Mirella Dottori
WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
Stem Cells International
title WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
title_full WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
title_fullStr WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
title_full_unstemmed WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
title_short WDR62 Regulates Early Neural and Glial Progenitor Specification of Human Pluripotent Stem Cells
title_sort wdr62 regulates early neural and glial progenitor specification of human pluripotent stem cells
url http://dx.doi.org/10.1155/2017/7848932
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