Vitamin D Deficiency in Cystic Fibrosis

Cystic Fibrosis is the most common inherited genetic respiratory disorder in the Western World. Hypovitaminosis D is almost universal in CF patients, likely due to a combination of inadequate absorption, impaired metabolism, and lack of sun exposure. Inadequate levels are associated with the high pr...

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Bibliographic Details
Main Authors: William B. Hall, Amy A. Sparks, Robert M. Aris
Format: Article
Language:English
Published: Wiley 2010-01-01
Series:International Journal of Endocrinology
Online Access:http://dx.doi.org/10.1155/2010/218691
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Summary:Cystic Fibrosis is the most common inherited genetic respiratory disorder in the Western World. Hypovitaminosis D is almost universal in CF patients, likely due to a combination of inadequate absorption, impaired metabolism, and lack of sun exposure. Inadequate levels are associated with the high prevalence of bone disease or osteoporosis in CF patients, which is associated with increased morbidity including fractures, kyphosis, and worsening pulmonary status. Treatment goals include regular monitoring 25 hydroxyvitamin D (25OHD) levels with aggressive treatment for those with levels <75 nmol/L (<30 ng/mL). More research is needed to determine optimal supplementation goals and strategies.
ISSN:1687-8337
1687-8345