Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report
Papillary Intralymphatic Angioendothelioma (PILA), or Dąbska Tumour, is an exceedingly rare lymphovascular neoplasm of intermediate malignancy, predominantly affecting cutaneous and soft tissue sites. This case report highlights an unusual presentation of PILA in the mesentery of a 38-year-old male,...
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Tehran University of Medical Sciences
2025-07-01
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| Series: | Case Reports in Clinical Practice |
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| Online Access: | https://crcp.tums.ac.ir/index.php/crcp/article/view/1032 |
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| author | Abdus Salam Raju Dinuke de Silva Yasser Farooque Tristan Rutland |
| author_facet | Abdus Salam Raju Dinuke de Silva Yasser Farooque Tristan Rutland |
| author_sort | Abdus Salam Raju |
| collection | DOAJ |
| description | Papillary Intralymphatic Angioendothelioma (PILA), or Dąbska Tumour, is an exceedingly rare lymphovascular neoplasm of intermediate malignancy, predominantly affecting cutaneous and soft tissue sites. This case report highlights an unusual presentation of PILA in the mesentery of a 38-year-old male, a site not previously documented. He initially underwent a splenectomy for symptomatic splenic hemangioma. His symptoms recurred two years later, presenting with haemoperitoneum and extensive abdominal involvement, including the colon, small bowel mesentery, and diaphragms. An en-bloc extended right hemicolectomy and partial hepatectomy achieved complete resection. Histopathology revealed hobnail endothelial cells and characteristic papillary structures, confirming PILA. Despite its rare visceral occurrence and diagnostic challenges, the patient showed no recurrence at six months post-surgery. This case underscores the importance of histopathological analysis and awareness of atypical presentations. Wider surgical excision remains the cornerstone of treatment, with vigilant follow-up essential for detecting recurrence and guiding future management
protocols for this rare entity.
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| format | Article |
| id | doaj-art-ddce176e28a04a2c8b0facf9edf76397 |
| institution | Kabale University |
| issn | 2538-2683 2538-2691 |
| language | English |
| publishDate | 2025-07-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Case Reports in Clinical Practice |
| spelling | doaj-art-ddce176e28a04a2c8b0facf9edf763972025-08-20T04:02:32ZengTehran University of Medical SciencesCase Reports in Clinical Practice2538-26832538-26912025-07-019610.18502/crcp.v9i6.18946Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case ReportAbdus Salam Raju0Dinuke de Silva1Yasser Farooque2Tristan Rutland3Department of General Surgery, Upper GI Surgery Liverpool Hospital, Sydney, NSW Australia. AND Western Sydney University, Sydney, NSW Australia.Department of Anatomical Pathology, NSW Health Pathology, Sydney, NSW Australia.Department of General Surgery, Upper GI Surgery Liverpool Hospital, Sydney, NSW Australia.Western Sydney University, Sydney, NSW Australia. AND Department of Anatomical Pathology, NSW Health Pathology, Sydney, NSW Australia.Papillary Intralymphatic Angioendothelioma (PILA), or Dąbska Tumour, is an exceedingly rare lymphovascular neoplasm of intermediate malignancy, predominantly affecting cutaneous and soft tissue sites. This case report highlights an unusual presentation of PILA in the mesentery of a 38-year-old male, a site not previously documented. He initially underwent a splenectomy for symptomatic splenic hemangioma. His symptoms recurred two years later, presenting with haemoperitoneum and extensive abdominal involvement, including the colon, small bowel mesentery, and diaphragms. An en-bloc extended right hemicolectomy and partial hepatectomy achieved complete resection. Histopathology revealed hobnail endothelial cells and characteristic papillary structures, confirming PILA. Despite its rare visceral occurrence and diagnostic challenges, the patient showed no recurrence at six months post-surgery. This case underscores the importance of histopathological analysis and awareness of atypical presentations. Wider surgical excision remains the cornerstone of treatment, with vigilant follow-up essential for detecting recurrence and guiding future management protocols for this rare entity. https://crcp.tums.ac.ir/index.php/crcp/article/view/1032PILAIntralymphatic angioendotheliomaDabska tumour |
| spellingShingle | Abdus Salam Raju Dinuke de Silva Yasser Farooque Tristan Rutland Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report Case Reports in Clinical Practice PILA Intralymphatic angioendothelioma Dabska tumour |
| title | Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report |
| title_full | Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report |
| title_fullStr | Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report |
| title_full_unstemmed | Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report |
| title_short | Diagnosis of Papillary Intralymphatic Angioendothelioma in the Abdominal Viscera: A Case Report |
| title_sort | diagnosis of papillary intralymphatic angioendothelioma in the abdominal viscera a case report |
| topic | PILA Intralymphatic angioendothelioma Dabska tumour |
| url | https://crcp.tums.ac.ir/index.php/crcp/article/view/1032 |
| work_keys_str_mv | AT abdussalamraju diagnosisofpapillaryintralymphaticangioendotheliomaintheabdominalvisceraacasereport AT dinukedesilva diagnosisofpapillaryintralymphaticangioendotheliomaintheabdominalvisceraacasereport AT yasserfarooque diagnosisofpapillaryintralymphaticangioendotheliomaintheabdominalvisceraacasereport AT tristanrutland diagnosisofpapillaryintralymphaticangioendotheliomaintheabdominalvisceraacasereport |