Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH)
Neuroblastoma is an embryonic cancer arising from neural crest stem cell and almost exclusively a pediatric neoplasm. In adults, neuroblastoma is rare and presents worse prognosis compared to children. The most common presentation of this neoplasia is a painless abdominal mass. Other signs and sympt...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações Ltda.
2023-08-01
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| Series: | Brazilian Journal of Oncology |
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| Online Access: | https://www.brazilianjournalofoncology.com.br/details/253/en-US/case-report--a-rare-mediastinal-neuroblastoma-in-an-adult-associated-with-syndrome-of-inappropriate-secretion-of-antidiuretic-hormone--siadh- |
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| author | Caio Silvério de Souza Carine Matos Bispo Patury José Slaibi Paulo Roberto Fontes Athanazio Lister Cedro Ramos Juvenal Mascarenhas Nassri Laíse Oliveira Pales Santos Carina Manuela Souza Barreto Michelle Oliveira Espírito-Santo Laiane Campos Pereira Marianna Santos Rodrigues |
| author_facet | Caio Silvério de Souza Carine Matos Bispo Patury José Slaibi Paulo Roberto Fontes Athanazio Lister Cedro Ramos Juvenal Mascarenhas Nassri Laíse Oliveira Pales Santos Carina Manuela Souza Barreto Michelle Oliveira Espírito-Santo Laiane Campos Pereira Marianna Santos Rodrigues |
| author_sort | Caio Silvério de Souza |
| collection | DOAJ |
| description | Neuroblastoma is an embryonic cancer arising from neural crest stem cell and almost exclusively a pediatric neoplasm. In adults, neuroblastoma is rare and presents worse prognosis compared to children. The most common presentation of this neoplasia is a painless abdominal mass. Other signs and symptoms can be related to mass effect from the primary tumor or as a result of metastatic disease, or paraneoplastic syndromes. There are no well-established treatment guidelines for adults with neuroblastoma. In general, the principle of treatment is determined by risk assessment system, using a multimodal treatment (surgery, chemotherapy, and radiotherapy) based on treatment protocols for this neoplasm in children. This case report refers to the diagnosis of neuroblastoma in mediastinum in a 52-year-old woman with locally advanced disease and not able to be removed to diagnosis, accompanied by hyponatremia as paraneoplastic syndrome, which presented a good response to the treatment established. |
| format | Article |
| id | doaj-art-dd6a2a05565d4315a61c07bbb024dee4 |
| institution | Kabale University |
| issn | 2526-8732 |
| language | English |
| publishDate | 2023-08-01 |
| publisher | Thieme Revinter Publicações Ltda. |
| record_format | Article |
| series | Brazilian Journal of Oncology |
| spelling | doaj-art-dd6a2a05565d4315a61c07bbb024dee42025-08-20T03:25:05ZengThieme Revinter Publicações Ltda.Brazilian Journal of Oncology2526-87322023-08-011910.5935/2526-8732.20230405Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH)Caio Silvério de Souza0Carine Matos Bispo Patury1José Slaibi2Paulo Roberto Fontes Athanazio3Lister Cedro Ramos4Juvenal Mascarenhas Nassri5Laíse Oliveira Pales Santos6Carina Manuela Souza Barreto7Michelle Oliveira Espírito-Santo8Laiane Campos Pereira9Marianna Santos Rodrigues10Assistência multidisciplinar em oncologia - AMO, Clinical Oncology - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Clinical Oncology - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Mastology - Ilhéus - Bahia - BrazilImagepat, Pathology - Salvador - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Radiology - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Thoracic surgery - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Oncology nurse - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Oncology nurse - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Oncology nutriotinist - Ilhéus - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Oncology pharmaceuticals - Ilheús - Bahia - BrazilAssistência multidisciplinar em oncologia - AMO, Oncology psychology - Ilhéus - Bahia - BrazilNeuroblastoma is an embryonic cancer arising from neural crest stem cell and almost exclusively a pediatric neoplasm. In adults, neuroblastoma is rare and presents worse prognosis compared to children. The most common presentation of this neoplasia is a painless abdominal mass. Other signs and symptoms can be related to mass effect from the primary tumor or as a result of metastatic disease, or paraneoplastic syndromes. There are no well-established treatment guidelines for adults with neuroblastoma. In general, the principle of treatment is determined by risk assessment system, using a multimodal treatment (surgery, chemotherapy, and radiotherapy) based on treatment protocols for this neoplasm in children. This case report refers to the diagnosis of neuroblastoma in mediastinum in a 52-year-old woman with locally advanced disease and not able to be removed to diagnosis, accompanied by hyponatremia as paraneoplastic syndrome, which presented a good response to the treatment established.https://www.brazilianjournalofoncology.com.br/details/253/en-US/case-report--a-rare-mediastinal-neuroblastoma-in-an-adult-associated-with-syndrome-of-inappropriate-secretion-of-antidiuretic-hormone--siadh-neuroblastomamediastinal neoplasmsadult. |
| spellingShingle | Caio Silvério de Souza Carine Matos Bispo Patury José Slaibi Paulo Roberto Fontes Athanazio Lister Cedro Ramos Juvenal Mascarenhas Nassri Laíse Oliveira Pales Santos Carina Manuela Souza Barreto Michelle Oliveira Espírito-Santo Laiane Campos Pereira Marianna Santos Rodrigues Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) Brazilian Journal of Oncology neuroblastoma mediastinal neoplasms adult. |
| title | Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) |
| title_full | Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) |
| title_fullStr | Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) |
| title_full_unstemmed | Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) |
| title_short | Case report: a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone (SIADH) |
| title_sort | case report a rare mediastinal neuroblastoma in an adult associated with syndrome of inappropriate secretion of antidiuretic hormone siadh |
| topic | neuroblastoma mediastinal neoplasms adult. |
| url | https://www.brazilianjournalofoncology.com.br/details/253/en-US/case-report--a-rare-mediastinal-neuroblastoma-in-an-adult-associated-with-syndrome-of-inappropriate-secretion-of-antidiuretic-hormone--siadh- |
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