Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children
Tracheobronchomegaly is a rare developmental defect in children, which is characterized by the expansion of the trachea and large bronchi, the diagnosis and treatment of which are made more often in adult practice, when the clinical diagnostic picture acquires the obvious features of Mounier-Kuhn sy...
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Luchevaya Diagnostika, LLC
2020-06-01
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| Series: | Вестник рентгенологии и радиологии |
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| Online Access: | https://www.russianradiology.ru/jour/article/view/568 |
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| author | N. A. Il’ina L. E. Vorob’eva M. D. Bakradze A. S. Polyakova |
| author_facet | N. A. Il’ina L. E. Vorob’eva M. D. Bakradze A. S. Polyakova |
| author_sort | N. A. Il’ina |
| collection | DOAJ |
| description | Tracheobronchomegaly is a rare developmental defect in children, which is characterized by the expansion of the trachea and large bronchi, the diagnosis and treatment of which are made more often in adult practice, when the clinical diagnostic picture acquires the obvious features of Mounier-Kuhn syndrome. In this connection, the need arises for the early detection of this pathology in children and its differentiation from other diseases and malformations of the tracheobronchial tree, which mask a recurrent inflammatory process in the lung and upper respiratory tract, and primarily with those, such as cystic fibrosis and primary ciliary dyskinesia.The paper describes a case of secondary tracheobronchomegaly in a child with obvious clinical manifestations of Mounier-Kuhn syndrome in the presence of bronchiectasis, pulmonary fibrosis, and signs of systemic connective tissue disease. It discusses the possibilities of chest computed tomography in the diagnosis of this defect in children, as well as its causes. The sizes of the trachea and main bronchi in this patient are compared with those in the groups of children of the same age and sex who have cystic fibrosis or diffuse pulmonary fibrosis to identify a more significant role of hereditary connective tissue diseases in the development of secondary tracheobronchomegaly. The authors propose to separate the concepts of tracheobronchomegaly and Mounier-Kuhn syndrome in children and to recognize the threshold for tracheal expansion in these patients having +3SD or more. |
| format | Article |
| id | doaj-art-d8a380d101a840ad829af0bf593b948e |
| institution | Kabale University |
| issn | 0042-4676 2619-0478 |
| language | English |
| publishDate | 2020-06-01 |
| publisher | Luchevaya Diagnostika, LLC |
| record_format | Article |
| series | Вестник рентгенологии и радиологии |
| spelling | doaj-art-d8a380d101a840ad829af0bf593b948e2025-08-20T03:35:08ZengLuchevaya Diagnostika, LLCВестник рентгенологии и радиологии0042-46762619-04782020-06-01101317518210.20862/0042-4676-2020-101-3-175-182338Difficulties in the Differential Diagnosis of Tracheobronchomegaly in ChildrenN. A. Il’ina0L. E. Vorob’eva1M. D. Bakradze2A. S. Polyakova3I.I. Mechnikov North-Western State Medical University, Ministry of Health of the Russian FederationNational Medical Research Center of Children’s Health, Ministry of Health of the Russian FederationNational Medical Research Center of Children’s Health, Ministry of Health of the Russian Federation; Pirogov Russian National Research Medical University, Ministry of Health of the Russian FederationNational Medical Research Center of Children’s Health, Ministry of Health of the Russian Federation; Pirogov Russian National Research Medical University, Ministry of Health of the Russian FederationTracheobronchomegaly is a rare developmental defect in children, which is characterized by the expansion of the trachea and large bronchi, the diagnosis and treatment of which are made more often in adult practice, when the clinical diagnostic picture acquires the obvious features of Mounier-Kuhn syndrome. In this connection, the need arises for the early detection of this pathology in children and its differentiation from other diseases and malformations of the tracheobronchial tree, which mask a recurrent inflammatory process in the lung and upper respiratory tract, and primarily with those, such as cystic fibrosis and primary ciliary dyskinesia.The paper describes a case of secondary tracheobronchomegaly in a child with obvious clinical manifestations of Mounier-Kuhn syndrome in the presence of bronchiectasis, pulmonary fibrosis, and signs of systemic connective tissue disease. It discusses the possibilities of chest computed tomography in the diagnosis of this defect in children, as well as its causes. The sizes of the trachea and main bronchi in this patient are compared with those in the groups of children of the same age and sex who have cystic fibrosis or diffuse pulmonary fibrosis to identify a more significant role of hereditary connective tissue diseases in the development of secondary tracheobronchomegaly. The authors propose to separate the concepts of tracheobronchomegaly and Mounier-Kuhn syndrome in children and to recognize the threshold for tracheal expansion in these patients having +3SD or more.https://www.russianradiology.ru/jour/article/view/568tracheobronchomegalymounier-kuhn syndromecongenital lung malformationscongenital bronchial malformationsbronchiectasiscystic fibrosiskartagener’s syndromeprimary ciliary dyskinesiapulmonary fibrosischronic lung diseasescomputed tomography |
| spellingShingle | N. A. Il’ina L. E. Vorob’eva M. D. Bakradze A. S. Polyakova Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children Вестник рентгенологии и радиологии tracheobronchomegaly mounier-kuhn syndrome congenital lung malformations congenital bronchial malformations bronchiectasis cystic fibrosis kartagener’s syndrome primary ciliary dyskinesia pulmonary fibrosis chronic lung diseases computed tomography |
| title | Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children |
| title_full | Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children |
| title_fullStr | Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children |
| title_full_unstemmed | Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children |
| title_short | Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children |
| title_sort | difficulties in the differential diagnosis of tracheobronchomegaly in children |
| topic | tracheobronchomegaly mounier-kuhn syndrome congenital lung malformations congenital bronchial malformations bronchiectasis cystic fibrosis kartagener’s syndrome primary ciliary dyskinesia pulmonary fibrosis chronic lung diseases computed tomography |
| url | https://www.russianradiology.ru/jour/article/view/568 |
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