Lipoid Proteinosis: A Rare Encounter in Dental Office

Lipoid proteinosis is a sporadic congenital metabolic disorder which is characterized by deposition of hyaline material in dermis, submucosal connective tissue, and various internal organs. It has an extremely low prevalence rate with less than 300 cases reported so far. This progressive disease has...

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Main Authors: Prasannasrinivas Deshpande, Mahima Veeranna Guledgud, Karthikeya Patil, Usha Hegde, Ankita Sahni, Sreeshlya Huchanahalli Sheshanna
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2015/670369
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author Prasannasrinivas Deshpande
Mahima Veeranna Guledgud
Karthikeya Patil
Usha Hegde
Ankita Sahni
Sreeshlya Huchanahalli Sheshanna
author_facet Prasannasrinivas Deshpande
Mahima Veeranna Guledgud
Karthikeya Patil
Usha Hegde
Ankita Sahni
Sreeshlya Huchanahalli Sheshanna
author_sort Prasannasrinivas Deshpande
collection DOAJ
description Lipoid proteinosis is a sporadic congenital metabolic disorder which is characterized by deposition of hyaline material in dermis, submucosal connective tissue, and various internal organs. It has an extremely low prevalence rate with less than 300 cases reported so far. This progressive disease has a vast spectrum of manifestations ranging from asymptomatic lesions to fatal seizures and respiratory obstruction making timely diagnosis of this rare disorder an imperative task for oral health care practitioners. We report a case of characteristic oral manifestations of lipoid proteinosis in a 28-year-old male patient along with a review of relevant prevailing literature.
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publisher Wiley
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series Case Reports in Dentistry
spelling doaj-art-d818645cdd3b442fbccdb867aa2b7ecd2025-08-20T03:23:52ZengWileyCase Reports in Dentistry2090-64472090-64552015-01-01201510.1155/2015/670369670369Lipoid Proteinosis: A Rare Encounter in Dental OfficePrasannasrinivas Deshpande0Mahima Veeranna Guledgud1Karthikeya Patil2Usha Hegde3Ankita Sahni4Sreeshlya Huchanahalli Sheshanna5Department of Oral Medicine & Radiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaDepartment of Oral Medicine & Radiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaDepartment of Oral Medicine & Radiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaDepartment of Oral Pathology and Microbiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaDepartment of Oral Medicine & Radiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaDepartment of Oral Pathology and Microbiology, JSS Dental College and Hospital, JSS University, Mysore, Karnataka 570015, IndiaLipoid proteinosis is a sporadic congenital metabolic disorder which is characterized by deposition of hyaline material in dermis, submucosal connective tissue, and various internal organs. It has an extremely low prevalence rate with less than 300 cases reported so far. This progressive disease has a vast spectrum of manifestations ranging from asymptomatic lesions to fatal seizures and respiratory obstruction making timely diagnosis of this rare disorder an imperative task for oral health care practitioners. We report a case of characteristic oral manifestations of lipoid proteinosis in a 28-year-old male patient along with a review of relevant prevailing literature.http://dx.doi.org/10.1155/2015/670369
spellingShingle Prasannasrinivas Deshpande
Mahima Veeranna Guledgud
Karthikeya Patil
Usha Hegde
Ankita Sahni
Sreeshlya Huchanahalli Sheshanna
Lipoid Proteinosis: A Rare Encounter in Dental Office
Case Reports in Dentistry
title Lipoid Proteinosis: A Rare Encounter in Dental Office
title_full Lipoid Proteinosis: A Rare Encounter in Dental Office
title_fullStr Lipoid Proteinosis: A Rare Encounter in Dental Office
title_full_unstemmed Lipoid Proteinosis: A Rare Encounter in Dental Office
title_short Lipoid Proteinosis: A Rare Encounter in Dental Office
title_sort lipoid proteinosis a rare encounter in dental office
url http://dx.doi.org/10.1155/2015/670369
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