Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma
Abstract Background Systemic amyloidosis is a kind of clinical syndrome in which amyloid is deposited between the cells of various organs in the body, resulting in gradual failure of the function of the affected organs. Depending on the site of amyloid deposition, it may show various clinical sympto...
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BMC
2024-12-01
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| Series: | International Journal of Emergency Medicine |
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| Online Access: | https://doi.org/10.1186/s12245-024-00801-3 |
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| author | Yaqi Sheng Huadong Zhu |
| author_facet | Yaqi Sheng Huadong Zhu |
| author_sort | Yaqi Sheng |
| collection | DOAJ |
| description | Abstract Background Systemic amyloidosis is a kind of clinical syndrome in which amyloid is deposited between the cells of various organs in the body, resulting in gradual failure of the function of the affected organs. Depending on the site of amyloid deposition, it may show various clinical symptoms of multiple system involvement. Patient concerns A 44-years-old female with spontaneous giant retroperitoneal hematoma was admitted to the emergency department of Peking Union Medical College Hospital in Mar 2023. Diagnoses She was found with a extremely X-factor deficiency and diagnosed with AL amyloidosis according to pathological findings finally. Interventions and outcomes She received a variety of treatments to improve her coagulation function and underwent chemotherapy for AL in the hematology department which improved her coagulation function and was discharged to her local hospital for follow-up treatment. Conclusion This case provides a new reference for emergency doctors in the diagnosis and treatment of acute severe hemorrhagic diseases. |
| format | Article |
| id | doaj-art-d6bd65d927b54ae0a87bc3255e712eee |
| institution | DOAJ |
| issn | 1865-1380 |
| language | English |
| publishDate | 2024-12-01 |
| publisher | BMC |
| record_format | Article |
| series | International Journal of Emergency Medicine |
| spelling | doaj-art-d6bd65d927b54ae0a87bc3255e712eee2025-08-20T02:57:39ZengBMCInternational Journal of Emergency Medicine1865-13802024-12-011711610.1186/s12245-024-00801-3Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematomaYaqi Sheng0Huadong Zhu1Emergency Department, The State Key Laboratory for Complex, Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Science and Peking Union Medical CollegeEmergency Department, The State Key Laboratory for Complex, Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Science and Peking Union Medical CollegeAbstract Background Systemic amyloidosis is a kind of clinical syndrome in which amyloid is deposited between the cells of various organs in the body, resulting in gradual failure of the function of the affected organs. Depending on the site of amyloid deposition, it may show various clinical symptoms of multiple system involvement. Patient concerns A 44-years-old female with spontaneous giant retroperitoneal hematoma was admitted to the emergency department of Peking Union Medical College Hospital in Mar 2023. Diagnoses She was found with a extremely X-factor deficiency and diagnosed with AL amyloidosis according to pathological findings finally. Interventions and outcomes She received a variety of treatments to improve her coagulation function and underwent chemotherapy for AL in the hematology department which improved her coagulation function and was discharged to her local hospital for follow-up treatment. Conclusion This case provides a new reference for emergency doctors in the diagnosis and treatment of acute severe hemorrhagic diseases.https://doi.org/10.1186/s12245-024-00801-3Immunoglobulin light chain amyloidosis (AL)Factor X deficiencyCase report |
| spellingShingle | Yaqi Sheng Huadong Zhu Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma International Journal of Emergency Medicine Immunoglobulin light chain amyloidosis (AL) Factor X deficiency Case report |
| title | Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma |
| title_full | Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma |
| title_fullStr | Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma |
| title_full_unstemmed | Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma |
| title_short | Case report: a case of AL amyloidosis with spontaneous giant retroperitoneal hematoma |
| title_sort | case report a case of al amyloidosis with spontaneous giant retroperitoneal hematoma |
| topic | Immunoglobulin light chain amyloidosis (AL) Factor X deficiency Case report |
| url | https://doi.org/10.1186/s12245-024-00801-3 |
| work_keys_str_mv | AT yaqisheng casereportacaseofalamyloidosiswithspontaneousgiantretroperitonealhematoma AT huadongzhu casereportacaseofalamyloidosiswithspontaneousgiantretroperitonealhematoma |