Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.

The stabilisation of HIF-α is central to the transcriptional response of animals to hypoxia, regulating the expression of hundreds of genes including those involved in angiogenesis, metabolism and metastasis. HIF-α is degraded under normoxic conditions by proline hydroxylation, which allows for reco...

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Main Authors: Cameron E Snell, Helen Turley, Alan McIntyre, Demin Li, Massimo Masiero, Christopher J Schofield, Kevin C Gatter, Adrian L Harris, Francesco Pezzella
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2014-01-01
Series:PLoS ONE
Online Access:https://doi.org/10.1371/journal.pone.0088955
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author Cameron E Snell
Helen Turley
Alan McIntyre
Demin Li
Massimo Masiero
Christopher J Schofield
Kevin C Gatter
Adrian L Harris
Francesco Pezzella
author_facet Cameron E Snell
Helen Turley
Alan McIntyre
Demin Li
Massimo Masiero
Christopher J Schofield
Kevin C Gatter
Adrian L Harris
Francesco Pezzella
author_sort Cameron E Snell
collection DOAJ
description The stabilisation of HIF-α is central to the transcriptional response of animals to hypoxia, regulating the expression of hundreds of genes including those involved in angiogenesis, metabolism and metastasis. HIF-α is degraded under normoxic conditions by proline hydroxylation, which allows for recognition and ubiquitination by the von-Hippel-Lindau (VHL) E3 ligase complex. The aim of our study was to investigate the posttranslational modification of HIF-1α in tumours, to assess whether there are additional mechanisms besides reduced hydroxylation leading to stability. To this end we optimised antibodies against the proline-hydroxylated forms of HIF-1α for use in formalin fixed paraffin embedded (FFPE) immunohistochemistry to assess effects in tumour cells in vivo. We found that HIF-1α proline-hydroxylated at both VHL binding sites (Pro402 and Pro564), was present in hypoxic regions of a wide range of tumours, tumour xenografts and in moderately hypoxic cells in vitro. Staining for hydroxylated HIF-1α can identify a subset of breast cancer patients with poorer prognosis and may be a better marker than total HIF-1α levels. The expression of unhydroxylated HIF-1α positively correlates with VHL in breast cancer suggesting that VHL may be rate-limiting for HIF degradation. Our conclusions are that the degradation of proline-hydroxylated HIF-1α may be rate-limited in tumours and therefore provides new insights into mechanisms of HIF upregulation. Persistence of proline-hydroxylated HIF-1α in perinecrotic areas suggests there is adequate oxygen to support prolyl hydroxylase domain (PHD) activity and proline-hydroxylated HIF-1α may be the predominant form associated with the poorer prognosis that higher levels of HIF-1α confer.
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spelling doaj-art-d61ea88e516e49f18f6fe0fe2b4b05152025-08-20T03:10:47ZengPublic Library of Science (PLoS)PLoS ONE1932-62032014-01-0192e8895510.1371/journal.pone.0088955Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.Cameron E SnellHelen TurleyAlan McIntyreDemin LiMassimo MasieroChristopher J SchofieldKevin C GatterAdrian L HarrisFrancesco PezzellaThe stabilisation of HIF-α is central to the transcriptional response of animals to hypoxia, regulating the expression of hundreds of genes including those involved in angiogenesis, metabolism and metastasis. HIF-α is degraded under normoxic conditions by proline hydroxylation, which allows for recognition and ubiquitination by the von-Hippel-Lindau (VHL) E3 ligase complex. The aim of our study was to investigate the posttranslational modification of HIF-1α in tumours, to assess whether there are additional mechanisms besides reduced hydroxylation leading to stability. To this end we optimised antibodies against the proline-hydroxylated forms of HIF-1α for use in formalin fixed paraffin embedded (FFPE) immunohistochemistry to assess effects in tumour cells in vivo. We found that HIF-1α proline-hydroxylated at both VHL binding sites (Pro402 and Pro564), was present in hypoxic regions of a wide range of tumours, tumour xenografts and in moderately hypoxic cells in vitro. Staining for hydroxylated HIF-1α can identify a subset of breast cancer patients with poorer prognosis and may be a better marker than total HIF-1α levels. The expression of unhydroxylated HIF-1α positively correlates with VHL in breast cancer suggesting that VHL may be rate-limiting for HIF degradation. Our conclusions are that the degradation of proline-hydroxylated HIF-1α may be rate-limited in tumours and therefore provides new insights into mechanisms of HIF upregulation. Persistence of proline-hydroxylated HIF-1α in perinecrotic areas suggests there is adequate oxygen to support prolyl hydroxylase domain (PHD) activity and proline-hydroxylated HIF-1α may be the predominant form associated with the poorer prognosis that higher levels of HIF-1α confer.https://doi.org/10.1371/journal.pone.0088955
spellingShingle Cameron E Snell
Helen Turley
Alan McIntyre
Demin Li
Massimo Masiero
Christopher J Schofield
Kevin C Gatter
Adrian L Harris
Francesco Pezzella
Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
PLoS ONE
title Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
title_full Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
title_fullStr Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
title_full_unstemmed Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
title_short Proline-hydroxylated hypoxia-inducible factor 1α (HIF-1α) upregulation in human tumours.
title_sort proline hydroxylated hypoxia inducible factor 1α hif 1α upregulation in human tumours
url https://doi.org/10.1371/journal.pone.0088955
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