Livedoid Vasculopathy Successfully Treated With JAK Inhibitors

ABSTRACT Livedoid vasculopathy is a rare thrombotic disease of the small blood vessels. It manifests as fixed violaceous macules, noninflammatory retiform purpura, painful ulcers, and white atrophic scars on the lower extremities. The pathophysiology involves the type 1 interferon pathway. Many pati...

Full description

Saved in:
Bibliographic Details
Main Authors: Antoine Delpuech, Emilie Tournier, Pierre Sohier, Nicolas Dupin, Chloe Challamel, Sara Altandi, Serge Boulinguez, Carle Paul
Format: Article
Language:English
Published: Wiley 2025-06-01
Series:JEADV Clinical Practice
Subjects:
Online Access:https://doi.org/10.1002/jvc2.593
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:ABSTRACT Livedoid vasculopathy is a rare thrombotic disease of the small blood vessels. It manifests as fixed violaceous macules, noninflammatory retiform purpura, painful ulcers, and white atrophic scars on the lower extremities. The pathophysiology involves the type 1 interferon pathway. Many patients do not improve with oral anticoagulants. We report here two cases of patients with refractory livedoid vasculopathy treated successfully with JAK inhibitors. The first patient was treated with baricitinib with complete remission of leg ulcers after 4 months of treatment. The second patient was treated with upadacitinib and achieved complete remission after 6 months of treatment. Clinical and biological tolerability was excellent in both patients. JAK inhibitors, through their effect on the interferon pathway, may be a promising treatment for livedoid vasculopathy.
ISSN:2768-6566