Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India

Introduction Acute promyelocytic leukemia (APL) is a subtype of acute myeloid leukemia with specific molecular pathogenesis, clinical features, and treatment. It is cytogenetically characterized by translocation t (15;17) (q24;q21). The location of breakpoints within the PML gene determin...

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Main Authors: Shweta Gondha, Prerna Walia, Beena Brahmbhatt, Jayendrakumar Patel, Toral Mandalia, Disha Jethva
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2025-06-01
Series:Indian Journal of Medical and Paediatric Oncology
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Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1801738
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author Shweta Gondha
Prerna Walia
Beena Brahmbhatt
Jayendrakumar Patel
Toral Mandalia
Disha Jethva
author_facet Shweta Gondha
Prerna Walia
Beena Brahmbhatt
Jayendrakumar Patel
Toral Mandalia
Disha Jethva
author_sort Shweta Gondha
collection DOAJ
description Introduction Acute promyelocytic leukemia (APL) is a subtype of acute myeloid leukemia with specific molecular pathogenesis, clinical features, and treatment. It is cytogenetically characterized by translocation t (15;17) (q24;q21). The location of breakpoints within the PML gene determines the formation of distinct promyelocytic leukemia-retinoic acid receptor α (PML-RARα) transcript subtypes which have prognostic significance. Breakpoints in intron 6 result in the long (L or bcr-1) subtype, those in exon 6 produce the variant (V or bcr-2) subtype, and breakpoints in intron 3 lead to the short (S or bcr-3) subtype.
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series Indian Journal of Medical and Paediatric Oncology
spelling doaj-art-d5a5bbdef6c0474290f930fc64452ada2025-08-20T02:22:34ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58510975-21292025-06-01460331231710.1055/s-0044-1801738Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western IndiaShweta Gondha0Prerna Walia1Beena Brahmbhatt2Jayendrakumar Patel3Toral Mandalia4Disha Jethva5Department of Oncopathology, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, IndiaDepartment of Oncopathology, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, IndiaDepartment of Oncopathology, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, IndiaMolecular Diagnostic and Research Lab, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, IndiaMolecular Diagnostic and Research Lab, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, IndiaMolecular Diagnostic and Research Lab, The Gujarat Cancer and Research Institute, Ahmedabad, Gujarat, India Introduction Acute promyelocytic leukemia (APL) is a subtype of acute myeloid leukemia with specific molecular pathogenesis, clinical features, and treatment. It is cytogenetically characterized by translocation t (15;17) (q24;q21). The location of breakpoints within the PML gene determines the formation of distinct promyelocytic leukemia-retinoic acid receptor α (PML-RARα) transcript subtypes which have prognostic significance. Breakpoints in intron 6 result in the long (L or bcr-1) subtype, those in exon 6 produce the variant (V or bcr-2) subtype, and breakpoints in intron 3 lead to the short (S or bcr-3) subtype.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1801738acute promyelocytic leukemiaPML-RARα transcriptsbcr-3 transcript
spellingShingle Shweta Gondha
Prerna Walia
Beena Brahmbhatt
Jayendrakumar Patel
Toral Mandalia
Disha Jethva
Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
Indian Journal of Medical and Paediatric Oncology
acute promyelocytic leukemia
PML-RARα transcripts
bcr-3 transcript
title Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
title_full Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
title_fullStr Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
title_full_unstemmed Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
title_short Pattern of Expression of PML-RARα Transcripts in Acute Promyelocytic Leukemia Patients and Its Correlation with Overall Survival: A Retrospective Study from Western India
title_sort pattern of expression of pml rarα transcripts in acute promyelocytic leukemia patients and its correlation with overall survival a retrospective study from western india
topic acute promyelocytic leukemia
PML-RARα transcripts
bcr-3 transcript
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1801738
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