Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran

Background. Thyroid peroxidase gene (TPO) mutations are one of the most common causes of thyroid dyshormonogenesis in patients with congenital hypothyroidism (CH). In this study, the prevalence of TPO gene mutations in patients with thyroid dyshormonogenesis in Isfahan was investigated. Methods. In...

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Main Authors: Mahin Hashemipour, Fahimeh Soheilipour, Sakineh Karimizare, Hossein Khanahmad, Morteza Karimipour, Sepideh Aminzadeh, Leila Kokabee, Massoud Amini, Silva Hovsepian, Rezvaneh Hadian
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:International Journal of Endocrinology
Online Access:http://dx.doi.org/10.1155/2012/717283
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author Mahin Hashemipour
Fahimeh Soheilipour
Sakineh Karimizare
Hossein Khanahmad
Morteza Karimipour
Sepideh Aminzadeh
Leila Kokabee
Massoud Amini
Silva Hovsepian
Rezvaneh Hadian
author_facet Mahin Hashemipour
Fahimeh Soheilipour
Sakineh Karimizare
Hossein Khanahmad
Morteza Karimipour
Sepideh Aminzadeh
Leila Kokabee
Massoud Amini
Silva Hovsepian
Rezvaneh Hadian
author_sort Mahin Hashemipour
collection DOAJ
description Background. Thyroid peroxidase gene (TPO) mutations are one of the most common causes of thyroid dyshormonogenesis in patients with congenital hypothyroidism (CH). In this study, the prevalence of TPO gene mutations in patients with thyroid dyshormonogenesis in Isfahan was investigated. Methods. In this cross-sectional study, genomic DNA of 41 patients with permanent CH due to thyroid dyshormonogenesis was extracted using the salting out method. The 17 exonic regions of the TPO gene were amplified. SSCP technique was performed for scanning of the exonic regions of the TPO gene, except exon 8. DNA sequencing was performed for those with different migration patterns in SSCP by chain termination method. Exon 8 was sequenced directly in all patients. In 4 patients, all fragments were also sequenced. Results. One missense mutation c.2669G>A (NM_000547.5) at exon 15 (14th coding exon) in one patient in homozygous form and seven different single nucleotide polymorphisms (SNPs) in exons 1, 7, 8, 11, and 15 of TPO gene. Conclusion. The TPO gene mutations among CH patients with dyshormonogenesis in Isfahan were less frequent in comparison with other similar studies. It may be due to the presence of other unknown gene mutations which could not be detected by SSCP and sequencing methods.
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spelling doaj-art-d528decbb8514d4c864c49b97ad88d2f2025-08-20T02:19:58ZengWileyInternational Journal of Endocrinology1687-83371687-83452012-01-01201210.1155/2012/717283717283Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, IranMahin Hashemipour0Fahimeh Soheilipour1Sakineh Karimizare2Hossein Khanahmad3Morteza Karimipour4Sepideh Aminzadeh5Leila Kokabee6Massoud Amini7Silva Hovsepian8Rezvaneh Hadian9Isfahan Endocrine and Metabolism Research Center, Child Growth and Development Research Center, Isfahan University of Medical Sciences, Isfahan, IranIsfahan Endocrine and Metabolism Research Center, Child Growth and Development Research Center, Isfahan University of Medical Sciences, Isfahan, IranMolecular Medicine Department, Pasteur Institute of Iran, Tehran, IranMolecular Medicine Department, Pasteur Institute of Iran, Tehran, IranMolecular Medicine Department, Pasteur Institute of Iran, Tehran, IranMolecular Medicine Department, Pasteur Institute of Iran, Tehran, IranMolecular Medicine Department, Pasteur Institute of Iran, Tehran, IranIsfahan Endocrine and Metabolism Research Center, Isfahan University of Medical Sciences, Isfahan, IranIsfahan Endocrine and Metabolism Research Center, Child Growth and Development Research Center, Isfahan University of Medical Sciences, Isfahan, IranIsfahan Endocrine and Metabolism Research Center, Isfahan University of Medical Sciences, Isfahan, IranBackground. Thyroid peroxidase gene (TPO) mutations are one of the most common causes of thyroid dyshormonogenesis in patients with congenital hypothyroidism (CH). In this study, the prevalence of TPO gene mutations in patients with thyroid dyshormonogenesis in Isfahan was investigated. Methods. In this cross-sectional study, genomic DNA of 41 patients with permanent CH due to thyroid dyshormonogenesis was extracted using the salting out method. The 17 exonic regions of the TPO gene were amplified. SSCP technique was performed for scanning of the exonic regions of the TPO gene, except exon 8. DNA sequencing was performed for those with different migration patterns in SSCP by chain termination method. Exon 8 was sequenced directly in all patients. In 4 patients, all fragments were also sequenced. Results. One missense mutation c.2669G>A (NM_000547.5) at exon 15 (14th coding exon) in one patient in homozygous form and seven different single nucleotide polymorphisms (SNPs) in exons 1, 7, 8, 11, and 15 of TPO gene. Conclusion. The TPO gene mutations among CH patients with dyshormonogenesis in Isfahan were less frequent in comparison with other similar studies. It may be due to the presence of other unknown gene mutations which could not be detected by SSCP and sequencing methods.http://dx.doi.org/10.1155/2012/717283
spellingShingle Mahin Hashemipour
Fahimeh Soheilipour
Sakineh Karimizare
Hossein Khanahmad
Morteza Karimipour
Sepideh Aminzadeh
Leila Kokabee
Massoud Amini
Silva Hovsepian
Rezvaneh Hadian
Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
International Journal of Endocrinology
title Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
title_full Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
title_fullStr Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
title_full_unstemmed Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
title_short Thyroid Peroxidase Gene Mutation in Patients with Congenital Hypothyroidism in Isfahan, Iran
title_sort thyroid peroxidase gene mutation in patients with congenital hypothyroidism in isfahan iran
url http://dx.doi.org/10.1155/2012/717283
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