An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature

Abstract. Bartter syndrome is a group of autosomal recessive renal tubular disorders; it has two types of presentation: antenatal and classic. The antenatal type presents as severe unexplained polyhydramnios in the second trimester. This is due to fetal urinary losses of sodium, chloride, and potass...

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Main Authors: Aleena M. Shajan, Manish Kumar, Preethi Navaneethan, Sumita Danda, Manisha M. Beck, Yang Pan
Format: Article
Language:English
Published: Wolters Kluwer Health 2023-04-01
Series:Maternal-Fetal Medicine
Online Access:http://journals.lww.com/10.1097/FM9.0000000000000182
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author Aleena M. Shajan
Manish Kumar
Preethi Navaneethan
Sumita Danda
Manisha M. Beck
Yang Pan
author_facet Aleena M. Shajan
Manish Kumar
Preethi Navaneethan
Sumita Danda
Manisha M. Beck
Yang Pan
author_sort Aleena M. Shajan
collection DOAJ
description Abstract. Bartter syndrome is a group of autosomal recessive renal tubular disorders; it has two types of presentation: antenatal and classic. The antenatal type presents as severe unexplained polyhydramnios in the second trimester. This is due to fetal urinary losses of sodium, chloride, and potassium, leading to fetal polyuria. The classic type presents in the late neonatal or infancy stage, with dehydration, dyselectrolytemia, failure to thrive, and nephrocalcinosis. Antenatal scans are normal in such cases. Type I and II Bartter syndrome presents in the antenatal period, whereas type IV has a classic presentation. We describe an unusual case of type IVa Bartter syndrome presenting in the antenatal period, with severe polyhydramnios. The initial diagnosis was made based on amniotic fluid chloride levels and later confirmed by performing a genetic test. Genetic testing is important for confirming diagnosis and prognostication regarding the condition.
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institution Kabale University
issn 2096-6954
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language English
publishDate 2023-04-01
publisher Wolters Kluwer Health
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series Maternal-Fetal Medicine
spelling doaj-art-d50dcd992c1b429db9de86c6e3b209e42025-08-20T03:48:23ZengWolters Kluwer HealthMaternal-Fetal Medicine2096-69542641-58952023-04-015212813010.1097/FM9.0000000000000182202304000-00012An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of LiteratureAleena M. Shajan0Manish Kumar1Preethi Navaneethan2Sumita Danda3Manisha M. Beck4Yang Pan1 Fetal Medicine Unit, Department of ObGyn, Christian Medical College and Hospital, Vellore, Tamil Nadu 632004, India2 Department of Neonatology, Christian Medical College and Hospital, Vellore, Tamil Nadu 632004, India1 Fetal Medicine Unit, Department of ObGyn, Christian Medical College and Hospital, Vellore, Tamil Nadu 632004, India3 Department of Clinical Genetics, Christian Medical College and Hospital, Vellore, Tamil Nadu 632004, India.1 Fetal Medicine Unit, Department of ObGyn, Christian Medical College and Hospital, Vellore, Tamil Nadu 632004, IndiaAbstract. Bartter syndrome is a group of autosomal recessive renal tubular disorders; it has two types of presentation: antenatal and classic. The antenatal type presents as severe unexplained polyhydramnios in the second trimester. This is due to fetal urinary losses of sodium, chloride, and potassium, leading to fetal polyuria. The classic type presents in the late neonatal or infancy stage, with dehydration, dyselectrolytemia, failure to thrive, and nephrocalcinosis. Antenatal scans are normal in such cases. Type I and II Bartter syndrome presents in the antenatal period, whereas type IV has a classic presentation. We describe an unusual case of type IVa Bartter syndrome presenting in the antenatal period, with severe polyhydramnios. The initial diagnosis was made based on amniotic fluid chloride levels and later confirmed by performing a genetic test. Genetic testing is important for confirming diagnosis and prognostication regarding the condition.http://journals.lww.com/10.1097/FM9.0000000000000182
spellingShingle Aleena M. Shajan
Manish Kumar
Preethi Navaneethan
Sumita Danda
Manisha M. Beck
Yang Pan
An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
Maternal-Fetal Medicine
title An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
title_full An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
title_fullStr An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
title_full_unstemmed An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
title_short An Unusual Case of BSND Gene–Related (Type IV) Bartter Syndrome Presenting as Antenatal Bartter Syndrome: A Case Report and Review of Literature
title_sort unusual case of bsnd gene related type iv bartter syndrome presenting as antenatal bartter syndrome a case report and review of literature
url http://journals.lww.com/10.1097/FM9.0000000000000182
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