Isolated cardiac sarcoidosis: A clinical challenge
Sarcoidosis is an inflammatory disease characterised by non-caseating granulomas of unclear aetiology. Isolated cardiac sarcoidosis (ICS) is rare and occurs when there is granulomatous infiltration of myocardial tissue without evidence of extracardiac sarcoidosis. The heterogeneity in clinical manif...
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| Format: | Article |
| Language: | English |
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Elsevier
2024-11-01
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| Series: | Clinical Medicine |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1470211824054307 |
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| author | Paul Njoku Sumbal Rani Orestis Paschalis Emanuela Alati Amit K.J. Mandal Constantinos G. Missouris |
| author_facet | Paul Njoku Sumbal Rani Orestis Paschalis Emanuela Alati Amit K.J. Mandal Constantinos G. Missouris |
| author_sort | Paul Njoku |
| collection | DOAJ |
| description | Sarcoidosis is an inflammatory disease characterised by non-caseating granulomas of unclear aetiology. Isolated cardiac sarcoidosis (ICS) is rare and occurs when there is granulomatous infiltration of myocardial tissue without evidence of extracardiac sarcoidosis. The heterogeneity in clinical manifestations often presents a diagnostic challenge which leads to delays in treatment initiation. Our case highlights the often quiescent presentation of ICS, the importance of early treatment and the diagnostic challenges that contribute to its underdiagnosis. |
| format | Article |
| id | doaj-art-d31d1617047e4c93ae3ddc8b39760268 |
| institution | OA Journals |
| issn | 1470-2118 |
| language | English |
| publishDate | 2024-11-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Clinical Medicine |
| spelling | doaj-art-d31d1617047e4c93ae3ddc8b397602682025-08-20T02:06:57ZengElsevierClinical Medicine1470-21182024-11-0124610024510.1016/j.clinme.2024.100245Isolated cardiac sarcoidosis: A clinical challengePaul Njoku0Sumbal Rani1Orestis Paschalis2Emanuela Alati3Amit K.J. Mandal4Constantinos G. Missouris5Departments of Cardiology and Medicine, Wexham Park Hospital, Frimley Health NHS Foundation Trust, United Kingdom; Corresponding author at: Wexham Park Hospital, Slough, Berkshire SL2 4HL, United Kingdom.Departments of Cardiology and Medicine, Wexham Park Hospital, Frimley Health NHS Foundation Trust, United KingdomUniversity of Cambridge, United KingdomDepartments of Cardiology and Medicine, Wexham Park Hospital, Frimley Health NHS Foundation Trust, United KingdomDepartments of Cardiology and Medicine, Wexham Park Hospital, Frimley Health NHS Foundation Trust, United KingdomDepartments of Cardiology and Medicine, Wexham Park Hospital, Frimley Health NHS Foundation Trust, United Kingdom; Department of Clinical Cardiology, University of Nicosia Medical School, CyprusSarcoidosis is an inflammatory disease characterised by non-caseating granulomas of unclear aetiology. Isolated cardiac sarcoidosis (ICS) is rare and occurs when there is granulomatous infiltration of myocardial tissue without evidence of extracardiac sarcoidosis. The heterogeneity in clinical manifestations often presents a diagnostic challenge which leads to delays in treatment initiation. Our case highlights the often quiescent presentation of ICS, the importance of early treatment and the diagnostic challenges that contribute to its underdiagnosis.http://www.sciencedirect.com/science/article/pii/S1470211824054307Cardiac arrhythmiaSarcoidCardiac sarcoidPET scanCardiac magnetic resonanceIsolated cardiac sarcoidosis |
| spellingShingle | Paul Njoku Sumbal Rani Orestis Paschalis Emanuela Alati Amit K.J. Mandal Constantinos G. Missouris Isolated cardiac sarcoidosis: A clinical challenge Clinical Medicine Cardiac arrhythmia Sarcoid Cardiac sarcoid PET scan Cardiac magnetic resonance Isolated cardiac sarcoidosis |
| title | Isolated cardiac sarcoidosis: A clinical challenge |
| title_full | Isolated cardiac sarcoidosis: A clinical challenge |
| title_fullStr | Isolated cardiac sarcoidosis: A clinical challenge |
| title_full_unstemmed | Isolated cardiac sarcoidosis: A clinical challenge |
| title_short | Isolated cardiac sarcoidosis: A clinical challenge |
| title_sort | isolated cardiac sarcoidosis a clinical challenge |
| topic | Cardiac arrhythmia Sarcoid Cardiac sarcoid PET scan Cardiac magnetic resonance Isolated cardiac sarcoidosis |
| url | http://www.sciencedirect.com/science/article/pii/S1470211824054307 |
| work_keys_str_mv | AT paulnjoku isolatedcardiacsarcoidosisaclinicalchallenge AT sumbalrani isolatedcardiacsarcoidosisaclinicalchallenge AT orestispaschalis isolatedcardiacsarcoidosisaclinicalchallenge AT emanuelaalati isolatedcardiacsarcoidosisaclinicalchallenge AT amitkjmandal isolatedcardiacsarcoidosisaclinicalchallenge AT constantinosgmissouris isolatedcardiacsarcoidosisaclinicalchallenge |