Histological Findings of ETosis in Hermansky-Pudlak Syndrome with Pulmonary Fibrosis: A Follow-Up Case Report
Hermansky-Pudlak syndrome (HPS), both alone and in conjunction with pulmonary fibrosis (HPS-PF), is a rare, genetically heterogeneous, autosomal recessive disorder that affects multiple organs, including the lungs. In cases of HPS-PF, pulmonary fibrosis is preceded by local inflammation. We prese...
Saved in:
| Main Authors: | Sergio Michael Navarro, Aneel Ashrani, Myung Soo Park, Dong Chen |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Korean Society for Thoracic & Cardiovascular Surgery
2025-01-01
|
| Series: | Journal of Chest Surgery |
| Subjects: | |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
Similar Items
-
Hermansky-Pudlak Syndrome: An unusual pattern of pulmonary fibrosis
by: Matthew Donnan, et al.
Published: (2024-01-01) -
Application of Forced Oscillation Technique in Assessing Pulmonary Fibrosis in Hermansky–Pudlak Syndrome
by: Wilfredo De Jesús-Rojas, et al.
Published: (2024-10-01) -
Hermansky-Pudlak syndrome 2 — a novel mutation with factor VII deficiency: a fluke from India
by: Vibha Gupta, et al.
Published: (2025-07-01) -
Homozygous HPS1 variant in an Iranian sibling pair with Hermansky–Pudlak syndrome
by: Ensiyeh Bahadoran, et al.
Published: (2025-08-01) -
Kidney melanosis associated with a novel HSP-1 Hermansky-Pudlak oculocutaneous albinism mutation: a case report
by: Alaa A. Ali, et al.
Published: (2025-07-01)