Case of congenital Langerhans cells histiocytosis in an infant
In this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characteri...
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| Format: | Article |
| Language: | Russian |
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ABV-press
2014-07-01
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| Series: | Онкогематология |
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| Online Access: | https://oncohematology.abvpress.ru/ongm/article/view/98 |
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| author | T. T. Valiev L. A. Makhonova A. M. Kovrigina E. N. Sholokhova N. N. Tupitsyn I. N. Serebryakova G. L. Mentkevich |
| author_facet | T. T. Valiev L. A. Makhonova A. M. Kovrigina E. N. Sholokhova N. N. Tupitsyn I. N. Serebryakova G. L. Mentkevich |
| author_sort | T. T. Valiev |
| collection | DOAJ |
| description | In this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characterized. Authors concluded that timely diagnostics is very important to risk-adapted therapy at children with LCH. |
| format | Article |
| id | doaj-art-d26e6e25a9a04fc5b59604abbb1ab07f |
| institution | DOAJ |
| issn | 1818-8346 2413-4023 |
| language | Russian |
| publishDate | 2014-07-01 |
| publisher | ABV-press |
| record_format | Article |
| series | Онкогематология |
| spelling | doaj-art-d26e6e25a9a04fc5b59604abbb1ab07f2025-08-20T03:21:30ZrusABV-pressОнкогематология1818-83462413-40232014-07-0162192210.17650/1818-8346-2011-6-2-19-22113Case of congenital Langerhans cells histiocytosis in an infantT. T. Valiev0L. A. Makhonova1A. M. Kovrigina2E. N. Sholokhova3N. N. Tupitsyn4I. N. Serebryakova5G. L. Mentkevich6Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesInstitute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesIn this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characterized. Authors concluded that timely diagnostics is very important to risk-adapted therapy at children with LCH.https://oncohematology.abvpress.ru/ongm/article/view/98langerhans cell histiocytosisnewbornsdiagnosistherapy |
| spellingShingle | T. T. Valiev L. A. Makhonova A. M. Kovrigina E. N. Sholokhova N. N. Tupitsyn I. N. Serebryakova G. L. Mentkevich Case of congenital Langerhans cells histiocytosis in an infant Онкогематология langerhans cell histiocytosis newborns diagnosis therapy |
| title | Case of congenital Langerhans cells histiocytosis in an infant |
| title_full | Case of congenital Langerhans cells histiocytosis in an infant |
| title_fullStr | Case of congenital Langerhans cells histiocytosis in an infant |
| title_full_unstemmed | Case of congenital Langerhans cells histiocytosis in an infant |
| title_short | Case of congenital Langerhans cells histiocytosis in an infant |
| title_sort | case of congenital langerhans cells histiocytosis in an infant |
| topic | langerhans cell histiocytosis newborns diagnosis therapy |
| url | https://oncohematology.abvpress.ru/ongm/article/view/98 |
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