Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)

We report on the clinical, cytogenetic, and imaging findings in a patient with a 7q terminal deletion. The 11-year-old girl had mental retardation, microcephaly, a distinctive face, relatively small hands and feet, and sacral dysgenesis. High resolution GTG banding (550-850 bands) showed a 7q termin...

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Main Authors: Pen-Hua Su, Jia-Yuh Chen, Suh-Jen Chen, Teng-Fu Tsao, Yu-Jie Lai
Format: Article
Language:English
Published: Elsevier 2008-10-01
Series:Pediatrics and Neonatology
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Online Access:http://www.sciencedirect.com/science/article/pii/S1875957209600073
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author Pen-Hua Su
Jia-Yuh Chen
Suh-Jen Chen
Teng-Fu Tsao
Yu-Jie Lai
author_facet Pen-Hua Su
Jia-Yuh Chen
Suh-Jen Chen
Teng-Fu Tsao
Yu-Jie Lai
author_sort Pen-Hua Su
collection DOAJ
description We report on the clinical, cytogenetic, and imaging findings in a patient with a 7q terminal deletion. The 11-year-old girl had mental retardation, microcephaly, a distinctive face, relatively small hands and feet, and sacral dysgenesis. High resolution GTG banding (550-850 bands) showed a 7q terminal deletion. A detailed evaluation of associated malformations and the overall clinical picture should be taken into account when identifying the underlying diagnosis in cases of sacral dysgenesis with mental retardation.
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institution OA Journals
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publishDate 2008-10-01
publisher Elsevier
record_format Article
series Pediatrics and Neonatology
spelling doaj-art-d03a3ea2d2274e1aa1da84f98524b7c12025-08-20T02:03:54ZengElsevierPediatrics and Neonatology1875-95722008-10-0149518919210.1016/S1875-9572(09)60007-3Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)Pen-Hua Su0Jia-Yuh Chen1Suh-Jen Chen2Teng-Fu Tsao3Yu-Jie Lai4Division of Genetics and Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, TaiwanDepartment of Pediatrics, Chung Shan Medical University, Taichung, TaiwanDivision of Genetics and Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, TaiwanDepartment of Diagnostic Radiology, Chung Shan Medical University Hospital, Taichung, TaiwanDivision of Genetics and Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, TaiwanWe report on the clinical, cytogenetic, and imaging findings in a patient with a 7q terminal deletion. The 11-year-old girl had mental retardation, microcephaly, a distinctive face, relatively small hands and feet, and sacral dysgenesis. High resolution GTG banding (550-850 bands) showed a 7q terminal deletion. A detailed evaluation of associated malformations and the overall clinical picture should be taken into account when identifying the underlying diagnosis in cases of sacral dysgenesis with mental retardation.http://www.sciencedirect.com/science/article/pii/S1875957209600073chromosome 7qdeletionsacral dysgenesis
spellingShingle Pen-Hua Su
Jia-Yuh Chen
Suh-Jen Chen
Teng-Fu Tsao
Yu-Jie Lai
Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
Pediatrics and Neonatology
chromosome 7q
deletion
sacral dysgenesis
title Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
title_full Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
title_fullStr Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
title_full_unstemmed Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
title_short Sacral Dysgenesis Associated with Terminal Deletion of Chromosome 7 (q36-qter)
title_sort sacral dysgenesis associated with terminal deletion of chromosome 7 q36 qter
topic chromosome 7q
deletion
sacral dysgenesis
url http://www.sciencedirect.com/science/article/pii/S1875957209600073
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AT jiayuhchen sacraldysgenesisassociatedwithterminaldeletionofchromosome7q36qter
AT suhjenchen sacraldysgenesisassociatedwithterminaldeletionofchromosome7q36qter
AT tengfutsao sacraldysgenesisassociatedwithterminaldeletionofchromosome7q36qter
AT yujielai sacraldysgenesisassociatedwithterminaldeletionofchromosome7q36qter