When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report

Langerhans cell histiocytosis (LCH) is a rare and heterogeneous disease that appears mainly in children and frequently affects bone structures such as the skull, with possible involvement of the orbit. In this paper, we present the case of an 11-year-old boy who came to the emergency department wit...

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Main Authors: Henrique Teixeira, Mariana Branco Lopes, Ricardo São Pedro, Maria Helena Rosa, Luís Antunes
Format: Article
Language:English
Published: Portuguese Society of Otolaryngology and Head and Neck Surgery 2022-03-01
Series:Revista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
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Online Access:https://journalsporl.com/index.php/sporl/article/view/2161
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author Henrique Teixeira
Mariana Branco Lopes
Ricardo São Pedro
Maria Helena Rosa
Luís Antunes
author_facet Henrique Teixeira
Mariana Branco Lopes
Ricardo São Pedro
Maria Helena Rosa
Luís Antunes
author_sort Henrique Teixeira
collection DOAJ
description Langerhans cell histiocytosis (LCH) is a rare and heterogeneous disease that appears mainly in children and frequently affects bone structures such as the skull, with possible involvement of the orbit. In this paper, we present the case of an 11-year-old boy who came to the emergency department with left periorbital edema and erythema with about 10 days of progressive worsening. Computed tomography was compatible with complicated left frontal sinusitis with bone erosion into the orbit and intracranial compartment, and magnetic resonance imaging corroborated these findings. Due to the lack of improvement with medical therapy, surgical exploration was performed through an external approach, identifying a lesion in which the anatomopathological study confirmed the diagnosis of LCH.
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publishDate 2022-03-01
publisher Portuguese Society of Otolaryngology and Head and Neck Surgery
record_format Article
series Revista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
spelling doaj-art-cd8fc78960ef48d8be7f312387fbbbb72025-08-20T03:23:43ZengPortuguese Society of Otolaryngology and Head and Neck SurgeryRevista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço2184-64992022-03-0160110.34631/sporl.997When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-reportHenrique Teixeira0Mariana Branco Lopes1Ricardo São Pedro2Maria Helena Rosa3Luís Antunes4Hospital Garcia de Orta, PortugalHospital Garcia de Orta, PortugalHospital Garcia de Orta, PortugalHospital Garcia de Orta, PortugalHospital Garcia de Orta, Portugal Langerhans cell histiocytosis (LCH) is a rare and heterogeneous disease that appears mainly in children and frequently affects bone structures such as the skull, with possible involvement of the orbit. In this paper, we present the case of an 11-year-old boy who came to the emergency department with left periorbital edema and erythema with about 10 days of progressive worsening. Computed tomography was compatible with complicated left frontal sinusitis with bone erosion into the orbit and intracranial compartment, and magnetic resonance imaging corroborated these findings. Due to the lack of improvement with medical therapy, surgical exploration was performed through an external approach, identifying a lesion in which the anatomopathological study confirmed the diagnosis of LCH. https://journalsporl.com/index.php/sporl/article/view/2161Langerhans cell HistiocytosisPre-septal cellulitisFrontal boneOrbitPediatrics
spellingShingle Henrique Teixeira
Mariana Branco Lopes
Ricardo São Pedro
Maria Helena Rosa
Luís Antunes
When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
Revista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
Langerhans cell Histiocytosis
Pre-septal cellulitis
Frontal bone
Orbit
Pediatrics
title When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
title_full When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
title_fullStr When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
title_full_unstemmed When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
title_short When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report
title_sort when it s not a complicated frontal sinusitis a langerhans cell histiocytosis case report
topic Langerhans cell Histiocytosis
Pre-septal cellulitis
Frontal bone
Orbit
Pediatrics
url https://journalsporl.com/index.php/sporl/article/view/2161
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