A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.

Previously we have shown that compacted DNA nanoparticles can drive high levels of transgene expression after subretinal injection in the mouse eye. Here we delivered compacted DNA nanoparticles containing a therapeutic gene to the retinas of a mouse model of retinitis pigmentosa. Nanoparticles cont...

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Main Authors: Xue Cai, Zack Nash, Shannon M Conley, Steven J Fliesler, Mark J Cooper, Muna I Naash
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2009-01-01
Series:PLoS ONE
Online Access:https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0005290&type=printable
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author Xue Cai
Zack Nash
Shannon M Conley
Steven J Fliesler
Mark J Cooper
Muna I Naash
author_facet Xue Cai
Zack Nash
Shannon M Conley
Steven J Fliesler
Mark J Cooper
Muna I Naash
author_sort Xue Cai
collection DOAJ
description Previously we have shown that compacted DNA nanoparticles can drive high levels of transgene expression after subretinal injection in the mouse eye. Here we delivered compacted DNA nanoparticles containing a therapeutic gene to the retinas of a mouse model of retinitis pigmentosa. Nanoparticles containing the wild-type retinal degeneration slow (Rds) gene were injected into the subretinal space of rds(+/-) mice on postnatal day 5. Gene expression was sustained for up to four months at levels up to four times higher than in controls injected with saline or naked DNA. The nanoparticles were taken up into virtually all photoreceptors and mediated significant structural and biochemical rescue of the disease without histological or functional evidence of toxicity. Electroretinogram recordings showed that nanoparticle-mediated gene transfer restored cone function to a near-normal level in contrast to transfer of naked plasmid DNA. Rod function was also improved. These findings demonstrate that compacted DNA nanoparticles represent a viable option for development of gene-based interventions for ocular diseases and obviate major barriers commonly encountered with non-viral based therapies.
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spelling doaj-art-ca011eb9110643069edecc239df414072025-08-20T02:38:27ZengPublic Library of Science (PLoS)PLoS ONE1932-62032009-01-0144e529010.1371/journal.pone.0005290A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.Xue CaiZack NashShannon M ConleySteven J FlieslerMark J CooperMuna I NaashPreviously we have shown that compacted DNA nanoparticles can drive high levels of transgene expression after subretinal injection in the mouse eye. Here we delivered compacted DNA nanoparticles containing a therapeutic gene to the retinas of a mouse model of retinitis pigmentosa. Nanoparticles containing the wild-type retinal degeneration slow (Rds) gene were injected into the subretinal space of rds(+/-) mice on postnatal day 5. Gene expression was sustained for up to four months at levels up to four times higher than in controls injected with saline or naked DNA. The nanoparticles were taken up into virtually all photoreceptors and mediated significant structural and biochemical rescue of the disease without histological or functional evidence of toxicity. Electroretinogram recordings showed that nanoparticle-mediated gene transfer restored cone function to a near-normal level in contrast to transfer of naked plasmid DNA. Rod function was also improved. These findings demonstrate that compacted DNA nanoparticles represent a viable option for development of gene-based interventions for ocular diseases and obviate major barriers commonly encountered with non-viral based therapies.https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0005290&type=printable
spellingShingle Xue Cai
Zack Nash
Shannon M Conley
Steven J Fliesler
Mark J Cooper
Muna I Naash
A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
PLoS ONE
title A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
title_full A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
title_fullStr A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
title_full_unstemmed A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
title_short A partial structural and functional rescue of a retinitis pigmentosa model with compacted DNA nanoparticles.
title_sort partial structural and functional rescue of a retinitis pigmentosa model with compacted dna nanoparticles
url https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0005290&type=printable
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