Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle

Today we are talking about Craniofacial microsomia or First and second branchial arch syndrome (CFM) as the second most common congenital malformation of the maxillofacial area after cleft lip and palate with extremely diverse phenotype and different types. First and second branchial arch syndrome a...

Full description

Saved in:
Bibliographic Details
Main Authors: O. Z. Topolnitskiy, T. A. Tutueva, N. I. Imshenetskaya, M. A. Mamedov
Format: Article
Language:Russian
Published: LLC "Endo Press" 2019-02-01
Series:Эндодонтия Today
Subjects:
Online Access:https://www.endodont.ru/jour/article/view/17
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849244628352499712
author O. Z. Topolnitskiy
T. A. Tutueva
N. I. Imshenetskaya
M. A. Mamedov
author_facet O. Z. Topolnitskiy
T. A. Tutueva
N. I. Imshenetskaya
M. A. Mamedov
author_sort O. Z. Topolnitskiy
collection DOAJ
description Today we are talking about Craniofacial microsomia or First and second branchial arch syndrome (CFM) as the second most common congenital malformation of the maxillofacial area after cleft lip and palate with extremely diverse phenotype and different types. First and second branchial arch syndrome amount to 11% of all defects in the formation of tissues and organs of the maxillofacial area. The aim of our study was to improve the quality of prevention and care for patients with CFM syndrome. Questionnaires developed for parents have included questions for the anamnesis of life and disease, hereditary factors, gestation course, the growth and development of children with such pathology. The data of 18 patients treated at the Department of pediatric maxillofacial surgery of MSMSU were analyzed. During the study exogenous and endogenous factors influencing the development of craniofacial microsomia syndromes (CFM) were identified. It was justified to use the ears of parents as a template of the missing organ of the child within preoperative preparation. It was revealed that the pathology of the urinary system and small abnormalities of the heart cannot be associated with the symptoms of CFM.
format Article
id doaj-art-c8745345c74f40fdb7c6ce32ac48ca9f
institution Kabale University
issn 1683-2981
1726-7242
language Russian
publishDate 2019-02-01
publisher LLC "Endo Press"
record_format Article
series Эндодонтия Today
spelling doaj-art-c8745345c74f40fdb7c6ce32ac48ca9f2025-08-20T03:59:05ZrusLLC "Endo Press"Эндодонтия Today1683-29811726-72422019-02-01163727510.25636 / PMP.2.2018.3.1417Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricleO. Z. Topolnitskiy0T. A. Tutueva1N. I. Imshenetskaya2M. A. Mamedov3ФГБОУ ВО МГМСУ им. А. И. Евдокимова.ФГБОУ ВО МГМСУ им. А. И. Евдокимова.ФГБОУ ВО МГМСУ им. А. И. Евдокимова.ФГБОУ ВО МГМСУ им. А. И. Евдокимова.Today we are talking about Craniofacial microsomia or First and second branchial arch syndrome (CFM) as the second most common congenital malformation of the maxillofacial area after cleft lip and palate with extremely diverse phenotype and different types. First and second branchial arch syndrome amount to 11% of all defects in the formation of tissues and organs of the maxillofacial area. The aim of our study was to improve the quality of prevention and care for patients with CFM syndrome. Questionnaires developed for parents have included questions for the anamnesis of life and disease, hereditary factors, gestation course, the growth and development of children with such pathology. The data of 18 patients treated at the Department of pediatric maxillofacial surgery of MSMSU were analyzed. During the study exogenous and endogenous factors influencing the development of craniofacial microsomia syndromes (CFM) were identified. It was justified to use the ears of parents as a template of the missing organ of the child within preoperative preparation. It was revealed that the pathology of the urinary system and small abnormalities of the heart cannot be associated with the symptoms of CFM.https://www.endodont.ru/jour/article/view/17craniofacial microsomiacomorbide pathologyexogenous and endogenous factors
spellingShingle O. Z. Topolnitskiy
T. A. Tutueva
N. I. Imshenetskaya
M. A. Mamedov
Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
Эндодонтия Today
craniofacial microsomia
comorbide pathology
exogenous and endogenous factors
title Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
title_full Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
title_fullStr Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
title_full_unstemmed Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
title_short Introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia. Determination of the frequency of inheritance of the shape of the auricle
title_sort introduction of the distance methods of genetic counseling for the parents of children with craniofacial microsomia determination of the frequency of inheritance of the shape of the auricle
topic craniofacial microsomia
comorbide pathology
exogenous and endogenous factors
url https://www.endodont.ru/jour/article/view/17
work_keys_str_mv AT oztopolnitskiy introductionofthedistancemethodsofgeneticcounselingfortheparentsofchildrenwithcraniofacialmicrosomiadeterminationofthefrequencyofinheritanceoftheshapeoftheauricle
AT tatutueva introductionofthedistancemethodsofgeneticcounselingfortheparentsofchildrenwithcraniofacialmicrosomiadeterminationofthefrequencyofinheritanceoftheshapeoftheauricle
AT niimshenetskaya introductionofthedistancemethodsofgeneticcounselingfortheparentsofchildrenwithcraniofacialmicrosomiadeterminationofthefrequencyofinheritanceoftheshapeoftheauricle
AT mamamedov introductionofthedistancemethodsofgeneticcounselingfortheparentsofchildrenwithcraniofacialmicrosomiadeterminationofthefrequencyofinheritanceoftheshapeoftheauricle