Fraser Syndrome-Oral Manifestations and a Dental Care Protocol
Fraser syndrome is a rare genetic malformation with an autosomal recessive pattern of inheritance and an incidence of consanguinity ranging from 15% to 25%. A 5-year-old male patient who is a carrier of Fraser syndrome initiated treatment in the pediatric dentistry sector. The patient was fed parent...
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| Format: | Article |
| Language: | English |
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Wiley
2014-01-01
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| Series: | Case Reports in Dentistry |
| Online Access: | http://dx.doi.org/10.1155/2014/486108 |
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| author | Talita Lopes de Oliveira Giselle Rodrigues de Sant’Anna |
| author_facet | Talita Lopes de Oliveira Giselle Rodrigues de Sant’Anna |
| author_sort | Talita Lopes de Oliveira |
| collection | DOAJ |
| description | Fraser syndrome is a rare genetic malformation with an autosomal recessive pattern of inheritance and an incidence of consanguinity ranging from 15% to 25%. A 5-year-old male patient who is a carrier of Fraser syndrome initiated treatment in the pediatric dentistry sector. The patient was fed parenterally since birth, experienced recurring bouts of chronic lung disease, and was referred to the pediatric dentistry sector by the medical team. Radiographic examination revealed the presence of all permanent teeth. Supragingival dental calculus, halitosis, and gingival inflammation were also observed. Dental calculus was removed by manual scraping, and chemotherapeutic agents were used, chlorhexidine 0,12%, chlorhexidine gel 2%, and PVP-I, to control the bacterial flora. The patient is still being monitored after an 8-year follow-up period, the complications associated with periodontal disease decreased, and since the initiation of treatment, the patient has not needed to be hospitalized because of chronic lung disease. This study reports the case of a patient diagnosed with Fraser syndrome and describes the clinical manifestations (general and oral). |
| format | Article |
| id | doaj-art-c86debf5e7e84fac8439458ce4e003f0 |
| institution | DOAJ |
| issn | 2090-6447 2090-6455 |
| language | English |
| publishDate | 2014-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dentistry |
| spelling | doaj-art-c86debf5e7e84fac8439458ce4e003f02025-08-20T03:24:03ZengWileyCase Reports in Dentistry2090-64472090-64552014-01-01201410.1155/2014/486108486108Fraser Syndrome-Oral Manifestations and a Dental Care ProtocolTalita Lopes de Oliveira0Giselle Rodrigues de Sant’Anna1Cruzeiro do Sul University (UNICSUL), Rua José Garcia de Souza 422, 08673-040 Suzano, SP, BrazilCruzeiro do Sul University, Rua Saturnino dos Santos 106, 04124-150 São Paulo, SP, BrazilFraser syndrome is a rare genetic malformation with an autosomal recessive pattern of inheritance and an incidence of consanguinity ranging from 15% to 25%. A 5-year-old male patient who is a carrier of Fraser syndrome initiated treatment in the pediatric dentistry sector. The patient was fed parenterally since birth, experienced recurring bouts of chronic lung disease, and was referred to the pediatric dentistry sector by the medical team. Radiographic examination revealed the presence of all permanent teeth. Supragingival dental calculus, halitosis, and gingival inflammation were also observed. Dental calculus was removed by manual scraping, and chemotherapeutic agents were used, chlorhexidine 0,12%, chlorhexidine gel 2%, and PVP-I, to control the bacterial flora. The patient is still being monitored after an 8-year follow-up period, the complications associated with periodontal disease decreased, and since the initiation of treatment, the patient has not needed to be hospitalized because of chronic lung disease. This study reports the case of a patient diagnosed with Fraser syndrome and describes the clinical manifestations (general and oral).http://dx.doi.org/10.1155/2014/486108 |
| spellingShingle | Talita Lopes de Oliveira Giselle Rodrigues de Sant’Anna Fraser Syndrome-Oral Manifestations and a Dental Care Protocol Case Reports in Dentistry |
| title | Fraser Syndrome-Oral Manifestations and a Dental Care Protocol |
| title_full | Fraser Syndrome-Oral Manifestations and a Dental Care Protocol |
| title_fullStr | Fraser Syndrome-Oral Manifestations and a Dental Care Protocol |
| title_full_unstemmed | Fraser Syndrome-Oral Manifestations and a Dental Care Protocol |
| title_short | Fraser Syndrome-Oral Manifestations and a Dental Care Protocol |
| title_sort | fraser syndrome oral manifestations and a dental care protocol |
| url | http://dx.doi.org/10.1155/2014/486108 |
| work_keys_str_mv | AT talitalopesdeoliveira frasersyndromeoralmanifestationsandadentalcareprotocol AT gisellerodriguesdesantanna frasersyndromeoralmanifestationsandadentalcareprotocol |