Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report

Modern pathogenetic therapy of idiopathic pulmonary arterial hypertension (IPAH), a severe life-threatening cardiovascular disease of unknown etiology, leads to a positive clinical effect due to reverse remodeling of the vessels of the microvasculature of the lungs. Highly effective drugs of specifi...

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Main Authors: S. A. Musashaykhova, Z. S. Valieva, A. K. Osokina, I. Z. Korobkova, V. V. Gramovich, N. M. Danilov, T. V. Martynyuk
Format: Article
Language:Russian
Published: InterMedservice 2022-12-01
Series:Евразийский Кардиологический Журнал
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Online Access:https://www.heartj.asia/jour/article/view/6353
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author S. A. Musashaykhova
Z. S. Valieva
A. K. Osokina
I. Z. Korobkova
V. V. Gramovich
N. M. Danilov
T. V. Martynyuk
author_facet S. A. Musashaykhova
Z. S. Valieva
A. K. Osokina
I. Z. Korobkova
V. V. Gramovich
N. M. Danilov
T. V. Martynyuk
author_sort S. A. Musashaykhova
collection DOAJ
description Modern pathogenetic therapy of idiopathic pulmonary arterial hypertension (IPAH), a severe life-threatening cardiovascular disease of unknown etiology, leads to a positive clinical effect due to reverse remodeling of the vessels of the microvasculature of the lungs. Highly effective drugs of specific therapy that act on the main targets of pathogenesis have now been introduced into clinical practice.The presented clinical case of a patient with diagnosed in 2014 IPAH with an initial functional class III according to the WHO classification demonstrates high long-term efficacy and safety of specific therapy based on the use of the soluble guanylate cyclase stimulator riociguat for 5 years after replacing previous therapy with sildenafil with further implementation of the strategy of sequential combination therapy due to the addition of ambrisentan and selexipag.
format Article
id doaj-art-c863d9d7f08d4d9791a8af2cbbb45589
institution Kabale University
issn 2225-1685
2305-0748
language Russian
publishDate 2022-12-01
publisher InterMedservice
record_format Article
series Евразийский Кардиологический Журнал
spelling doaj-art-c863d9d7f08d4d9791a8af2cbbb455892025-08-20T03:58:59ZrusInterMedserviceЕвразийский Кардиологический Журнал2225-16852305-07482022-12-0104748110.38109/2225-1685-2022-4-74-816284Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case reportS. A. Musashaykhova0Z. S. Valieva1A. K. Osokina2I. Z. Korobkova3V. V. Gramovich4N. M. Danilov5T. V. Martynyuk6A.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of СardiologyA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of СardiologyA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of СardiologyA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of Сardiology; Russian Medical Academy of Continuous Professional Education of the Ministry of Health of RussiaA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of СardiologyA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of СardiologyA.L. Myasnikov Research Institute of Clinical Cardiology, E.I. Chazov National Medical Research Centre of Сardiology; N.I. Pirogov Russian National Research Medical UniversityModern pathogenetic therapy of idiopathic pulmonary arterial hypertension (IPAH), a severe life-threatening cardiovascular disease of unknown etiology, leads to a positive clinical effect due to reverse remodeling of the vessels of the microvasculature of the lungs. Highly effective drugs of specific therapy that act on the main targets of pathogenesis have now been introduced into clinical practice.The presented clinical case of a patient with diagnosed in 2014 IPAH with an initial functional class III according to the WHO classification demonstrates high long-term efficacy and safety of specific therapy based on the use of the soluble guanylate cyclase stimulator riociguat for 5 years after replacing previous therapy with sildenafil with further implementation of the strategy of sequential combination therapy due to the addition of ambrisentan and selexipag.https://www.heartj.asia/jour/article/view/6353idiopathic pulmonary arterial hypertensionspecific therapysildenafilriociguatambrisentanselexipagcase report
spellingShingle S. A. Musashaykhova
Z. S. Valieva
A. K. Osokina
I. Z. Korobkova
V. V. Gramovich
N. M. Danilov
T. V. Martynyuk
Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
Евразийский Кардиологический Журнал
idiopathic pulmonary arterial hypertension
specific therapy
sildenafil
riociguat
ambrisentan
selexipag
case report
title Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
title_full Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
title_fullStr Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
title_full_unstemmed Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
title_short Possibilities of long-term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy: case report
title_sort possibilities of long term effective treatment of idiopathic pulmonary arterial hypertension by replacing sildenafil with riociguat and using sequential combination therapy case report
topic idiopathic pulmonary arterial hypertension
specific therapy
sildenafil
riociguat
ambrisentan
selexipag
case report
url https://www.heartj.asia/jour/article/view/6353
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