Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report

ABSTRACT Triangular lunulae, typically associated with Nail–Patella Syndrome, may also present in other syndromes, as seen in this case. Papillon–Lefèvre syndrome is a rare genodermatosis linked to significant morbidity. Consanguinity is a recognized high‐risk factor. Early diagnosis and treatment c...

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Main Authors: Zarak Khan Shiraz, Fahad Faizullah, Qaisar Ali Khan, Irfan Ullah, Mehran Khan, Bader Semakieh, Zain Ul Islam, Ravina Verma
Format: Article
Language:English
Published: Wiley 2025-04-01
Series:Clinical Case Reports
Subjects:
Online Access:https://doi.org/10.1002/ccr3.70339
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author Zarak Khan Shiraz
Fahad Faizullah
Qaisar Ali Khan
Irfan Ullah
Mehran Khan
Bader Semakieh
Zain Ul Islam
Ravina Verma
author_facet Zarak Khan Shiraz
Fahad Faizullah
Qaisar Ali Khan
Irfan Ullah
Mehran Khan
Bader Semakieh
Zain Ul Islam
Ravina Verma
author_sort Zarak Khan Shiraz
collection DOAJ
description ABSTRACT Triangular lunulae, typically associated with Nail–Patella Syndrome, may also present in other syndromes, as seen in this case. Papillon–Lefèvre syndrome is a rare genodermatosis linked to significant morbidity. Consanguinity is a recognized high‐risk factor. Early diagnosis and treatment can reduce morbidity in affected individuals, and raising societal awareness about consanguinity can help alleviate the disease's burden in populations where this practice is prevalent.
format Article
id doaj-art-c83b3ef0c90b4bd1bce678f6e8ed49a0
institution OA Journals
issn 2050-0904
language English
publishDate 2025-04-01
publisher Wiley
record_format Article
series Clinical Case Reports
spelling doaj-art-c83b3ef0c90b4bd1bce678f6e8ed49a02025-08-20T02:18:33ZengWileyClinical Case Reports2050-09042025-04-01134n/an/a10.1002/ccr3.70339Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case ReportZarak Khan Shiraz0Fahad Faizullah1Qaisar Ali Khan2Irfan Ullah3Mehran Khan4Bader Semakieh5Zain Ul Islam6Ravina Verma7Khyber Teaching Hospital MTI KTH Peshawar PakistanHayatabad Medical Complex Peshawar PakistanKhyber Teaching Hospital MTI KTH Peshawar PakistanKhyber Teaching Hospital MTI KTH Peshawar PakistanKhyber Teaching Hospital MTI KTH Peshawar PakistanArkansas College of Osteopathic Medicine Fort Smith Arkansas USAKMU Institute of Dental Sciences Kohat PakistanSt. George's University School of Medicine True Blue GrenadaABSTRACT Triangular lunulae, typically associated with Nail–Patella Syndrome, may also present in other syndromes, as seen in this case. Papillon–Lefèvre syndrome is a rare genodermatosis linked to significant morbidity. Consanguinity is a recognized high‐risk factor. Early diagnosis and treatment can reduce morbidity in affected individuals, and raising societal awareness about consanguinity can help alleviate the disease's burden in populations where this practice is prevalent.https://doi.org/10.1002/ccr3.70339case reportgenetic disordersNail–Patella syndromePapillon–Lefèvre syndrometriangular lunulae
spellingShingle Zarak Khan Shiraz
Fahad Faizullah
Qaisar Ali Khan
Irfan Ullah
Mehran Khan
Bader Semakieh
Zain Ul Islam
Ravina Verma
Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
Clinical Case Reports
case report
genetic disorders
Nail–Patella syndrome
Papillon–Lefèvre syndrome
triangular lunulae
title Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
title_full Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
title_fullStr Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
title_full_unstemmed Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
title_short Triangular Lunulae in Papillon–Lefèvre Syndrome: A Case Report
title_sort triangular lunulae in papillon lefevre syndrome a case report
topic case report
genetic disorders
Nail–Patella syndrome
Papillon–Lefèvre syndrome
triangular lunulae
url https://doi.org/10.1002/ccr3.70339
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AT irfanullah triangularlunulaeinpapillonlefevresyndromeacasereport
AT mehrankhan triangularlunulaeinpapillonlefevresyndromeacasereport
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