Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old f...
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| Format: | Article |
| Language: | English |
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Wiley
2019-01-01
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| Series: | Case Reports in Pathology |
| Online Access: | http://dx.doi.org/10.1155/2019/9576487 |
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| author | Yara A. Alnashwan Khaled A. H. Ali Samir S. Amr |
| author_facet | Yara A. Alnashwan Khaled A. H. Ali Samir S. Amr |
| author_sort | Yara A. Alnashwan |
| collection | DOAJ |
| description | Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented. |
| format | Article |
| id | doaj-art-c81e1ca3d53a480999eae99cd2f0c60e |
| institution | OA Journals |
| issn | 2090-6781 2090-679X |
| language | English |
| publishDate | 2019-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pathology |
| spelling | doaj-art-c81e1ca3d53a480999eae99cd2f0c60e2025-08-20T02:20:06ZengWileyCase Reports in Pathology2090-67812090-679X2019-01-01201910.1155/2019/95764879576487Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged SurvivalYara A. Alnashwan0Khaled A. H. Ali1Samir S. Amr2Department of Pathology, Faculty of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi ArabiaDepartment of Pathology, Almana General Hospital, Dammam, Saudi ArabiaDepartment of Pathology and Laboratory Medicine, King Fahad Specialist Hospital, Dammam, Saudi ArabiaMalignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented.http://dx.doi.org/10.1155/2019/9576487 |
| spellingShingle | Yara A. Alnashwan Khaled A. H. Ali Samir S. Amr Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival Case Reports in Pathology |
| title | Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival |
| title_full | Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival |
| title_fullStr | Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival |
| title_full_unstemmed | Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival |
| title_short | Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival |
| title_sort | metastasizing malignant granular cell tumor abrikossoff tumor of the anterior abdominal wall with prolonged survival |
| url | http://dx.doi.org/10.1155/2019/9576487 |
| work_keys_str_mv | AT yaraaalnashwan metastasizingmalignantgranularcelltumorabrikossofftumoroftheanteriorabdominalwallwithprolongedsurvival AT khaledahali metastasizingmalignantgranularcelltumorabrikossofftumoroftheanteriorabdominalwallwithprolongedsurvival AT samirsamr metastasizingmalignantgranularcelltumorabrikossofftumoroftheanteriorabdominalwallwithprolongedsurvival |