Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classica...
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Language: | English |
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Wiley
2017-01-01
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Series: | Case Reports in Pediatrics |
Online Access: | http://dx.doi.org/10.1155/2017/5693501 |
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author | Kenan Barut Sezgin Sahin Amra Adrovic Velat Sen Ozgur Kasapcopur |
author_facet | Kenan Barut Sezgin Sahin Amra Adrovic Velat Sen Ozgur Kasapcopur |
author_sort | Kenan Barut |
collection | DOAJ |
description | Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Although the majority of patients of pulmonary hemosiderosis are considered idiopathic, secondary hemosiderosis associated with known diseases could be seen. In this case report, we aimed to present gradually increased pulmonary manifestations due to pulmonary hemosiderosis with recurrent macrophage activation syndrome attacks in a child with systemic juvenile idiopathic arthritis. |
format | Article |
id | doaj-art-c7c89e8964c34a52ae5443c5c78f23e2 |
institution | Kabale University |
issn | 2090-6803 2090-6811 |
language | English |
publishDate | 2017-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Pediatrics |
spelling | doaj-art-c7c89e8964c34a52ae5443c5c78f23e22025-02-03T05:46:26ZengWileyCase Reports in Pediatrics2090-68032090-68112017-01-01201710.1155/2017/56935015693501Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic ArthritisKenan Barut0Sezgin Sahin1Amra Adrovic2Velat Sen3Ozgur Kasapcopur4Department of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Chest Disease, Medical Faculty, Dicle University, Diyarbakir, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyMacrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Although the majority of patients of pulmonary hemosiderosis are considered idiopathic, secondary hemosiderosis associated with known diseases could be seen. In this case report, we aimed to present gradually increased pulmonary manifestations due to pulmonary hemosiderosis with recurrent macrophage activation syndrome attacks in a child with systemic juvenile idiopathic arthritis.http://dx.doi.org/10.1155/2017/5693501 |
spellingShingle | Kenan Barut Sezgin Sahin Amra Adrovic Velat Sen Ozgur Kasapcopur Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis Case Reports in Pediatrics |
title | Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis |
title_full | Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis |
title_fullStr | Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis |
title_full_unstemmed | Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis |
title_short | Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis |
title_sort | idiopathic pulmonary hemosiderosis in a child with recurrent macrophage activation syndrome secondary to systemic juvenile idiopathic arthritis |
url | http://dx.doi.org/10.1155/2017/5693501 |
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