First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice
Bickerstaff Brainstem Encephalitis (BBE) is a rare immunologic condition characterized by CNS inflammation, presenting with ataxia, external ophthalmoplegia, altered consciousness, and quadriplegia. A 25-year-old male with no significant medical history exhibited symptoms of blurred vision, diplopia...
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| Language: | English |
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Elsevier
2025-02-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043324012731 |
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| author | Ahmad Almohamed Ayham Qatza Haifa Alsamman Suaad Hamsho Mohammad Atia Rahaf tamer Almaya Mhd Ali Waddah Kazkz |
| author_facet | Ahmad Almohamed Ayham Qatza Haifa Alsamman Suaad Hamsho Mohammad Atia Rahaf tamer Almaya Mhd Ali Waddah Kazkz |
| author_sort | Ahmad Almohamed |
| collection | DOAJ |
| description | Bickerstaff Brainstem Encephalitis (BBE) is a rare immunologic condition characterized by CNS inflammation, presenting with ataxia, external ophthalmoplegia, altered consciousness, and quadriplegia. A 25-year-old male with no significant medical history exhibited symptoms of blurred vision, diplopia, facial numbness, and imbalance following a respiratory infection. Brain MRI revealed hyperintense lesions in the cerebral peduncle and pons on T2-weighted/FLAIR sequences but not on T1-weighted sequences, indicative of demyelination. Lumbar puncture showed clear cerebrospinal fluid with lymphocytic pleocytosis (80 cells/μl, 95% lymphocytes) and normal protein levels. The patient was treated with intravenous methylprednisolone (1000 mg/day for five days), resulting in recovery and normal follow-up MRI findings. Early diagnosis and treatment are crucial to minimize complications and improve outcomes. Additionally, airway management is essential for patients with impaired respiratory function, and long-term rehabilitation may be necessary for those recovering from encephalitis. |
| format | Article |
| id | doaj-art-c7b70dd806c24390ab10cff9a5abfaa6 |
| institution | DOAJ |
| issn | 1930-0433 |
| language | English |
| publishDate | 2025-02-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj-art-c7b70dd806c24390ab10cff9a5abfaa62025-08-20T02:49:41ZengElsevierRadiology Case Reports1930-04332025-02-012021211121410.1016/j.radcr.2024.11.006First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practiceAhmad Almohamed0Ayham Qatza1Haifa Alsamman2Suaad Hamsho3Mohammad Atia4Rahaf tamer5Almaya Mhd Ali6Waddah Kazkz7Faculty of Medicine, Hama University, Hama, SyriaFaculty of Medicine, Hama University, Hama, Syria; Corresponding author.Neurology Department, Hama National Hospital, Hama, SyriaRheumatology Department, Faculty of Medicine, Damascus University, Damascus, SyriaFaculty of Medicine, Al-sham Private University, Damascus, SyriaFaculty of Medicine, Hama University, Hama, SyriaFaculty of Pharmacy, Aleppo University, Aleppo, SyriaNeurology Department, Hama National Hospital, Hama, SyriaBickerstaff Brainstem Encephalitis (BBE) is a rare immunologic condition characterized by CNS inflammation, presenting with ataxia, external ophthalmoplegia, altered consciousness, and quadriplegia. A 25-year-old male with no significant medical history exhibited symptoms of blurred vision, diplopia, facial numbness, and imbalance following a respiratory infection. Brain MRI revealed hyperintense lesions in the cerebral peduncle and pons on T2-weighted/FLAIR sequences but not on T1-weighted sequences, indicative of demyelination. Lumbar puncture showed clear cerebrospinal fluid with lymphocytic pleocytosis (80 cells/μl, 95% lymphocytes) and normal protein levels. The patient was treated with intravenous methylprednisolone (1000 mg/day for five days), resulting in recovery and normal follow-up MRI findings. Early diagnosis and treatment are crucial to minimize complications and improve outcomes. Additionally, airway management is essential for patients with impaired respiratory function, and long-term rehabilitation may be necessary for those recovering from encephalitis.http://www.sciencedirect.com/science/article/pii/S1930043324012731Bickerstaff brainstem encephalitisFunctional neurologic disorderMethylprednisoloneCase report |
| spellingShingle | Ahmad Almohamed Ayham Qatza Haifa Alsamman Suaad Hamsho Mohammad Atia Rahaf tamer Almaya Mhd Ali Waddah Kazkz First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice Radiology Case Reports Bickerstaff brainstem encephalitis Functional neurologic disorder Methylprednisolone Case report |
| title | First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice |
| title_full | First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice |
| title_fullStr | First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice |
| title_full_unstemmed | First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice |
| title_short | First case report on Bickerstaff brainstem encephalitis in a young adult from Syria: Bridging clinical knowledge and practice |
| title_sort | first case report on bickerstaff brainstem encephalitis in a young adult from syria bridging clinical knowledge and practice |
| topic | Bickerstaff brainstem encephalitis Functional neurologic disorder Methylprednisolone Case report |
| url | http://www.sciencedirect.com/science/article/pii/S1930043324012731 |
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