Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications

Congenital long QT syndrome (LQTS) is a potentially life-threatening hereditary arrhythmia characterized by a prolonged QT interval on electrocardiogram (ECG) due to delayed ventricular repolarization. This condition predisposes individuals to severe arrhythmic events, including ventricular tachycar...

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Main Authors: Qing Li, Yi-Fei Wang, Bin Wang, Ting-Ting Lv, Ping Zhang
Format: Article
Language:English
Published: IMR Press 2025-04-01
Series:Reviews in Cardiovascular Medicine
Subjects:
Online Access:https://www.imrpress.com/journal/RCM/26/4/10.31083/RCM28251
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author Qing Li
Yi-Fei Wang
Bin Wang
Ting-Ting Lv
Ping Zhang
author_facet Qing Li
Yi-Fei Wang
Bin Wang
Ting-Ting Lv
Ping Zhang
author_sort Qing Li
collection DOAJ
description Congenital long QT syndrome (LQTS) is a potentially life-threatening hereditary arrhythmia characterized by a prolonged QT interval on electrocardiogram (ECG) due to delayed ventricular repolarization. This condition predisposes individuals to severe arrhythmic events, including ventricular tachycardia and sudden cardiac death. Traditional approaches to LQTS research and treatment are limited by an incomplete understanding of its gene-specific pathophysiology, variable clinical presentation, and the challenges associated with developing effective, personalized therapies. Recent advances in human induced pluripotent stem cell (iPSC) technology have opened new avenues for elucidating LQTS mechanisms and testing therapeutic strategies. By generating cardiomyocytes from patient-specific iPSCs (iPSC-CMs), it is now possible to recreate the patient’s genetic context and study LQTS in a controlled environment. This comprehensive review describes how iPSC technology deepens our understanding of LQTS and accelerates the development of tailored treatments, as well as ongoing challenges such as incomplete cell maturation and cellular heterogeneity.
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series Reviews in Cardiovascular Medicine
spelling doaj-art-c69e751714504685aafc2bd20afbd04a2025-08-20T02:28:55ZengIMR PressReviews in Cardiovascular Medicine1530-65502025-04-012642825110.31083/RCM28251S1530-6550(25)01741-7Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical ApplicationsQing Li0Yi-Fei Wang1Bin Wang2Ting-Ting Lv3Ping Zhang4School of Clinical Medicine, Tsinghua University, 100084 Beijing, ChinaSchool of Clinical Medicine, Tsinghua University, 100084 Beijing, ChinaSchool of Clinical Medicine, Tsinghua University, 100084 Beijing, ChinaDepartment of Cardiology, Beijing Tsinghua Changgung Hospital, School of Clinical Medicine, Tsinghua University, 102218 Beijing, ChinaSchool of Clinical Medicine, Tsinghua University, 100084 Beijing, ChinaCongenital long QT syndrome (LQTS) is a potentially life-threatening hereditary arrhythmia characterized by a prolonged QT interval on electrocardiogram (ECG) due to delayed ventricular repolarization. This condition predisposes individuals to severe arrhythmic events, including ventricular tachycardia and sudden cardiac death. Traditional approaches to LQTS research and treatment are limited by an incomplete understanding of its gene-specific pathophysiology, variable clinical presentation, and the challenges associated with developing effective, personalized therapies. Recent advances in human induced pluripotent stem cell (iPSC) technology have opened new avenues for elucidating LQTS mechanisms and testing therapeutic strategies. By generating cardiomyocytes from patient-specific iPSCs (iPSC-CMs), it is now possible to recreate the patient’s genetic context and study LQTS in a controlled environment. This comprehensive review describes how iPSC technology deepens our understanding of LQTS and accelerates the development of tailored treatments, as well as ongoing challenges such as incomplete cell maturation and cellular heterogeneity.https://www.imrpress.com/journal/RCM/26/4/10.31083/RCM28251congenital long qt syndromeinduced pluripotent stem cellsprecision medicine
spellingShingle Qing Li
Yi-Fei Wang
Bin Wang
Ting-Ting Lv
Ping Zhang
Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
Reviews in Cardiovascular Medicine
congenital long qt syndrome
induced pluripotent stem cells
precision medicine
title Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
title_full Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
title_fullStr Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
title_full_unstemmed Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
title_short Induced Pluripotent Stem Cells in Congenital Long QT Syndrome: Research Progress and Clinical Applications
title_sort induced pluripotent stem cells in congenital long qt syndrome research progress and clinical applications
topic congenital long qt syndrome
induced pluripotent stem cells
precision medicine
url https://www.imrpress.com/journal/RCM/26/4/10.31083/RCM28251
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