Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler

We report the use of diffusion-weighted magnetic resonance imaging to diagnose and manage a rare case of a symptomatic thoracic intramedullary congenital epidermoid cyst with associated dermal sinus in a girl. Congenital intramedullary epidermoid cysts with associated dermal sinuses are very rare oc...

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Main Authors: Michael G. Fazio, Alyson M. Kil, Veronica J. Rooks, Timothy J. Biega
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Case Reports in Radiology
Online Access:http://dx.doi.org/10.1155/2013/878713
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author Michael G. Fazio
Alyson M. Kil
Veronica J. Rooks
Timothy J. Biega
author_facet Michael G. Fazio
Alyson M. Kil
Veronica J. Rooks
Timothy J. Biega
author_sort Michael G. Fazio
collection DOAJ
description We report the use of diffusion-weighted magnetic resonance imaging to diagnose and manage a rare case of a symptomatic thoracic intramedullary congenital epidermoid cyst with associated dermal sinus in a girl. Congenital intramedullary epidermoid cysts with associated dermal sinuses are very rare occurrences and seldom present symptomatically in very young children. We present a case of a 32-month old with a draining dimpled skin lesion. Magnetic resonance images demonstrated an intramedullary epidermoid with a dorsal dermal sinus tract opening to the skin surface which was confirmed surgically. The patient was treated with debulking to prevent recurrent infection and progression of neurological symptoms. This case demonstrates the use of diffuse-weighted MRI to assist in the diagnosis and surgical management of an atypical presentation of a rare developmental abnormality, which is not well documented in the pediatric radiological literature. Failure to diagnosis may have significant neurological permanent debilitating consequences.
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institution Kabale University
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publishDate 2013-01-01
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series Case Reports in Radiology
spelling doaj-art-c63c94b7b1f54d8ea68f1c2315d66ca22025-02-03T05:46:45ZengWileyCase Reports in Radiology2090-68622090-68702013-01-01201310.1155/2013/878713878713Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a ToddlerMichael G. Fazio0Alyson M. Kil1Veronica J. Rooks2Timothy J. Biega3Department of Radiology, MCHK-DR, Tripler Army Medical Center, 1 Jarrett White Road, Honolulu, HI 96859, USAKeck School of Medicine, University of Southern California, Los Angeles, CA, USADepartment of Radiology, MCHK-DR, Tripler Army Medical Center, 1 Jarrett White Road, Honolulu, HI 96859, USADepartment of Radiology, MCHK-DR, Tripler Army Medical Center, 1 Jarrett White Road, Honolulu, HI 96859, USAWe report the use of diffusion-weighted magnetic resonance imaging to diagnose and manage a rare case of a symptomatic thoracic intramedullary congenital epidermoid cyst with associated dermal sinus in a girl. Congenital intramedullary epidermoid cysts with associated dermal sinuses are very rare occurrences and seldom present symptomatically in very young children. We present a case of a 32-month old with a draining dimpled skin lesion. Magnetic resonance images demonstrated an intramedullary epidermoid with a dorsal dermal sinus tract opening to the skin surface which was confirmed surgically. The patient was treated with debulking to prevent recurrent infection and progression of neurological symptoms. This case demonstrates the use of diffuse-weighted MRI to assist in the diagnosis and surgical management of an atypical presentation of a rare developmental abnormality, which is not well documented in the pediatric radiological literature. Failure to diagnosis may have significant neurological permanent debilitating consequences.http://dx.doi.org/10.1155/2013/878713
spellingShingle Michael G. Fazio
Alyson M. Kil
Veronica J. Rooks
Timothy J. Biega
Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
Case Reports in Radiology
title Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
title_full Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
title_fullStr Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
title_full_unstemmed Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
title_short Diffusion-Weighted Magnetic Resonance Imaging of an Intramedullary Epidermoid Cyst with Dorsal Dermal Sinus Tract in a Toddler
title_sort diffusion weighted magnetic resonance imaging of an intramedullary epidermoid cyst with dorsal dermal sinus tract in a toddler
url http://dx.doi.org/10.1155/2013/878713
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