Primary Intracranial Adenoid Cystic Carcinoma: A Case Report

Adenoid cystic carcinoma (ACC) is a rare slow-growing but aggressive malignant tumor arising from the epithelial cells of mucous-secreting glands. Primary intracranial ACC is one of the rarest entity. We report a case of a 61 years old male presenting with difficulty in swallowing, slurring of spee...

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Main Authors: Pralisha Maharjan, Gopi Aryal, Reena Rana
Format: Article
Language:English
Published: Nepal Medical Association 2025-01-01
Series:Journal of Nepal Medical Association
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Online Access:https://www.jnma.com.np/jnma/index.php/jnma/article/view/8890
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author Pralisha Maharjan
Gopi Aryal
Reena Rana
author_facet Pralisha Maharjan
Gopi Aryal
Reena Rana
author_sort Pralisha Maharjan
collection DOAJ
description Adenoid cystic carcinoma (ACC) is a rare slow-growing but aggressive malignant tumor arising from the epithelial cells of mucous-secreting glands. Primary intracranial ACC is one of the rarest entity. We report a case of a 61 years old male presenting with difficulty in swallowing, slurring of speech, generalized body weakness. Patient had residual right cerebellopontine angle (CPA) mass causing midline shift and fourth ventricular obstruction on MRI. Patient underwent right retrosigmoid craniotomy with excision of CPA mass. Histopathological examination confirmed the case as primary intracranial ACC.
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institution Kabale University
issn 0028-2715
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series Journal of Nepal Medical Association
spelling doaj-art-c5e5e725c4414cce9725a8cdd6bea4462025-02-04T09:26:16ZengNepal Medical AssociationJournal of Nepal Medical Association0028-27151815-672X2025-01-016328210.31729/jnma.8890Primary Intracranial Adenoid Cystic Carcinoma: A Case ReportPralisha Maharjan0Gopi Aryal1Reena Rana2Nepal Mediciti Hospital, Sainbu, Lalitpur, NepalNepal Mediciti Hospital, Sainbu, Lalitpur, NepalNepal Mediciti Hospital, Sainbu, Lalitpur, Nepal Adenoid cystic carcinoma (ACC) is a rare slow-growing but aggressive malignant tumor arising from the epithelial cells of mucous-secreting glands. Primary intracranial ACC is one of the rarest entity. We report a case of a 61 years old male presenting with difficulty in swallowing, slurring of speech, generalized body weakness. Patient had residual right cerebellopontine angle (CPA) mass causing midline shift and fourth ventricular obstruction on MRI. Patient underwent right retrosigmoid craniotomy with excision of CPA mass. Histopathological examination confirmed the case as primary intracranial ACC. https://www.jnma.com.np/jnma/index.php/jnma/article/view/8890adenoid cystic carcinomacraniotomyintracranial
spellingShingle Pralisha Maharjan
Gopi Aryal
Reena Rana
Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
Journal of Nepal Medical Association
adenoid cystic carcinoma
craniotomy
intracranial
title Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
title_full Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
title_fullStr Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
title_full_unstemmed Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
title_short Primary Intracranial Adenoid Cystic Carcinoma: A Case Report
title_sort primary intracranial adenoid cystic carcinoma a case report
topic adenoid cystic carcinoma
craniotomy
intracranial
url https://www.jnma.com.np/jnma/index.php/jnma/article/view/8890
work_keys_str_mv AT pralishamaharjan primaryintracranialadenoidcysticcarcinomaacasereport
AT gopiaryal primaryintracranialadenoidcysticcarcinomaacasereport
AT reenarana primaryintracranialadenoidcysticcarcinomaacasereport