Pernicious Anemia in an Adult with Trisomy 21

Pernicious anemia is an autoimmune disease caused by the malabsorption of vitamin B12. It usually appears in the elderly. People with trisomy 21 are susceptible to autoimmune diseases. This susceptibility is thought to be due to altered expression of the AIRE gene, which is located in the 21q22.3 re...

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Main Authors: Kentaro Kamada, Osamu Kawano, Satoshi Yakuwa, Kentaro Wakasa, Kimiaki Uetake
Format: Article
Language:English
Published: Wiley 2023-01-01
Series:Case Reports in Immunology
Online Access:http://dx.doi.org/10.1155/2023/2747756
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author Kentaro Kamada
Osamu Kawano
Satoshi Yakuwa
Kentaro Wakasa
Kimiaki Uetake
author_facet Kentaro Kamada
Osamu Kawano
Satoshi Yakuwa
Kentaro Wakasa
Kimiaki Uetake
author_sort Kentaro Kamada
collection DOAJ
description Pernicious anemia is an autoimmune disease caused by the malabsorption of vitamin B12. It usually appears in the elderly. People with trisomy 21 are susceptible to autoimmune diseases. This susceptibility is thought to be due to altered expression of the AIRE gene, which is located in the 21q22.3 region. Although pernicious anemia is not common in people with trisomy 21, AIRE is pointed out as a susceptibility gene of pernicious anemia in a genome-wide association study. Here, we report a man with trisomy 21, who suffered from the pernicious anemia. When he was in his 30 s, he visited our hospital because of diarrhea and poor oral intake. He showed thrombocytopenic purpura-like features, and was diagnosed as pernicious anemia. After supplementation of vitamin B12, he recovered from the illness. The reason for his early onset may be because of trisomy 21. Altered expression of AIRE might trigger the disease.
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spelling doaj-art-c5d23439f8c44c9bb0a83b5ebcd336e72025-08-20T03:24:47ZengWileyCase Reports in Immunology2090-66172023-01-01202310.1155/2023/2747756Pernicious Anemia in an Adult with Trisomy 21Kentaro Kamada0Osamu Kawano1Satoshi Yakuwa2Kentaro Wakasa3Kimiaki Uetake4Department of PediatricsDepartment of PediatricsDepartment of PediatricsDepartment of HematologyDepartment of PediatricsPernicious anemia is an autoimmune disease caused by the malabsorption of vitamin B12. It usually appears in the elderly. People with trisomy 21 are susceptible to autoimmune diseases. This susceptibility is thought to be due to altered expression of the AIRE gene, which is located in the 21q22.3 region. Although pernicious anemia is not common in people with trisomy 21, AIRE is pointed out as a susceptibility gene of pernicious anemia in a genome-wide association study. Here, we report a man with trisomy 21, who suffered from the pernicious anemia. When he was in his 30 s, he visited our hospital because of diarrhea and poor oral intake. He showed thrombocytopenic purpura-like features, and was diagnosed as pernicious anemia. After supplementation of vitamin B12, he recovered from the illness. The reason for his early onset may be because of trisomy 21. Altered expression of AIRE might trigger the disease.http://dx.doi.org/10.1155/2023/2747756
spellingShingle Kentaro Kamada
Osamu Kawano
Satoshi Yakuwa
Kentaro Wakasa
Kimiaki Uetake
Pernicious Anemia in an Adult with Trisomy 21
Case Reports in Immunology
title Pernicious Anemia in an Adult with Trisomy 21
title_full Pernicious Anemia in an Adult with Trisomy 21
title_fullStr Pernicious Anemia in an Adult with Trisomy 21
title_full_unstemmed Pernicious Anemia in an Adult with Trisomy 21
title_short Pernicious Anemia in an Adult with Trisomy 21
title_sort pernicious anemia in an adult with trisomy 21
url http://dx.doi.org/10.1155/2023/2747756
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AT osamukawano perniciousanemiainanadultwithtrisomy21
AT satoshiyakuwa perniciousanemiainanadultwithtrisomy21
AT kentarowakasa perniciousanemiainanadultwithtrisomy21
AT kimiakiuetake perniciousanemiainanadultwithtrisomy21