Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible
Focal nodular hyperplasia (FNH)-like lesions of the liver are rare in the pediatric population and are seldom reported as congenital lesions. The differential diagnosis between these lesions and pure-fetal hepatoblastoma (HBL) is challenging. We present a case of a congenital FNH-like hepatic lesion...
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| Format: | Article |
| Language: | English |
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BMJ Publishing Group
2025-04-01
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| Series: | World Journal of Pediatric Surgery |
| Online Access: | https://wjps.bmj.com/content/8/2/e000980.full |
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| author | Rita Alaggio Andrea Zanini Michela Casanova Maurizio Cheli Alessandra Gatto Chiara Natale Alessandra Preziosi Francesco Macchini |
| author_facet | Rita Alaggio Andrea Zanini Michela Casanova Maurizio Cheli Alessandra Gatto Chiara Natale Alessandra Preziosi Francesco Macchini |
| author_sort | Rita Alaggio |
| collection | DOAJ |
| description | Focal nodular hyperplasia (FNH)-like lesions of the liver are rare in the pediatric population and are seldom reported as congenital lesions. The differential diagnosis between these lesions and pure-fetal hepatoblastoma (HBL) is challenging. We present a case of a congenital FNH-like hepatic lesion, managed with a right hepatectomy due to suspected fetal HBL. Additionally, a review of all published cases of congenital FNH-like lesions of the liver was carried out.MRI |
| format | Article |
| id | doaj-art-c57507a11d2347ed8877a91efdb25421 |
| institution | OA Journals |
| issn | 2516-5410 |
| language | English |
| publishDate | 2025-04-01 |
| publisher | BMJ Publishing Group |
| record_format | Article |
| series | World Journal of Pediatric Surgery |
| spelling | doaj-art-c57507a11d2347ed8877a91efdb254212025-08-20T02:12:19ZengBMJ Publishing GroupWorld Journal of Pediatric Surgery2516-54102025-04-018210.1136/wjps-2024-000980Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausibleRita Alaggio0Andrea Zanini1Michela Casanova2Maurizio Cheli3Alessandra Gatto4Chiara Natale5Alessandra Preziosi6Francesco Macchini71Pathological Anatomy, DIMED—Department of Medicine, University of Padova, Padova, Italy1Divisione di Pneumologia e Laboratorio di Citoimmunopatologia dell`Apparato Cardio Respiratorio, Fondazione Salvatore Maugeri, IRCCS, Veruno (NO) e Tradate, Pavia, Italy1 Pediatric Oncology Unit, Fondazione IRCCS Istituto Nazionale dei Tumori, Milano, ItalyPediatric Surgery, ASST Papa Giovanni XXIII, Bergamo, ItalyDepartment of Pediatric Surgery, ASST Grande Ospedale Metropolitano Niguarda, Milan, ItalyDepartment of Pediatric Surgery, ASST Grande Ospedale Metropolitano Niguarda, Milan, ItalyDepartment of Pediatric Surgery, ASST Grande Ospedale Metropolitano Niguarda, Milan, ItalyDepartment of Pediatric Surgery, ASST Grande Ospedale Metropolitano Niguarda, Milan, ItalyFocal nodular hyperplasia (FNH)-like lesions of the liver are rare in the pediatric population and are seldom reported as congenital lesions. The differential diagnosis between these lesions and pure-fetal hepatoblastoma (HBL) is challenging. We present a case of a congenital FNH-like hepatic lesion, managed with a right hepatectomy due to suspected fetal HBL. Additionally, a review of all published cases of congenital FNH-like lesions of the liver was carried out.MRIhttps://wjps.bmj.com/content/8/2/e000980.full |
| spellingShingle | Rita Alaggio Andrea Zanini Michela Casanova Maurizio Cheli Alessandra Gatto Chiara Natale Alessandra Preziosi Francesco Macchini Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible World Journal of Pediatric Surgery |
| title | Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible |
| title_full | Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible |
| title_fullStr | Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible |
| title_full_unstemmed | Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible |
| title_short | Congenital focal nodular hyperplasia-like lesion mimicking hepatoblastoma: anecdotal but plausible |
| title_sort | congenital focal nodular hyperplasia like lesion mimicking hepatoblastoma anecdotal but plausible |
| url | https://wjps.bmj.com/content/8/2/e000980.full |
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