Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant

Scimitar syndrome is a rare congenital anomaly characterized by partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava (IVC) creating a tubular opacity paralleling the right cardiac border on chest radiography which resembles a curved Turkish sword or scimitar. Assoc...

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Main Authors: Allison Lastinger, Malek El Yaman, Robert Gustafson, Panitan Yossuck
Format: Article
Language:English
Published: Elsevier 2016-06-01
Series:Pediatrics and Neonatology
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S187595721300154X
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author Allison Lastinger
Malek El Yaman
Robert Gustafson
Panitan Yossuck
author_facet Allison Lastinger
Malek El Yaman
Robert Gustafson
Panitan Yossuck
author_sort Allison Lastinger
collection DOAJ
description Scimitar syndrome is a rare congenital anomaly characterized by partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava (IVC) creating a tubular opacity paralleling the right cardiac border on chest radiography which resembles a curved Turkish sword or scimitar. Associated pulmonary and vascular anomalies have been reported in cases of Scimitar syndrome, most commonly hypoplasia of right lung, dextroposition of the heart, hypoplasia of the right pulmonary artery, and aberrant arterial supply from the descending aorta to the affected lobe of the right lung. To the best of our knowledge, this is the first case of Scimitar syndrome with an H-type tracheoesophageal fistula that has ever been reported.
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series Pediatrics and Neonatology
spelling doaj-art-c3f02565786843ca98b2bb44bceef8a02025-08-20T02:25:47ZengElsevierPediatrics and Neonatology1875-95722016-06-0157323623910.1016/j.pedneo.2013.06.010Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn InfantAllison Lastinger0Malek El Yaman1Robert Gustafson2Panitan Yossuck3Department of Pediatrics-Internal Medicine, WVU School of Medicine, Morgantown, WV 26505, USADepartment of Pediatrics, WVU School of Medicine, Morgantown, WV 26505, USADepartment of Pediatric Cardiovascular and Thoracic Surgery, WVU School of Medicine, Morgantown, WV 26505, USADepartment of Pediatrics-Internal Medicine, WVU School of Medicine, Morgantown, WV 26505, USAScimitar syndrome is a rare congenital anomaly characterized by partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava (IVC) creating a tubular opacity paralleling the right cardiac border on chest radiography which resembles a curved Turkish sword or scimitar. Associated pulmonary and vascular anomalies have been reported in cases of Scimitar syndrome, most commonly hypoplasia of right lung, dextroposition of the heart, hypoplasia of the right pulmonary artery, and aberrant arterial supply from the descending aorta to the affected lobe of the right lung. To the best of our knowledge, this is the first case of Scimitar syndrome with an H-type tracheoesophageal fistula that has ever been reported.http://www.sciencedirect.com/science/article/pii/S187595721300154XH-type trachea-esophageal fistulaPAPVRpartial anomalous pulmonary venous returnScimitar syndrome
spellingShingle Allison Lastinger
Malek El Yaman
Robert Gustafson
Panitan Yossuck
Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
Pediatrics and Neonatology
H-type trachea-esophageal fistula
PAPVR
partial anomalous pulmonary venous return
Scimitar syndrome
title Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
title_full Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
title_fullStr Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
title_full_unstemmed Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
title_short Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant
title_sort scimitar syndrome and h type tracheo esophageal fistula in a newborn infant
topic H-type trachea-esophageal fistula
PAPVR
partial anomalous pulmonary venous return
Scimitar syndrome
url http://www.sciencedirect.com/science/article/pii/S187595721300154X
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