Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report

Pulmonary Langerhans cell histiocytosis (PLCH) is a disease characterized by the infiltration of Langerhans cells into the lungs, affecting young adults with a history of smoking. Spontaneous pneumothorax is a recognized complication of PLCH. We present a case of a 19-year-old male nonsmoker who pre...

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Main Authors: Swaroop Kumar Mudda, Dhruv Bansal, Priya Bansal, Ritika Sud, Motilal Negi
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-12-01
Series:The Journal of Association of Chest Physicians
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Online Access:https://journals.lww.com/10.4103/jacp.jacp_32_24
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author Swaroop Kumar Mudda
Dhruv Bansal
Priya Bansal
Ritika Sud
Motilal Negi
author_facet Swaroop Kumar Mudda
Dhruv Bansal
Priya Bansal
Ritika Sud
Motilal Negi
author_sort Swaroop Kumar Mudda
collection DOAJ
description Pulmonary Langerhans cell histiocytosis (PLCH) is a disease characterized by the infiltration of Langerhans cells into the lungs, affecting young adults with a history of smoking. Spontaneous pneumothorax is a recognized complication of PLCH. We present a case of a 19-year-old male nonsmoker who presented with recurrent pneumothorax, two episodes within a period of one month. Diagnostic workup, including imaging studies and lung biopsy, confirmed the diagnosis of PLCH. This case highlights the importance of considering PLCH in cases of recurrent pneumothorax, even with no history of smoking, and emphasizes the importance of timely diagnosis and management to prevent long-term pulmonary complications.
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institution Kabale University
issn 2320-8775
language English
publishDate 2024-12-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series The Journal of Association of Chest Physicians
spelling doaj-art-c2a670f91cc648aabdea57c5bf3f997a2025-01-04T10:31:42ZengWolters Kluwer Medknow PublicationsThe Journal of Association of Chest Physicians2320-87752024-12-0112419319610.4103/jacp.jacp_32_24Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case reportSwaroop Kumar MuddaDhruv BansalPriya BansalRitika SudMotilal NegiPulmonary Langerhans cell histiocytosis (PLCH) is a disease characterized by the infiltration of Langerhans cells into the lungs, affecting young adults with a history of smoking. Spontaneous pneumothorax is a recognized complication of PLCH. We present a case of a 19-year-old male nonsmoker who presented with recurrent pneumothorax, two episodes within a period of one month. Diagnostic workup, including imaging studies and lung biopsy, confirmed the diagnosis of PLCH. This case highlights the importance of considering PLCH in cases of recurrent pneumothorax, even with no history of smoking, and emphasizes the importance of timely diagnosis and management to prevent long-term pulmonary complications.https://journals.lww.com/10.4103/jacp.jacp_32_24pulmonary langerhans cell histiocytosispneumothoraxceliac diseaseeosinophilic granuloma of the lungcystic interstitial lung disease
spellingShingle Swaroop Kumar Mudda
Dhruv Bansal
Priya Bansal
Ritika Sud
Motilal Negi
Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
The Journal of Association of Chest Physicians
pulmonary langerhans cell histiocytosis
pneumothorax
celiac disease
eosinophilic granuloma of the lung
cystic interstitial lung disease
title Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
title_full Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
title_fullStr Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
title_full_unstemmed Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
title_short Pulmonary Langerhans cell histiocytosis—an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease: a case report
title_sort pulmonary langerhans cell histiocytosis an unlikely diagnosis in a nonsmoker with clubbing and concomitant celiac disease a case report
topic pulmonary langerhans cell histiocytosis
pneumothorax
celiac disease
eosinophilic granuloma of the lung
cystic interstitial lung disease
url https://journals.lww.com/10.4103/jacp.jacp_32_24
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